Isifo sezinso sePolycystic

Isifo sezinso sePolycystic (PKD) yisifo sezinso esidlula emindenini. Kulesi sifo, ama-cysts amaningi akha ezinso, abangele ukuthi akhuliswe.

I-PKD idluliselwa emindenini (ezuzwe njengefa). Lezi zinhlobo ezimbili ze-PKD ezizuzwe njenge-autosomal ephezulu futhi ezisebenzisa kakhulu i-autosomal.

Abantu abane-PKD banamaqoqo amaningi ama-cysts ezinso. Yini ngempela eyenza ama-cysts akheke akwaziwa.

I-PKD ihlotshaniswa nemibandela elandelayo:

• Ama-aneurysms we-aortic
• Ama-aneurysms obuchopho
• Ama-cysts asesibindi, amanyikwe, kanye namasende
• I-Diverticula yekoloni

Abantu abangaba yingxenye yabantu abane-PKD banama-cysts esibindi.

Izimpawu ze-PKD zingafaka noma yikuphi okulandelayo:

• Ubuhlungu besisu noma ubumnene
• Igazi emchameni
• Ukuchama ngokweqile ebusuku
• Ubuhlungu beFlank ohlangothini olulodwa noma zombili
• Ukozela
• Ubuhlungu obuhlangene
• Ukungajwayelekile kwesipikili

Ukuhlolwa kungakhombisa:

• Ubumnene besisu ngaphezu kwesibindi
• Isibindi esandisiwe
• Ukububula kwenhliziyo noma ezinye izimpawu zokunganeleki kwe-aortic noma ukungasebenzi kahle kwe-mitral
• Umfutho wegazi ophezulu
• Ukukhula ezinso noma esiswini

Ukuhlolwa okungenziwa kufaka phakathi:

• I-Cerebral angiography
• Qedela ukubalwa kwegazi (CBC) ukuhlola i-anemia
• Ukuhlolwa kwesibindi (igazi)
• Ukuhlolwa komchamo

Abantu abanomlando womuntu siqu noma womndeni we-PKD abanekhanda kufanele bahlolwe ukuthola ukuthi ngabe ama-aneurysms we-cerebral ayimbangela yini.

I-PKD nama-cysts esibindini noma kwezinye izitho kungatholakala kusetshenziswa izivivinyo ezilandelayo:

• Iskena se-CT esiswini
• Ukuskena kwe-MRI yesisu
• I-ultrasound yesisu
• I-pyelogram efakwa emithanjeni (IVP)

Uma amalungu amaningana omndeni wakho ene-PKD, kungenziwa izivivinyo zofuzo ukuthola ukuthi ngabe uphethe yini uhlobo lwe-PKD

Umgomo wokwelashwa ukulawula izimpawu nokuvimbela izinkinga. Ukwelashwa kungafaka:

• Imithi yengcindezi yegazi
• I-diuretics (amaphilisi wamanzi)
• Ukudla okunosawoti omningi

Noma yikuphi ukutheleleka kwe-urinary tract kufanele kuphathwe ngokushesha ngama-antibiotics.

Ama-cysts abuhlungu, athelelekile, aphuma igazi, noma abangela ukuvimba kungadinga ukukhishwa. Ngokuvamile kunama-cysts amaningi kakhulu okwenza kube usizo ukususa i-cyst ngayinye.

Ukuhlinzwa ukususa i-1 noma zombili izinso kungadingeka. Ukwelashwa kwezifo zezinso zokugcina kungafaka i-dialysis noma ukufakelwa kwezinso.

Imvamisa unganciphisa ukucindezelwa ukugula ngokujoyina iqembu lokwesekwa lapho amalungu abelana ngokuhlangenwe nakho okuvamile nezinkinga.

Lesi sifo sihamba kancane kancane. Ekugcineni, kungaholela ekuhlulekeni kwezinso ekugcineni. Iphinde ihlotshaniswe nesifo sesibindi, kufaka phakathi ukutheleleka kwama-cysts wesibindi.

Ukwelashwa kunganciphisa izimpawu iminyaka eminingi.

Abantu abane-PKD abangenazo ezinye izifo bangaba ukhetho olufanele ukufakelwa izinso.

Izinkinga zempilo ezingabangelwa yi-PKD zifaka:

• Ukushoda kwegazi
• Ukopha noma ukuqhekeka kwama-cysts
• Isifo sezinso sesikhathi eside (esingapheli)
• Isifo sezinso sokugcina
• Umfutho wegazi ophezulu
• Ukutheleleka kwama-cysts wesibindi
• Amatshe ezinso
• Ukwehluleka kwesibindi (kuya kokubi)
• Ukuphindaphindwa kwezifo zomgudu womchamo

Shayela umhlinzeki wakho wezempilo uma:

• Unezimpawu ze-PKD
• Unomlando womndeni we-PKD noma ukuphazamiseka okuhlobene nawo futhi uhlela ukuba nezingane (ungahle uthande ukuthola ukwelulekwa ngezofuzo)

Njengamanje, alukho umuthi ongavimbela ama-cysts ukuthi akhe noma akhulise.

Ama-cysts - izinso; Izinso - i-polycystic; Isifo sezinso se-polyosstic esibusa kakhulu ku-Autosomal; ADPKD

• Izinso nezinso zesibindi - i-CT scan
• Ama-cysts wesibindi ne-spleen - i-CT scan

I-Arnaout MA. Izifo zezinso zeCystic. Ku: IGoldman L, iSchafer AI, ama-eds. Imithi yeGoldman-Cecil. Umhla ka-26. IPhiladelphia, PA: Elsevier; 2020: isahluko 118.

ITorres VE, iHarris PC. Izifo ze-cystic zezinso. Ku: Yu ASL, Chertow GM, Luyckx VA, Marsden PA, Skorecki K, Taal MW, ama-eds. IBrenner neRector's The Kidney. Umhla ka-11. IPhiladelphia, PA: Elsevier; 2020: isahluko 45.