Umlobi: Laura McKinney
Usuku Lokudalwa: 10 Epreli 2021
Ukuvuselela Usuku: 1 Mhlawumbe 2024
Anonim
Hyperviscosity Syndrome | What Is The Cause?
Ividiyo: Hyperviscosity Syndrome | What Is The Cause?

-Delile

Yini i-hyperviscosity syndrome?

I-Hyperviscosity syndrome yisimo lapho igazi lingakwazi ukugeleza ngokukhululeka emithanjeni yakho.

Kulesi sifo, ukuvinjelwa kwemithambo yegazi kungenzeka ngenxa yamaseli abomvu amaningi kakhulu, amaseli amhlophe egazi, noma amaprotheni egazini lakho. Kungenzeka futhi nganoma yimaphi amangqamuzana egazi abomvu angajwayelekile, anjenge-sickle cell anemia.

I-Hyperviscosity yenzeka ezinganeni nakubantu abadala. Ezinganeni, kungathinta ukukhula kwazo ngokunciphisa ukugeleza kwegazi liye ezithweni ezibalulekile, njengenhliziyo, amathumbu, izinso nobuchopho.

Kubantu abadala, kungenzeka ngezifo ezizimele njenge-rheumatoid arthritis noma i-systemic lupus. Kungakhula futhi ngomdlavuza wegazi njenge-lymphoma ne-leukemia.

Ziyini izimpawu ze-hyperviscosity syndrome?

Izimpawu ezihambisana nalesi simo zifaka ikhanda elibuhlungu, ukuquleka, nethoni elibomvu esikhumbeni.

Uma ingane yakho ilele ngokungajwayelekile noma ingafuni ukondla ngokujwayelekile, lokhu kuyinkomba yokuthi kukhona okungahambi kahle.


Ngokuvamile, izimpawu ezihambisana nalesi simo zingumphumela wezinkinga ezenzeka lapho izitho ezibalulekile zingatholi i-oxygen eyanele ngegazi.

Ezinye izimpawu ze-hyperviscosity syndrome zifaka:

  • ukopha okungavamile
  • ukuphazamiseka okubukwayo
  • i-vertigo
  • ubuhlungu besifuba
  • ukuphelelwa umoya
  • ukudlikiza
  • ikhoma
  • ukuhamba kanzima

Yini ebangela i-hyperviscosity syndrome?

Lesi sifo sitholakala ezinganeni lapho izinga lamaseli abomvu egazi lingaphezu kwamaphesenti angama-65. Lokhu kungadalwa yizimo eziningi ezikhula ngesikhathi sokukhulelwa noma ngesikhathi sokuzalwa. Lokhu kungafaka:

  • ukubambezeleka kwesikhathi kwenkaba
  • izifo ezitholwa ngabazali
  • izimo zofuzo, njenge-Down syndrome
  • isifo sikashukela sokukhulelwa

Kungabangelwa futhi yizimo lapho kungenayo i-oxygen eyanele ehanjiswa ezicutshini ezisemzimbeni wengane yakho. I-twin-to-twin transfusion syndrome, isimo lapho amawele abelana ngokulinganayo ngegazi phakathi kwawo esibelethweni, kungaba esinye isizathu.


I-Hyperviscosity syndrome nayo ingadalwa yizimo ezithinta ukukhiqizwa kwamaseli egazi, kufaka phakathi:

  • i-leukemia, umdlavuza wegazi oholela kumaseli amhlophe amaningi kakhulu
  • polycythemia vera, umdlavuza wegazi oholela kumaseli abomvu amaningi kakhulu
  • i-thrombocytosis ebalulekile, isimo segazi esenzeka lapho umnkantsha ukhiqiza ama-platelet amaningi egazi
  • ukuphazamiseka kwe-myelodysplastic, iqembu lokuphazamiseka kwegazi elibangela izinombolo ezingajwayelekile zamaseli athile egazi, kuminyana amaseli aphilile emnkantsheni wethambo futhi kuvame ukuholela ekushoneni kwegazi okunzima

Kubantu abadala, i-hyperviscosity syndrome imvamisa idala izimpawu lapho i-viscosity yegazi iphakathi kuka-6 no-7, kulinganiswa ngokuhlobene nosawoti, kepha kungaba ngaphansi. Amanani ajwayelekile ngokuvamile aphakathi kuka-1.6 no-1.9.

Ngesikhathi sokwelashwa, inhloso ukwehlisa i-viscosity ezingeni elidingekayo ukuxazulula izimpawu zomuntu.

Ngubani osengozini ye-hyperviscosity syndrome?

Lesi simo sivame ukuthinta izinsana, kodwa futhi singakhula nasebudaleni. Inkambo yalesi simo incike embangela yayo:


  • Ingane yakho isengozini enkulu yokuthola le syndrome uma unomlando wayo womndeni.
  • Futhi, labo abanomlando wezimo ezinzima zomnkantsha basengozini enkulu yokuthola isifo se-hyperviscosity syndrome.

