Umlobi: John Pratt
Usuku Lokudalwa: 17 Ufebhuwari 2021
Ukuvuselela Usuku: 5 Ujuni 2025
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I-Scleroderma isifo esingalapheki sokuzivikela komzimba lapho kukhiqizwa ngokweqile i-collagen, okuholela ekuqineni kwesikhumba futhi kuthinte amalunga, imisipha, imithambo yegazi nezinye izitho zangaphakathi, njengamaphaphu nenhliziyo.

Lesi sifo sithinta kakhulu abesifazane abaneminyaka engaphezu kwengama-30, kodwa futhi singenzeka nakwabesilisa nasezinganeni, futhi sehlukaniswe ngezinhlobo ezimbili, i-localized and systemic scleroderma, ngokusho kwamandla aso. I-Scleroderma ayinawo amakhambi kanti ukwelashwa kwayo kwenziwa ukudambisa izimpawu nokunciphisa ukuqhubeka kwesifo.

Izimpawu ze-Scleroderma

Izimpawu ze-scleroderma ziguquka ngokuhamba kwesikhathi futhi, ngokusho kwezimpawu, i-scleroderma ingahlukaniswa nge:

  • Okuhlelekile, lapho izimpawu zibonakaliswa khona esikhumbeni nasezitho zangaphakathi, kubhekwa njengohlobo olunzima kakhulu lwe-scleroderma;
  • Kwenziwe kwasendaweni, lapho izimpawu zikhawulelwe esikhumbeni.

Ngokuvamile, izimpawu eziyinhloko ezihlobene ne-scleroderma yilezi:


  • Ukuqina nokuqina kwesikhumba;
  • Ukuvuvukala njalo kweminwe nezandla;
  • Ukwenza mnyama iminwe ezindaweni ezibandayo noma phakathi neziqephu zokuxineka ngokweqile, okwaziwa nangokuthi into kaRaynaud;
  • Ukulunywa okuqhubekayo esifundeni esithintekile;
  • Ukulahleka kwezinwele;
  • Amabala amnyama kakhulu futhi alula kakhulu esikhunjeni;
  • Ukubukeka kwamabala abomvu ebusweni.

Ukubonakaliswa kokuqala kwalesi sifo kuqala ezandleni futhi ngemuva kwezinyanga noma iminyaka kudlulela ebusweni, kushiya isikhumba siqinile, ngaphandle kokuqina futhi ngaphandle kwemibimbi, nakho okwenza kube nzima ukuvula umlomo ngokuphelele. Ngaphezu kwalokho, ezimweni ze-systemic scleroderma, lo muntu kungenzeka futhi ukuthi anyuse umfutho wegazi, ukugaya ukudla okungahambi kahle, ukuphefumula kancane, ukuncipha ngaphandle kwesizathu, ushintsho esibindini nasenhliziyweni.

Izinkinga ezingenzeka

Izinkinga ze-scleroderma zihlobene nokuqala kokwelashwa futhi zivame ukuvela kubantu abanohlobo lwesistimu yalesi sifo. Ngakho-ke, lapho ukwelashwa kungenziwanga ngokuyalelwa ngudokotela, umuntu uba nezinkinga ezithile njengobunzima bokuhambisa iminwe, ukugwinya noma ukuphefumula, i-anemia, isifo samathambo, izinkinga zenhliziyo nokuhluleka kwezinso, ngokwesibonelo.


Ukuxilongwa kwenziwa kanjani

Ukuxilongwa kwe-scleroderma kunzima, njengoba izimpawu ziguquka kancane futhi zingadidaniswa nezinye izinkinga zesikhumba. Ukuqinisekiswa kwalesi sifo kufanele kwenziwe ngudokotela wesikhumba noma we-rheumatologist, kucatshangelwa izimpawu nezimpawu ezethulwe ngumuntu, nomphumela wokuhlolwa kwe-imaging nelebhu.

Ngakho-ke, kungakhonjiswa ngudokotela ukwenza i-tomography noma isifuba se-X-ray kanye ne-biopsy yesikhumba, ngaphezu kokwenza ukuhlolwa kwe-ANA, okuwukuhlolwa kwelabhorethri okuhlose ukukhomba ubukhona bama-antibody ajikeleza egazini.

Ukwelashwa kwe-scleroderma

I-Scleroderma ayinawo umuthi, ngakho-ke, ukwelashwa kuhlose ukuvimbela ukuqhubeka kwesifo, kunciphise izimpawu futhi kuthuthukise izinga lomuntu lokuphila. Ukwelashwa okukhonjiswe yi-rheumatologist noma i-dermatologist kungahluka ngokuya ngohlobo lwe-scleroderma nezimpawu ezethulwe ngumuntu, futhi ukusetshenziswa kwemithi ethile kungakhonjiswa ngokuya ngecala, elingasetshenziswa ngqo esikhunjeni noma kokungeniswa, njenge ama-immunosuppressants noma ama-corticosteroids.


Endabeni yabantu abethula into kaRaynaud njengenye yezimpawu ze-scleroderma, kunconywa futhi ukugcina imiphetho yomzimba ifudumele.

Ngaphezu kwalokho, njengoba i-scleroderma ingahle ihambisane nokuqina okuhlangene, izikhathi ze-physiotherapy nazo zingakhonjiswa ukukhulisa ukuguquguquka okuhlangene, ukunciphisa ubuhlungu, ukuvimbela izinkontileka nokugcina ukusebenza kwamalungu nobukhulu.

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