Umlobi: Roger Morrison
Usuku Lokudalwa: 24 Usepthemba 2021
Ukuvuselela Usuku: 13 Usepthemba 2024
Anonim
Ayini ama-dacryocyte nezimbangela eziyinhloko - Impilo
Ayini ama-dacryocyte nezimbangela eziyinhloko - Impilo

-Delile

Ama-dacryocyte ahambelana nokushintsha kwesimo samaseli abomvu egazi, lapho lawa maseli athola isimo esifana nokwehla noma ukudabuka, yingakho kwaziwa nangokuthi yiseli elibomvu legazi. Lokhu kuguqulwa kwamangqamuzana abomvu egazi kungumphumela wezifo ezithinta kakhulu umnkantsha wethambo, njengakwisimo se-myelofibrosis, kepha futhi kungenziwa ngenxa yezinguquko zofuzo noma ezihlobene nobende.

Ukuba khona kwama-dacryocyte ajikelezayo kubizwa ngokuthi i-dacryocytosis futhi akubangeli zimpawu futhi akunakho ukwelashwa okuqondile, kutholakala kuphela ngesikhathi sokubalwa kwegazi. Izimpawu umuntu angaziveza zihlobene nesifo anaso futhi esiholela ekuguqulweni kwesakhiwo segazi elibomvu, okubalulekile ukuthi kuhlolwe ngudokotela ojwayelekile noma i-hematologist.

Izimbangela eziyinhloko zama-dacryocyte

Ukuvela kwama-dacryocyte akubangeli zimpawu noma uphawu, kuqinisekiswa kuphela ngesikhathi sokubalwa kwegazi ngesikhathi kufundwa isilayidi, okukhombisa ukuthi ingqamuzana elibomvu legazi linomumo ohlukile kunokujwayelekile, okukhonjisiwe embikweni.


Ukuvela kwama-dacryocyte kuvame kakhulu ukuhlobene nezinguquko kumnkantsha wethambo, obhekene nokukhiqizwa kwamaseli egazini. Ngakho-ke, izimbangela ezinkulu ze-dacryocytosis yilezi:

1. I-Myelofibrosis

I-Myelofibrosis yisifo esivezwa ukushintsha kwe-neoplastic emnkantsheni wethambo, okwenza ama-stem cells akhuthaze ukukhiqizwa kwe-collagen eyeqile, okuholela ekwakhiweni kwe-fibrosis emnkantsheni wethambo, ophazamisa ukukhiqizwa kwamangqamuzana egazi. Ngakho-ke, ngenxa yezinguquko emnkantsheni wethambo, ama-dacryocyte ajikelezayo angabonakala, ngaphezu kwalokho kungahle kube khona ubende obukhulisiwe nezimpawu nezimpawu ze-anemia.

Ukuxilongwa kokuqala kwe-myelofibrosis kwenziwa ngokubalwa kwegazi okuphelele futhi, ngokuya ngokuhlonza izinguquko, kungacelwa ukuhlolwa kwamangqamuzana ukukhomba ukuguquka kwezakhi ze-JAK 2 V617F, umongo wethambo kanye ne-myelogram ukuqinisekisa ukuthi ukukhiqizwa kwamaseli egazi . Qonda ukuthi i-myelogram yenziwa kanjani.


Okufanele ngikwenze: Ukwelashwa kwe-myelofibrosis kufanele kunconywe ngudokotela ngokusho kwezimpawu nezimpawu ezethulwe ngumuntu nesimo somnkantsha. Isikhathi esiningi, udokotela angancoma ukusetshenziswa kwezidakamizwa ze-JAK 2 inhibitor, ukuvimbela ukuqhubeka kwesifo nokuqeda izimpawu, noma kunjalo kwezinye izimo, kunganconywa ukufakelwa kwe-stem cell.

2. AmaTalassemias

I-Thalassemia yisifo se-hematological esibonakala ngokushintshwa kwezakhi zofuzo okuholela ekukhubazekeni kwenqubo ye-hemoglobin synthesis, engaphazamisa ukwakheka kweseli elibomvu, ngoba i-hemoglobin yakha leli seli, nokuba khona kwama-dacryocyte kungabonakala.

Ngaphezu kwalokho, ngenxa yezinguquko ekwakhekeni kwe-hemoglobin, ukuthuthwa komoya-mpilo ezithweni nasezicubu zomzimba kukhubazekile, okuholela ekubonakaleni kwezimpawu nezimpawu ezifana nokukhathala ngokweqile, ukucasuka, ukwehla kwamasosha omzimba nokungathandi ukudla , isibonelo.


Okufanele ngikwenze: Kubalulekile ukuthi udokotela akhombe uhlobo lwe-thalassemia umuntu okufanele akhombise ukwelashwa okufanele kakhulu, njengoba ekhonjiswa ukusetshenziswa kwezithasiselo zensimbi nokumpontshelwa igazi. Qonda ukuthi ukwelashwa kwe-thalassemia kwenziwa kanjani.

3. I-hemolytic anemia

Ku-hemolytic anemia, amangqamuzana abomvu egazi abhujiswa amasosha omzimba uqobo, abangela ukuthi umnkantsha ukhiqize amangqamuzana egazi amaningi bese uwadedela ekusakazeni. eyaziwa ngokuthi ama-reticulocytes.

Okufanele ngikwenze: I-hemolytic anemia ayelapheki ngaso sonke isikhathi, noma kunjalo ingalawulwa ngokusetshenziswa kwezidakamizwa okufanele zinconywe ngudokotela, njenge-corticosteroids kanye ne-immunosuppressants, isibonelo, ukulawula amasosha omzimba. Ezimweni ezimbi kakhulu, ukukhishwa kobende kungakhonjiswa, ngoba ubende yisitho lapho kwenzeka khona ukubhujiswa kwamaseli abomvu egazi. Ngakho-ke, ngokususwa kwalesi sitho, kungenzeka ukuthi kunciphiswe izinga lokucekelwa phansi kwamangqamuzana abomvu egazi futhi kuvunyelwe ukuhlala kwawo egazini.

Funda kabanzi nge-hemolytic anemia.

4. Abantu aba-Splenectomized

Abantu abaxhunyanisiwe yilabo okwakudingeka bahlinzwe ukuze kususwe ubende futhi, ngakho-ke, ngaphezu kokungabhubhisi amangqamuzana egazi abomvu amadala, akukho nokukhiqizwa kwamangqamuzana egazi abomvu amasha, ngoba lokhu futhi kungomunye wemisebenzi yabo. Lokhu kungadala "ukulayishwa ngokweqile" emnkantsheni wethambo ukuze inani lamaseli abomvu akhiqizwayo lanele ukusebenza kahle komzimba, ongagcina uholele ekubukekeni kwama-dacryocyte.

Okufanele ngikwenze: Ezimweni ezinjalo, kubalulekile ukuthi kulandelwe ukwelashwa ukuze kuhlolwe ukuthi impendulo yomzimba ingekho kanjani kulesi sitho.

Bona ukuthi ukukhishwa kobende kukhonjisiwe.

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