IPityriasis Rubra Pilaris

-Delile

• Izinhlobo ze-pityriasis rubra pilaris
• Izithombe ze-PRP
• Yini ebangela i-PRP?
• I-PRP izuzwe kanjani njengefa?
• Ziyini izimpawu ze-PRP?
• I-PRP itholakala kanjani?
• Yiziphi izinkinga ezingaba khona ze-PRP?
• Iphathwa kanjani i-PRP?
• Ngingavimbela i-PRP?
• Ngabe i-PRP izohamba?
• Khuluma nodokotela wakho

Isingeniso

I-Pityriasis rubra pilaris (PRP) isifo esingajwayelekile sesikhumba. Kubangela ukuvuvukala okungapheli nokuchitheka kwesikhumba.I-PRP ingathinta izingxenye zomzimba wakho noma umzimba wakho wonke. Lesi sifo singaqala ebuntwaneni noma ebudaleni. I-PRP ithinta abesilisa nabesifazane ngokulinganayo.

Izinhlobo ze-pityriasis rubra pilaris

Kunezinhlobo eziyisithupha ze-PRP.

Ukuqala kwe-Classical yabantu abadala i-PRP uhlobo oluvame kakhulu. Kwenzeka ebudaleni. Izimpawu zivame ukuphela ngemuva kweminyaka embalwa. Kwezinye izimo ezingavamile, izimpawu zibuya kamuva.

Ukuqala kwe-Atypical yabantu abadala i-PRP nayo iqala lapho usumdala. Kodwa-ke, izimpawu zingahlala iminyaka engaphezu kwengu-20.

Ukuqala kwentsha yakudala i-PRP kuqala ebuntwaneni. Izimpawu zivame ukuphela kungakapheli unyaka, kepha zingabuya ngokuhamba kwesikhathi.

Ukuqala kwentsha e-circumcribed PRP kuqala ngaphambi kokuthomba. Ngokuvamile kuthinta izintende zezandla zezingane, amathe ezinyawo zazo, namadolo nezindololwane. Izimpawu zingaphela phakathi neminyaka yobusha.

Ukuqala kwentsha ye-Atypical PRP kwesinye isikhathi kuzuzwa njengefa. Lokho kusho ukuthi kudlulile ngomndeni. Kungaba khona lapho kuzalwa noma kukhula ngesikhathi sobuntwana. Izimpawu zivame ukuhlala impilo yonke.

I-PRP ehlobene ne-HIV ixhunyaniswe ne-HIV. Kunzima kakhulu ukwelashwa.

Izithombe ze-PRP

Yini ebangela i-PRP?

Imbangela ngqo ye-PRP ayaziwa. I-PRP ivame ukwenzeka ngaphandle kwesizathu esicacile. Ngenkathi amanye amacala we-PRP ezuzwe njengefa, iningi alinalo. I-PRP ezuzwe njengefa ijwayele ukuba nzima kakhulu.

Ukuqala kwe-Classical PRP yabantu abadala kungaxhunyaniswa nomdlavuza wesikhumba oyimbangela. Kodwa-ke, ukuthi umdlavuza wesikhumba kwenzeka kangaki ngalolu hlobo lwe-PRP akwaziwa. Uma une-classical PRP, qiniseka ukuthi ubona udokotela wakho ukuze ahlole umdlavuza wesikhumba.

Ngokusho kweNational Organisation for Rare Disorders, ucwaningo lwakuqala luphakamisa ukuthi i-PRP kungenzeka ukuthi ibangelwe inkinga endleleni umzimba owenza ngayo uvithamini A. Kodwa-ke, kudingeka olunye ucwaningo ukuthola ukuthi lokhu kuliqiniso yini.

I-PRP nayo ingaxhunyaniswa nempendulo yesistimu yomzimba yokuzivikela, ngokusho kweGenetic and Rare Diseases Information Center.

I-PRP izuzwe kanjani njengefa?

I-PRP ingazuzwa njengefa. Ungathola ifa le-PRP uma omunye wabazali bakho edlulisa isakhi sofuzo esidala lesi sifo. Umzali wakho angaba ngumuntu ophethe ufuzo, okusho ukuthi banalo ufuzo kodwa abanakho ukugula. Uma omunye wabazali bakho ethwala isakhi sofuzo, kunethuba elingamaphesenti angama-50 lokuthi isakhi sidluliselwe kuwe. Kodwa-ke, ungahle ungathuthukisi i-PRP noma ngabe uzuze njengefa zofuzo.

Ziyini izimpawu ze-PRP?

I-PRP ibangela ama-scaly amabala abomvu, abomvu, noma abomvu okusawolintshi esikhunjeni sakho. Amachashazi avame ukunwaya. Ungase ube nezimagqabhagqabha ezinesikhumba kwezinye izingxenye zomzimba wakho kuphela. Zivame ukwenzeka ku:

• Izindololwane
• amadolo
• izandla
• izinyawo
• amaqakala

Isikhumba ezintendeni zezandla zakho nasematheni ezinyawo zakho nawo angaba bomvu futhi aqine. Amabala ama-scaly angagcina esabalele kuwo wonke umzimba.

I-PRP itholakala kanjani?

