Umlobi: John Stephens
Usuku Lokudalwa: 26 Ujanuwari 2021
Ukuvuselela Usuku: 1 Ujulayi 2024
Anonim
Konke Mayelana Ne-Antiphospholipid Syndrome (Hughes Syndrome) - Impilo
Konke Mayelana Ne-Antiphospholipid Syndrome (Hughes Syndrome) - Impilo

-Delile

Ukubuka konke

I-Hughes syndrome, eyaziwa nangokuthi "i-sticky syndrome" noma i-antiphospholipid syndrome (i-APS), yisimo sokuzilimaza esithinta indlela amangqamuzana akho egazi ahlangana ngayo, noma ahlanganiswe. I-Hughes syndrome ibhekwa njengengavamile.

Abesifazane abaphuphunyelwa yizisu ngokuphindaphindiwe kanye nabantu abanesifo sohlangothi ngaphambi kweminyaka engama-50 kwesinye isikhathi bathola ukuthi i-Hughes syndrome iyimbangela eyimbangela. Kulinganiselwa ukuthi i-Hughes syndrome ithinta abesifazane ngokuphindwe kathathu noma kahlanu kunabesilisa.

Yize imbangela ye-Hughes syndrome ingacacile, abacwaningi bakholelwa ukuthi ukudla, indlela yokuphila, kanye nezakhi zofuzo konke kungaba nomthelela ekuthuthukiseni lesi simo.

Izimpawu ze-Hughes syndrome

Izimpawu ze-Hughes syndrome kunzima ukuzibona, njengoba amahlule egazi akuyona into ongayibona kalula ngaphandle kwezinye izimo zempilo noma izinkinga. Ngezinye izikhathi i-Hughes syndrome ibangela ukuqubuka okubomvu noma ukuphuma kwegazi emakhaleni nasezinsinini zakho.

Ezinye izimpawu zokuthi ungaba ne-Hughes syndrome zifaka:

  • ukukhulelwa kwesisu okuphindayo noma ukuzala ingane ifile
  • amahlule egazi emilenzeni yakho
  • ukuhlaselwa kweschemic okudlulayo (i-TIA) (okufana nokushaywa unhlangothi, kepha ngaphandle kwemiphumela yaphakade ye-neurologic)
  • unhlangothi, ikakhulukazi uma ungaphansi kweminyaka engama-50
  • inani eliphansi leplatelet yegazi
  • isifo senhliziyo

Abantu abane-lupus abane-Hughes syndrome.


Ezimweni ezingavamile, i-Hughes syndrome engalashwa ingakhuphuka uma unezigameko zokujiya ngasikhathi sinye kuwo wonke umzimba. Lokhu kubizwa nge-antiphospholipid syndrome eyinhlekelele, futhi kungadala umonakalo omkhulu ezithweni zakho nasekufeni.

Izimbangela ze-Hughes syndrome

Abaphenyi basasebenza ukuqonda izimbangela zesifo i-Hughes. Kodwa bazimisele ukuthi kunesici sofuzo lapho kudlalwa khona.

I-Hughes syndrome ayidluliswanga ngqo ivela kumzali, ngendlela ezinye izimo zegazi, njenge-hemophilia, ezingaba ngayo. Kodwa ukuba nelungu lomndeni eline-Hughes syndrome kusho ukuthi kungenzeka ukuthi uthuthukise isimo.

Kungenzeka ukuthi isakhi sofuzo esixhunywe kwezinye izimo ezizimele naso senza i-Hughes syndrome. Lokho kuzochaza ukuthi kungani abantu abanalesi simo bavame ukuba nezinye izimo ezizimele.

Ukuba nezifo ezithile ezibangelwa amagciwane noma amagciwane, njenge E. coli noma i-parvovirus, ingadala i-Hughes syndrome ukuthi ikhule ngemuva kokuba isifo sesisuliwe. Imithi yokulawula isithuthwane, kanye nezindlela zokuvimbela inzalo ngomlomo, nazo zingadlala indima ekubangeleni lesi simo.


Lezi zinto zemvelo zingaphinde zihlanganyele nezinto zokuphila - njengokungazivocavoci ngokwanele nokudla ukudla okunamafutha amaningi - bese kubangela isifo i-Hughes.

Kepha izingane kanye nabantu abadala ngaphandle kwanoma yikuphi kwalokhu kutheleleka, izici zokuphila, noma ukusetshenziswa kwemithi basengathola i-Hughes syndrome nganoma yisiphi isikhathi.

Kudingeka izifundo eziningi ukuze kuxazululwe izimbangela zesifo i-Hughes.

