Bartter's syndrome: kuyini, izimpawu eziyinhloko kanye nokwelashwa

-Delile

• Izimpawu eziyinhloko
• Yelashwa kanjani

I-Bartter's syndrome yisifo esingajwayelekile esithinta izinso futhi sidale ukulahleka kwe-potassium, i-sodium ne-chlorine emchameni. Lesi sifo sinciphisa ukuhlushwa kwe-calcium egazini futhi sandisa ukukhiqizwa kwe-aldosterone ne-renin, ama-hormone abandakanyeka ekulawuleni umfutho wegazi.

Isizathu seBartter's Syndrome ngesofuzo futhi yisifo esidlula sisuka kubazali siye ezinganeni, sithinta abantu kusukela ebuntwaneni. Lesi sifo asinalo ikhambi, kepha uma sitholakale kusenesikhathi, singalawulwa ngemithi nangamaphilisi amaminerali.

Izimpawu eziyinhloko

Izimpawu zeBartter's Syndrome zivela ebuntwaneni, lezo eziyinhloko:

• Ukungondleki kahle;
• Ukubambezeleka kokukhula;
• Ubuthakathaka bemisipha;
• Ukuwohloka kwengqondo;
• Ukwanda kwevolumu yomchamo;
• Ukoma kakhulu;
• Ukwehla kwamanzi emzimbeni;
• Imfiva;
• Uhudo noma ukuhlanza.

Abantu abaneBartter's Syndrome banamazinga aphansi e-potassium, i-chlorine, i-sodium ne-calcium egazini labo, kodwa abanalo ushintsho emazingeni omfutho wegazi. Abanye abantu bangaba nezici zomzimba eziphakamisa lesi sifo, njengobuso obunxantathu, ibunzi elivelele kakhulu, amehlo amakhulu nezindlebe ezibheke phambili.

Ukuxilongwa kweBartter's Syndrome kwenziwa ngudokotela wezifo zomchamo, ngokuhlola izimpawu zesiguli nokuhlolwa kwegazi okuthola amazinga angajwayelekile ekugxileni kwe-potassium namahomoni, njenge-aldosterone ne-renin.

Yelashwa kanjani

Ukwelashwa kwe-Bartter's Syndrome kwenziwa ngokusetshenziswa kwama-potassium supplements noma amanye amaminerali, afana ne-magnesium noma i-calcium, ukukhulisa ukugcwala kwalezi zinto egazini, nokungenisa uketshezi oluningi, ukukhokhela ukulahleka okukhulu kwamanzi umchamo.

Izindlela zokwelapha ezondla i-potassium, njenge-spironolactone, nazo ziyasetshenziswa ekwelapheni lesi sifo, kanye nezidakamizwa ezingezona ukuvuvukala ezifana ne-indomethacin, okumele ithathwe kuze kube sekupheleni kokukhula ukuze ikwazi ukuthuthukisa ukukhula komuntu .

Iziguli kufanele zihlolwe umchamo, igazi nezinso ze-ultrasound. Lokhu kwenzelwa ukuqapha ukusebenza kwezinso nezindlela zesisu, ukuvimbela imiphumela yokwelashwa kulezi zitho.