Izimpawu nokwelashwa kwe-Hugles-Stovin Syndrome

-Delile

• Izimpawu
• Ukwelashwa
• Izinkinga

I-Hugles-stovin syndrome yisifo esingajwayelekile futhi esibi kakhulu esidala ama-aneurysms amaningi emthanjeni we-pulmonary kanye namacala amaningana we-vein thrombosis ejulile ngesikhathi sokuphila. Kusukela kuchazwa okokuqala kwalesi sifo emhlabeni wonke, bangaphansi kuka-40 abantu asebeke batholakala ngonyaka ka-2013.

Lesi sifo singaziveza ngezigaba ezi-3 ezihlukene, lapho okokuqala kuvame ukuvela nge-thrombophlebitis, isigaba sesibili esinama-pulmonary aneurysms, kanti isigaba sesithathu nesokugcina sibonakala ngokuthi kuqhume i-aneurism engadala ukukhwehlela kwegazi nokufa.

Udokotela ofanele kakhulu ukuxilonga nokwelapha lesi sifo yi-rheumatologist futhi yize imbangela yaso ingakaziwa ngokugcwele, kukholakala ukuthi kungenzeka ihlobene ne-systemic vasculitis.

Izimpawu

Izimpawu zikaHugles-stovin zifaka:

• Ukukhwehlela igazi;
• Kunzima ukuphefumula;
• Ukuzwa ukuphefumula okuncane;
• Ikhanda;
• Umkhuhlane ophakeme, ophikelelayo;
• Ukwehla kwesisindo cishe esingu-10% ngaphandle kwesizathu esisobala;
• I-Papilledema, okuwukuhlulwa kwe-optic papilla emele ukwanda kwengcindezi ngaphakathi kobuchopho;
• Ukuvuvukala nobuhlungu obukhulu enkonyane;
• Umbono ophindwe kabili kanye
• Ukudlikizela.

Imvamisa umuntu one-Hugles-stovin syndrome unezimpawu zeminyaka eminingi kanti lesi sifo singadideka nesifo sikaBehçet kanti abanye abacwaningi bakholelwa ukuthi lesi sifo empeleni siyisihumusho esingaphelele sesifo sikaBehçet.

Lesi sifo asijwayele ukutholakala ebuntwaneni futhi singatholwa ebusheni noma ebudaleni ngemuva kokwethula lezi zimpawu ezingenhla futhi sihlolwe njengokuhlolwa kwegazi, ama-X-ray esifubeni, ama-MRIs noma i-computed tomography yekhanda nesifuba, ngaphezu kwe-doppler ultrasound ukuhlola ukujikeleza kwegazi nenhliziyo. Ayikho indlela yokuxilonga futhi udokotela kufanele asole lesi sifo ngenxa yokufana kwaso nesifo sikaBehçet, kodwa ngaphandle kwazo zonke izici zaso.

Iminyaka yabantu abatholwe benale syndrome iyahluka phakathi kweminyaka eyi-12 nengama-48.

Ukwelashwa

Ukwelashwa kwe-Hugles-Stovin syndrome akucaci kakhulu, kepha udokotela angancoma ukusetshenziswa kwama-corticosteroids afana ne-hydrocortisone noma i-prednisone, ama-anticoagulants anjenge-enoxaparin, i-pulse therapy kanye ne-immunosuppressants efana ne-Infliximab noma i-Adalimumab enganciphisa ubungozi kanye nemiphumela ye-aneurysms ne-thrombosis, ngaleyo ndlela ithuthukise ikhwalithi yempilo futhi yehlise nengozi yokufa.

Izinkinga

IHugles-Stovin syndrome kungaba nzima ukuyelapha futhi inokufa okuphezulu ngoba imbangela yalesi sifo ayaziwa ngakho-ke ukwelashwa kungahle kunganeli ukugcina impilo yomuntu othintekile. Njengoba zimbalwa izigameko ezitholakala emhlabeni wonke, odokotela imvamisa abasazi lesi sifo, esingenza ukuxilongwa nokwelashwa kube nzima kakhulu.

Ngaphezu kwalokho, ama-anticoagulants kufanele asetshenziswe ngokucophelela okukhulu ngoba kwezinye izimo angandisa ingozi yokopha ngemuva kokuqhuma kwe-aneurysm nokuvuza kwegazi kungaba kukhulu kakhulu kangangokuba kuvimbela ukugcinwa kwempilo.