Kuyini nokuthi ungaphatha kanjani i-Becker dystrophy muscular

-Delile

• Yelashwa kanjani
• Izimpawu eziyinhloko
• Ukuxilongwa kwenziwa kanjani
• Yini engadala i-dystrophy

I-Becker muscular dystrophy yisifo sofuzo esidala ukubhujiswa kancane kancane kwemisipha eminingi yokuzithandela, okungukuthi, imisipha esikwazi ukuyilawula, njengaleyo yezinqulu, amahlombe, imilenze noma izingalo, ngokwesibonelo.

Imvamisa kuvame kakhulu emadodeni futhi izimpawu zokuqala zivela ebuntwaneni noma ngesikhathi sobusha, ziqala ngokuncipha kancane kancane kwamandla cishe kuyo yonke imisipha yomzimba, kepha ikakhulukazi emahlombe nasezinqeni.

Yize lesi sifo singelapheki, kungenzeka ukuthi uthole ukwelashwa ukudambisa izimpawu futhi ube nekhwalithi enhle yokuphila nokuphila isikhathi esifinyelela eminyakeni engama-50.

Yelashwa kanjani

Ukwelashwa kwe-Becker muscular dystrophy kwenziwa ukukhulula izimpawu zomuntu ngamunye futhi, ngakho-ke, kungahluka esimweni ngasinye. Kodwa-ke, izindlela zokwelashwa ezivame kakhulu zifaka:

• Amakhambi we-Corticosteroid, njenge-Betamethasone noma i-Prednisone: kusiza ukunciphisa ukuvuvukala kwemisipha ngenkathi kuvikelwa imicu yemisipha nevolumu yayo. Ngale ndlela kungenzeka ukugcina ukusebenza kwemisipha isikhathi eside;
• I-Physiotherapy: kusiza ukugcina ukunyakaza kwemisipha, ukuyelula nokuyivimbela ekubeni iqine kakhulu. Ngakho-ke, kungenzeka ukunciphisa inani lokulimala ezintanjeni nasemalungeni emisipha;
• Ukwelashwa emsebenzini: yizikhathi ezifundisa ukuthi ungaphila kanjani nemikhawulo emisha ebangelwa yilesi sifo, ukuqeqesha izindlela ezintsha zokwenza imisebenzi eyisisekelo yansuku zonke njengokudla, ukuhamba noma ukubhala, isibonelo.

Ngaphezu kwalokho, kusengadingeka ukwenza ukuhlinzwa, ikakhulukazi uma imisipha iba mfushane noma iqine kakhulu, ukuyikhulula futhi ilungise ukufushaniswa. Lapho izinkontileka zivela emisipheni yamahlombe noma emuva, zingadala ukukhubazeka emgogodleni odinga ukulungiswa futhi ngokuhlinzwa.

Esigabeni esinzima kakhulu sesifo, kujwayelekile ukuthi kuvele izinkinga ezinkulu, njengezinkinga zenhliziyo nokuphefumula kanzima, ngenxa yokucekelwa phansi kwemisipha yenhliziyo nemisipha yokuphefumula. Ezimweni ezinjalo, kungaqokwa udokotela wenhliziyo nodokotela wamaphaphu ukusiza ukusiza ukwelashwa.

Izimpawu eziyinhloko

Izimpawu zokuqala ze-Becker muscular dystrophy zivame ukuvela phakathi kweminyaka engu-5 nengu-15 ubudala, futhi zingafaka izimpawu ezifana nokuthi:

• Kancane kancane ubunzima bokuhamba nokukhuphuka izitebhisi;
• Ukuwa kaningi ngaphandle kwesizathu;
• Ukulahleka kwemisipha;
• Ukwenza buthakathaka imisipha yentamo nezingalo;
• Ukukhathala ngokweqile;
• Ukulahlekelwa ibhalansi nokuxhumanisa;

Ezimweni eziningi ingane ingayeka ukuhamba ize ibe neminyaka eyi-16, njengoba lesi sifo siqhubeka ngokushesha emalungeni aphansi. Kodwa-ke, lapho izimpawu zivela kamuva kunokujwayelekile, amandla okuhamba angagcinwa ngisho naphakathi kweminyaka engama-20 nengama-40.

Ukuxilongwa kwenziwa kanjani

Ezimweni eziningi, udokotela wezingane angalusola lolu hlobo lwe-dystrophy kuphela ngokuhlola izimpawu nokubheka ukulahleka kwezicubu zemisipha, ngokwesibonelo. Kodwa-ke, okunye ukuhlolwa kokuxilongwa okufana ne-muscle biopsy, ukuhlolwa kwenhliziyo nama-X-ray kungasiza ukuqinisekisa ubukhona be-Becker Muscular Dystrophy.

Yini engadala i-dystrophy

I-Becker's Muscular Dystrophy ivela ngenxa yokuguqulwa kofuzo okuvimbela ukukhiqizwa kwamaprotheni e-dystrophin, into ebaluleke kakhulu ukugcina amaseli emisipha angaqinile. Ngakho-ke, lapho le protein iphansi ngamanani aphansi emzimbeni, imisipha ayikwazi ukusebenza kahle, iqala ukubonakala izilonda ezichitha imicu yemisipha.

Njengesifo sofuzo, lolu hlobo lwe-dystrophy lungadluliselwa lisuka kubazali luye ezinganeni noma luvele ngenxa yokuguquka kwesimo ngesikhathi sokukhulelwa.