Prune isisu syndrome

I-Prune belly syndrome iyiqembu lezinkinga zokuzalwa ezingavamile ezibandakanya lezi zinkinga ezintathu eziyinhloko:

• Ukukhula kabi kwemisipha yesisu, okwenza isikhumba sendawo yesisu sishwabane njengesihlahla somunwe
• Amasende angehlisiwe
• Izinkinga zomgudu womchamo

Izimbangela eziqondile ze-prune belly syndrome azaziwa. Lesi simo sithinta kakhulu abafana.

Ngenkathi usesibelethweni, isisu sengane esikhulayo sigcwala uketshezi. Imvamisa, imbangela iyinkinga emkhakheni we-urinary. Uketshezi luyanyamalala ngemuva kokuzalwa, okuholela esiswini esishwabene esibukeka njengesihlahla sikaPrune. Lokhu kubonakala kuphawuleka kakhulu ngenxa yokushoda kwemisipha yesisu.

Imisipha yesisu ebuthakathaka ingadala:

• Ukuqunjelwa
• Ukubambezeleka ukuhlala nokuhamba
• Kunzima ukukhwehlela

Izinkinga zomgudu womchamo zingadala ubunzima bokuchama.

Owesifazane okhulelwe ingane ene-prune belly syndrome kungenzeka angabi nayo i-amniotic fluid eyanele (uketshezi oluzungeze umbungu). Lokhu kungadala ukuthi usana lube nezinkinga zamaphaphu ngokucindezelwa esibelethweni.

I-ultrasound eyenziwe ngesikhathi sokukhulelwa ingakhombisa ukuthi ingane inesibindi sokuvuvukala noma izinso ezikhulisiwe.

Kwezinye izimo, i-ultrasound yokukhulelwa ingasiza futhi ukunquma ukuthi ngabe ingane ine:

• Izinkinga zenhliziyo
• Amathambo noma imisipha engajwayelekile
• Izinkinga zesisu namathumbu
• Amaphaphu angathuthuki kahle

Ukuhlolwa okulandelayo kungenziwa enganeni ngemuva kokuzalwa ukuthola isimo:

• Ukuhlolwa kwegazi
• I-pyelogram efakwa emithanjeni (IVP)
• I-Ultrasound
• Ukuvala i-cystourethrogram (VCUG)
• I-X-ray
• Iskena se-CT
  

Ukuhlinzwa kusenesikhathi kunconywa ukulungisa imisipha ebuthakathaka yesisu, izinkinga zomgudu womchamo, namasende angafunwanga.

Ingane inganikezwa ama-antibiotic ukwelapha noma ukusiza ukuvimbela izifo ezithinta umchamo.

Izinsizakusebenza ezilandelayo zinganikeza imininingwane eminingi nge-prune belly syndrome:

• Prune Belly Syndrome Network - prunebelly.org
• Inhlangano Kazwelonke Yezinkinga Ezingajwayelekile - rarediseases.org/rare-diseases/prune-belly-syndrome

I-Prune belly syndrome iyinkinga enkulu futhi esongela impilo.

Izinsana eziningi ezinalesi sifo zizalwa zingasekho emhlabeni noma zife kungakapheli amasonto ambalwa okuqala okuphila. Imbangela yokufa ivela ezinkingeni ezinzima zamaphaphu noma zezinso, noma ekuhlanganeni kwezinkinga zokuzalwa.

Ezinye izingane ezisanda kuzalwa ziyaphila futhi zingakhula ngokujwayelekile. Abanye bayaqhubeka nokuba nezinkinga eziningi zezokwelapha nezentuthuko.

Izinkinga zincike ezinkingeni ezihlobene. Okuvame kakhulu yilezi:

• Ukuqunjelwa
• Ukukhubazeka kwamathambo (i-clubfoot, i-hip ehlukanisiwe, isitho esilahlekile, umunwe, noma inzwane, isifuba se-funnel)
• Izifo zomgudu womchamo (zingadinga i-dialysis kanye nokufakelwa kwezinso)

Amasende angehlisiwe angaholela ekuthini angatholi inzalo noma umdlavuza.

I-Prune belly syndrome ivame ukutholakala ngaphambi kokuzalwa noma lapho ingane izalwa.

Uma unengane ene-prune belly syndrome etholakele, shayela umhlinzeki wakho wezokunakekelwa kwempilo ngesibonakaliso sokuqala sokutheleleka ngomgudu womchamo noma ezinye izimpawu zomchamo.

Uma ukukhulelwa kwe-ultrasound kukhombisa ukuthi ingane yakho inesibindi sokuvuvukala noma izinso ezikhulisiwe, khuluma nesazi sokukhulelwa okuyingozi kakhulu noma i-perinatology.

Ayikho indlela eyaziwayo yokuvikela lesi simo. Uma ingane kutholakala ukuthi inokuvinjelwa komgudu womchamo ngaphambi kokuzalwa, ezimweni ezingavamile, ukuhlinzwa ngesikhathi sokukhulelwa kungasiza ekuvimbeleni inkinga ekuqhubekeni iye ekuthenweni kwesisu.

I-Eagle-Barrett syndrome; I-Triad syndrome

ICaldamone AA, Denes FT. Isifo sePrune-belly syndrome. Ku: Wein AJ, Kavoussi LR, Partin AW, Peters CA, ama-eds. ICampbell-Walsh Urology. Umhla ka-11. IPhiladelphia, PA: Elsevier; 2016: isahluko 140.

Umdala JS. Ukuvinjelwa komgudu womchamo. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Incwadi kaNelson Yezingane. Umhlaka 21. IPhiladelphia, PA: Elsevier; 2020: isahluko 555.

IMerguerian PA, iRowe CK. Ukukhubazeka okuthuthukayo kohlelo lwe-genitourinary. Ku: Gleason CA, Juul SE, ama-eds. Izifo zika-Avery Zomntwana osanda kuzalwa. Umhlaka 10. IPhiladelphia, PA: Elsevier; 2018: isahluko 88.