Umlobi: Eugene Taylor
Usuku Lokudalwa: 14 Agasti 2021
Ukuvuselela Usuku: 18 Ujuni 2024
Anonim
Haemolytic Uraemic Syndrome
Ividiyo: Haemolytic Uraemic Syndrome

-Delile

Kuyini i-Hemolytic Uremic Syndrome?

I-Hemolytic uremic syndrome (i-HUS) yisimo esiyinkimbinkimbi lapho ukusabela komzimba, okuvame kakhulu ngemuva kokutheleleka kwamathumbu emathunjini, kubangela amazinga aphansi wamangqamuzana egazi abomvu, amazinga aphansi eplatelet, nokulimala kwezinso.

Ukutheleleka kwepheshana lamathumbu (isisu sakho namathumbu akho) kuyimbangela evame kakhulu yalesi sifo. Amasosha omzimba aphendula ubuthi obukhishwe ngesikhathi sokutheleleka kwamagciwane emathunjini. Lokhu kudala ukulimala nokubhujiswa kwamangqamuzana egazi njengoba ejikeleza ngemithambo yegazi. Lokhu kufaka phakathi amangqamuzana abomvu egazi (RBC) nama-platelets, okubangela ukuthi bafe ngaphambi kwesikhathi. Izinso zithinteka ngezindlela ezimbili.Ukusabela komzimba kungadala ukulimala okuqondile kumaseli ezinso okuholela ekulimaleni kwezinso. Ngenye indlela, ukwakheka kwama-RBCs noma amaplatelet abhujisiwe kungavimba uhlelo lokuhlunga izinso futhi kubangele ukulimala kwezinso noma ukwakheka kwemikhiqizo kadoti emzimbeni, ngoba izinso azisakwazi ukuqeda imfucuza egazini.


Ukulimala kwezinso kungaba kubi impela uma kungalashwa. Ukwehluleka kwezinso, ukuphakama okuyingozi kwengcindezi yegazi, izinkinga zenhliziyo, nokushaywa unhlangothi konke okukhathazayo uma i-HUS iqhubeka ngaphandle kokwelashwa ngokushesha.

I-HUS iyimbangela evame kakhulu yokwehluleka okukhulu kwezinso ezinganeni. Kuvame kakhulu ezinganeni ezineminyaka engaphansi kwengu-5, yize izingane ezindala nabantu abadala nabo bangahlushwa yilesi sifo.

Ngenhlanhla, abantu abaningi abathola ukwelashwa ngokushesha bangalulama ngokugcwele ngaphandle kokulimala ngokuphelele kwezinso.

Ukuqaphela Izimpawu ze-Hemolytic Uremic Syndrome

Izimpawu ze-HUS ziyahlukahluka. Izimpawu zingafaka:

  • uhudo olunegazi
  • ubuhlungu besisu
  • isikhumba esiphaphathekile
  • ukucasuka
  • ukukhathala
  • imfiva
  • imihuzuko noma ukopha okungachazeki
  • ukuncipha ukuchama
  • ukuvuvukala kwesisu
  • igazi emchameni
  • ukudideka
  • ukuhlanza
  • ubuso obuvuvukile
  • izitho ezivuvukele
  • ukuquleka (okungavamile)

Yini Ebangela I-Hemolytic Uremic Syndrome?

I-HUS yenzeka lapho ukusabela komzimba kubangela ukubhujiswa kwamangqamuzana egazi. Lokhu kuholela emazingeni aphansi wamangqamuzana egazi abomvu, amazinga aphansi eplatelet, nokulimala kwezinso


HUS ezinganeni

Isizathu esivame kakhulu se-HUS ezinganeni ukutheleleka nge EscherichiaI-Coli (E. coli). Kunezinhlobo eziningi ezahlukahlukene ze E. coli, futhi eziningi azizibangeli izinkinga. Empeleni, E. coli amabhaktheriya ngokuvamile atholakala emathunjini abantu nezilwane ezinempilo. Kodwa-ke, ezinye izinhlobo ezithile ze- E. coli, okudluliswa ngokudla okungcolile, kubhekene nezifo ezingaholela ku-HUS. Izindikimba zamanzi ezingcoliswe indle nazo zingathwala E. coli.

Amanye amabhaktheriya afana ne- Shigellaisifo samathambo futhi Salmonella typhi kungadala HUS.

HUS in Abadala

I-HUS kubantu abadala nayo ingabangelwa ukutheleleka nge E. coli.. Kunezimbangela eziningi ezingezona ezamagciwane ze-HUS kubantu abadala ezingavamile kakhulu, kufaka phakathi:

  • ukukhulelwa
  • Ukutheleleka nge-HIV / AIDS
  • i-quinine (esetshenziselwa amajaqamba emisipha)
  • i-chemotherapy kanye nemithi yokuzivikela emzimbeni
  • amaphilisi okuvimbela inzalo
  • imithi elwa ne-platelet
  • umdlavuza
  • i-systemic lupus ne-glomerulonephritis

Ukuhlonza i-Hemolytic Uremic Syndrome

Olunye uvivinyo oluyisisekelo lungalawulwa ukuthola ukuthi ngabe amaseli egazi alimele noma umsebenzi wezinso wonakalisiwe:


I-CBC

Ukubalwa kwegazi okuphelele (CBC) kukala inani nobungako bama-RBC nama-platelets kusampula yegazi.