I-PRP ivame ukuphutha ngezinye, izimo zesikhumba ezivame kakhulu, njenge-psoriasis. Kungaphanjaniswa nokungajwayelekile kakhulu, njenge-lichen planus ne-pityriasis rosea. I-Psoriasis imakwe ngamachashaza esikhumba, anezikhala ezinesikhumba esivame ukuba bomvu. Kodwa-ke, ngokungafani ne-PRP, i-psoriasis ingalashwa kalula futhi ngempumelelo. I-PRP kungenzeka ingatholakali kuze kube yilapho ama-scaly patches ehluleka ukuphendula ekwelashweni kwe-psoriasis.

Uma udokotela wakho esola i-PRP, bangenza i-biopsy yesikhumba ukubasiza ukuthi benze ukuxilongwa. Ngale nqubo, udokotela wakho ususa isampula elincane lesikhumba sakho. Bese beyibuka ngaphansi kwesibonakhulu ukuze bayihlaziye.

Yiziphi izinkinga ezingaba khona ze-PRP?

Ngokwengxenye enkulu, i-PRP ingaba ilume futhi ingakhululeki. Lezi zimpawu zingancipha ngokuhamba kwesikhathi, noma ngabe ukuqubuka kubukeka sengathi kuya ngokuya kuba kubi. Isimo ngokuvamile asibangeli izinkinga eziningi.

Kodwa-ke, i-PRP Support Group iphawula ukuthi ukuqubuka kwesinye isikhathi kungaholela kwezinye izingqinamba, njenge-ectropion. Kulesi simo, ijwabu leso liyavela, liveze ubuso beso. I-PRP nayo ingaholela ezinkingeni ngokufakwa komlomo. Lokhu kungabangela ukucasuka nobuhlungu.

Ngokuhamba kwesikhathi, i-PRP ingaholela ku-keratoderma. Le nkinga idala ukuthi isikhumba esisezandleni zakho naphansi kwezinyawo zakho sikhuluphale kakhulu. Ukuqhekeka okujulile esikhunjeni, okubizwa ngokuthi ama-fissures, kungakhula.

Abanye abantu abane-PRP nabo bayazwela ekukhanyeni. Bangaba nenkinga yokujuluka noma ukulawula ukushisa komzimba lapho kushisa.

Iphathwa kanjani i-PRP?

Alikho ikhambi lamanje le-PRP, kepha ukwelashwa kunganciphisa izimpawu. Udokotela wakho angakunikeza eyodwa noma ngaphezulu yokwelashwa okulandelayo:

• Ama-topical cream aqukethe urea noma i-lactic acid. Lezi zihamba ngqo esikhunjeni sakho.
• Ama-retinoids omlomo. Izibonelo zifaka i-isotretinoin noma i-acitretin. Lokhu kuvela ku-vitamin A okwehlisa ukukhula nokuchitheka kwamaseli esikhumba.
• Uvithamini A. omlomo Lokhu kungasiza kwabanye abantu, kepha kuphela ngemithamo ephezulu kakhulu. Ama-retinoids asebenza kahle futhi asetshenziswa kakhulu kunevithamini A.
• IMethotrexate. Lesi yisidakamizwa somlomo esingasetshenziswa uma ama-retinoid engasebenzi.
• Ama-immunosuppressants. Le yimithi yokwelapha ecindezela amasosha omzimba. Kubandakanya i-cyclosporine ne-azathioprine.
• I-Biologics. Le yimithi ejojowe noma efakwa emithanjeni (IV) ethinta amasosha akho omzimba. Kubandakanya izidakamizwa i-adalimumab, i-etanercept, ne-infliximab.
• Ukwelashwa kokukhanya kwe-Ultraviolet. Lokhu kuvame ukunikezwa kuhlanganiswe ne-psoralen (umuthi okwenza ungazweli kakhulu elangeni) kanye ne-retinoid.

Ngingavimbela i-PRP?

Akunakwenzeka ukuvimbela i-PRP njengoba imbangela nokuqala kungaziwa. Uma usola ukuthi une-PRP, bheka udokotela wakho. Ukuqala ukwelashwa okusebenzela wena ngokushesha nje lapho uthola ukuxilongwa kuyisihluthulelo sokuqeda izimpawu zakho.

Ukuthola ukwelashwa okuphumelelayo nakho kubalulekile ngoba ungahlakulela izinhlobo ezingaphezu kweyodwa ze-PRP phakathi nalesi sifo.

Ngabe i-PRP izohamba?

Ngokuya ngohlobo lwe-PRP onayo, izimpawu zakho kungenzeka noma zingapheli. Uma une-PRP yakudala yabantu abadala, izimpawu zakho kungenzeka zihlale iminyaka embalwa noma ngaphansi bese zingaphinde zibuye.

Izimpawu zezinye izinhlobo ze-PRP zingahlala isikhathi eside. Kodwa-ke, ukwelashwa kungenza izimpawu zingabonakali kangako.

Khuluma nodokotela wakho

I-PRP isifo esingajwayelekile sesikhumba esikhonjiswe ukuvuvukala okungapheli nokuchitheka kwesikhumba sakho. Kungathinta umzimba wakho wonke noma izingxenye ezithile zawo. Ingaqala nganoma yisiphi isikhathi empilweni yakho. Yize lungekho ikhambi lamanje, ukwelashwa kungasiza ekunciphiseni izimpawu zakho.

Ukwelashwa kwe-PRP kufaka phakathi imithi yokwelapha, yomlomo, kanye nemijovo. Zihlanganisa nokwelashwa kokukhanya kwe-ultraviolet. Sebenza nodokotela wakho ukuthola ukwelashwa okusebenza kahle ukukhulula izimpawu zakho ze-PRP.