Ukuxilongwa kwe-Hughes syndrome

I-Hughes syndrome itholakala ngochungechunge lwezivivinyo zegazi. Lokhu kuhlolwa kwegazi kuhlaziya amasosha omzimba owenziwa amaseli akho omzimba ukubona ukuthi aziphatha ngendlela ejwayelekile noma ngabe akhomba amanye amaseli aphilile.

Ukuhlolwa kwegazi okujwayelekile okukhomba i-Hughes syndrome kubizwa ngokuthi yi-antibody immunoassay. Ungadinga ukuthi kwenziwe eziningana zalezi zinto ukukhipha ezinye izimo.

I-Hughes syndrome ingaqondwa kahle njenge-multiple sclerosis ngoba lezi zimo ezimbili zinezimpawu ezifanayo. Ukuhlolwa okuphelele kufanele kunqume ukuxilongwa kwakho okulungile, kepha kungathatha isikhathi.


Ukwelashwa kwe-Hughes syndrome

I-Hughes syndrome ingalashwa ngama-thinner egazi (imithi enciphisa ubungozi bamahlule egazi).

Abanye abantu abane-Hughes syndrome abazivezi izimpawu zamahlule egazi futhi ngeke badinge noma yikuphi ukwelashwa okungaphezu kwe-aspirin ukuvimbela ubungozi bokuqina kwamahlule.

Imithi ye-Anticoagulant, efana ne-warfarin (i-Coumadin) ingabekwa, ikakhulukazi uma unomlando we-vein thrombosis ejulile.

Uma uzama ukuthwala ukukhulelwa isikhathi futhi une-Hughes syndrome, ungahle unikezwe i-aspirin yedosi ephansi noma umthamo wansuku zonke we-heparin egazini.

Abesifazane abane-Hughes syndrome banamathuba angamaphesenti angama-80 okuthwala ingane baye esikhaleni uma betholakele bese beqala ukwelashwa okulula.

Ukudla nokuvivinya umzimba kwe-Hughes syndrome

Uma kutholakala ukuthi une-Hughes syndrome, ukudla okunempilo kunganciphisa ubungozi bezinkinga ezikhona, njengokushaywa unhlangothi.

Ukudla ukudla okunothe izithelo nemifino futhi okunamafutha amancane noshukela kuzokunikeza uhlelo lwempilo yenhliziyo olunempilo, okwenza ukuba amahlule egazi abe mancane kakhulu.

Uma welapha i-Hughes syndrome nge-warfarin (i-Coumadin), iMayo Clinic ikweluleka ukuthi uhambisane nokuthi udla amavithamini K angakanani.

Yize inani elincane likavithamini K lingahle lingathinti ukwelashwa kwakho, ukwehluka njalo kokudla kwakho uvithamini K kungenza ukuthi ukusebenza kahle kwemithi yakho kuguquke ngendlela eyingozi. I-Broccoli, amahlumela eBrussels, ubhontshisi we-garbanzo, ne-avocado okunye kokudla okunevithamini K.

Ukuvivinya umzimba njalo kungaba yingxenye yokuphatha isimo sakho. Gwema ukubhema futhi ugcine isisindo esinempilo sohlobo lomzimba wakho ukugcina inhliziyo nemithambo yakho iqinile futhi imelana kakhulu nomonakalo.

Umbono

Kubantu abaningi abane-Hughes syndrome, izimpawu nezimpawu zingaphathwa ngama-thinner wegazi kanye nemithi yokulwa ne-anticoagulant.

Kunezimo ezithile lapho lezi zindlela zokwelapha zingasebenzi, futhi ezinye izindlela zidinga ukusetshenziselwa ukugcina igazi lakho linganqwabeki.

Uma ishiywe ingalashwa, i-Hughes syndrome ingalimaza isistimu yakho yenhliziyo futhi ikhulise ubungozi bezinye izimo zezempilo, njengokukhulelwa kwesisu nokushaywa unhlangothi. Ukwelashwa kwe-Hughes syndrome kungukuphila konke, ngoba alikho ikhambi lalesi simo.

Uma uke waba nokulandelayo, khuluma nodokotela wakho ngokuhlolelwa i-Hughes syndrome:

  • amahlule egazi angaphezu kwesisodwa aqinisekisa izinkinga
  • ukukhishwa kwesisu okukodwa noma ngaphezulu ngemuva kweviki le-10 lokukhulelwa
  • ukuphuphuma kwesisu okungathathu noma ngaphezulu ekuqaleni kwenyanga yokuqala yokukhulelwa

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