Sitholakala kanjani isifo se-hyperviscosity syndrome?

Uma udokotela wakho esola ukuthi usana lwakho lunalesi sifo, bazo-oda ukuhlolwa kwegazi ukuthola inani lamaseli abomvu egazini lengane yakho.

Okunye ukuhlolwa kungadingeka ukuthola ukuxilongwa. Lokhu kungafaka:

  • gcwalisa ukubalwa kwegazi (CBC) ukubheka zonke izingxenye zegazi
  • ukuhlolwa kwe-bilirubin ukuhlola izinga le-bilirubin emzimbeni
  • i-urinalysis ukukala ushukela, igazi, namaprotheni emchameni
  • ukuhlolwa ushukela egazini ukuhlola amazinga kashukela egazini
  • ukuhlolwa kwe-creatinine ukukala ukusebenza kwezinso
  • ukuhlolwa kwegesi yegazi ukuhlola amazinga oksijini egazini
  • ukuhlolwa komsebenzi wesibindi ukuhlola izinga lamaprotheni wesibindi
  • ukuhlolwa kwamakhemikhali egazi ukuhlola ibhalansi yamakhemikhali egazi

Futhi, udokotela wakho angathola ukuthi ingane yakho ibhekene nezinto ezinjenge-jaundice, ukwehluleka kwezinso, noma izinkinga zokuphefumula ngenxa yesifo.

Ngabe iphathwa kanjani i-hyperviscosity syndrome?

Uma udokotela wengane yakho enquma ukuthi ingane yakho ine-hyperviscosity syndrome, ingane yakho izobhekwa ngezinkinga ezingaba khona.

Uma isimo sinzima, udokotela wakho angancoma ukumpontshelwa okuyingxenye yokushintshaniswa. Phakathi nale nqubo, kususwa inani elincane legazi. Ngasikhathi sinye, inani elikhishiwe lishintshwa ngesisombululo sosawoti. Lokhu kwehlisa inani eliphelele lamaseli abomvu egazi, okwenza igazi libe lincane kakhulu, ngaphandle kokulahlekelwa ivolumu yegazi.

Udokotela wakho futhi angancoma ukuphakelwa okuthe xaxa kwengane yakho ukuze ithuthukise ukufuthwa kwamanzi nokunciphisa ukushuba kwegazi. Uma ingane yakho ingaphenduli ekuphakelweni, kungadingeka ukuthi ithole uketshezi ngemithambo.

Kubantu abadala, i-hyperviscosity syndrome ivame ukubangelwa yisimo esingaphansi njenge-leukemia. Isimo sidinga ukwelashwa kahle kuqala ukubona ukuthi lokhu kuthuthukisa i-hyperviscosity. Ezimweni ezinzima, i-plasmapheresis ingasetshenziswa.

Uyini umbono wesikhathi eside?

Uma ingane yakho inesifo esincane se-hyperviscosity syndrome futhi ingenazo izimpawu, kungenzeka zingadingi ukwelashwa ngokushesha. Kukhona ithuba elihle lokululama ngokugcwele, ikakhulukazi uma imbangela ibonakala ingeyesikhashana.

Uma imbangela ihlobene nesimo sofuzo noma isimo sokuthola ifa, kungadinga ukwelashwa kwesikhathi eside.

Ezinye izingane ezitholwe zinalesi sifo zinezinkinga zokukhula noma zemizwa ngokuhamba kwesikhathi. Lokhu ngokuvamile kungumphumela wokushoda kokugeleza kwegazi ne-oxygen ebuchosheni nakwezinye izitho ezibalulekile.

Xhumana nodokotela wengane yakho uma ubona noma yiziphi izinguquko ekuziphatheni kosana lwakho, amaphethini wokudla, noma amaphethini wokulala.

Izinkinga zingenzeka uma isimo sinzima kakhulu noma uma ingane yakho ingaphenduli ekwelashweni. Lezi zinkinga zingabandakanya:

  • unhlangothi
  • ukwehluleka kwezinso
  • kwehle ukulawulwa kwezimoto
  • ukulahlekelwa ukunyakaza
  • ukufa kwezicubu zamathumbu
  • isithuthwane esivela njalo

Qiniseka ukuthi ubika noma yiziphi izimpawu ingane yakho enazo kudokotela wazo ngokushesha.

Kubantu abadala, i-hyperviscosity syndrome ivame ukuhlobene nenkinga yezokwelapha eyisisekelo.

Ukuphathwa okufanele kwanoma yikuphi ukugula okuqhubekayo, kanye nokufaka okuvela kuchwepheshe wegazi, kuyizindlela ezingcono kakhulu zokunciphisa izinkinga ezivela kulesi simo.

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