Okunye Ukuhlolwa Kwegazi

Ukuze uvivinye ukulahlekelwa umsebenzi wezinso, udokotela wakho angalawula ukuhlolwa kwe-BUN (okubheka imikhiqizo ephezulu ye-urea) kanye nokuhlolwa kwe-creatinine (ukufuna imikhiqizo esezingeni eliphakeme yemisipha). Imiphumela engajwayelekile ingakhombisa izinkinga zezinso.

Ukuhlolwa komchamo

Udokotela wakho uzofuna ukuhlola igazi noma amaprotheni emchameni wakho.

Isitoreji Sokulingisa

Amagciwane noma igazi esitokisini sakho kungasiza udokotela wakho ukuba ahlukanise imbangela yezimpawu zakho.

Uphathwa Kanjani I-Hemolytic Uremic Syndrome?

Imithi ejwayelekile ye-HUS ingafaka:

Ukubuyiselwa Kwe-Fluid

Ukwelashwa okuyisihluthulelo kwe-HUS ukushintshwa kuketshezi. Le ndlela yokwelashwa ingena esikhundleni se-electrolyte edingwa ngumzimba. Ama-electrolyte amaminerali afana ne-calcium, i-potassium ne-magnesium. Ukushintshwa kuketshezi futhi kwandisa ukugeleza kwegazi ngezinso ..Udokotela wakho uzokunika uketshezi olufakwa emithanjeni, kepha futhi angakukhuthaza ukuthi ukhuphule ukungena kwakho kuketshezi ngokuphuza amanzi amaningi noma izixazululo ze-electrolyte.

Ukumpontshelwa Igazi

Ukumpontshelwa igazi elibomvu kungadingeka uma unezinga eliphansi lama-RBC. Ukumpontshelwa igazi kwenziwa esibhedlela. Ukumpontshelwa kungakhulula izimpawu ezihambisana nokubalwa okuphansi kwe-RBC, njengokuphefumula okuncane nokukhathala okukhulu.

Lezi zimpawu ziyahambisana nokushoda kwegazi, isimo lapho umzimba wakho ungeke ukwazi ukukhiqiza amaseli abomvu egazi anele ukuhlinzeka izitho zomzimba ngeoksijini eyanele yokuqhuba imetabolism ejwayelekile. Lokhu kudalwe ukulahleka kwama-RBC’s.

Okunye Ukwelashwa

Udokotela wakho uzokususa kunoma imiphi imithi engaba imbangela eyinhloko ye-HUS.

Ukumpontshelwa kweplatelet kungadingeka uma unenani eliphansi leplatelet.

Ukushintshaniswa kweplasma kungenye indlela yokwelashwa, lapho udokotela wakho efaka khona iplasma yakho ngeplasma evela kumnikeli. Uzothola i-plasma enempilo yokuxhasa ukusakazwa kwamaseli abomvu egazi amasha nama-platelets.

Yiziphi izinkinga ezingaba khona zeHemolytic Uremic Syndrome?

Ezimweni ezimbi kakhulu uma izinso zakho zehlulekile, i-dialysis yezinso ingasetshenziselwa ukuhlunga imfucuza emzimbeni wakho. Lokhu ukwelashwa kwesikhashana kuze kube yilapho izinso zingasebenza ngokujwayelekile. Uma bengabuyisi umsebenzi ojwayelekile, ungadinga ukufakelwa izinso.

Izinkinga Zesikhathi Eside

Inkinga enkulu ye-HUS ukwehluleka kwezinso. Noma kunjalo, i-HUS nayo ingadala:

  • umfutho wegazi ophakeme
  • isifo sokuqaqamba kwamalunga
  • isimo sengqondo esishintshile
  • isithuthwane
  • isifo senhliziyo
  • unhlangothi
  • ikhoma

Ngenhlanhla, abantu abaningi bayakwazi ukululama ngokuphelele ku-HUS.

Uyini Umbono We-Hemolytic Uremic Syndrome?

I-HUS kungenzeka ibe yisimo esibi kakhulu. Kodwa-ke, kungenzeka ukuthi ululame ngokugcwele uma kutholakala ukuthi usesimweni sokuqala futhi uqale ukwelashwa khona manjalo. Shayela udokotela wakho noma kunini lapho uthuthukisa izimpawu ezikukhathazayo.

Ungakuvimbela Kanjani I-Hemolytic Uremic Syndrome?

Isizathu esivame kakhulu se-HUS ukutheleleka nge E. coli. Yize ungeke uwagwebe ngokuphelele la mabhaktheriya, unganciphisa ubungozi bokutheleleka ngo:

  • ukugeza izandla njalo
  • izitsha zokuwasha kahle
  • ukugcina izindawo zokulungiselela ukudla zihlanzekile
  • ukugcina ukudla okuluhlaza kwehlukile kokudla okulungele ukudliwa
  • ukukhipha inyama esiqandisini esikhundleni sokubala
  • ukungashiyi inyama ekamelweni lokushisa (lokhu kungadala ukukhula kwamagciwane).
  • ukupheka inyama iye kuma-degrees ama-Fahrenheit ayi-160 ukubulala amagciwane ayingozi
  • ukuwasha izithelo nemifino kahle
  • ukungabhukudi emanzini angcolile
  • ukugwema ukungenisa ujusi noma ubisi olungasetshenziswanga

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