Yini futhi kanjani ukuxilonga i-Ohtahara syndrome

-Delile

• Ungakuqinisekisa kanjani ukuxilongwa
• Yelashwa kanjani
• Yini ebangela lesi sifo

I-Ohtahara syndrome luhlobo olungavamile lwesifo sokuwa esivame ukuvela ezinganeni ezingaphansi kwezinyanga ezintathu ubudala, ngakho-ke yaziwa nangokuthi i-infantile epileptic encephalopathy.

Ukuquleka kokuqala kwalolu hlobo lwesifo sokuwa kuvame ukwenzeka phakathi ne-trimester yokugcina yokukhulelwa, kusengaphakathi kwesibeletho, kepha futhi kungavela phakathi nezinsuku zokuqala eziyishumi zokuphila kwengane, kubonakala ngezinciphiso zemisipha ezingazimisele ezishiya imilenze nezingalo ziqinile imizuzwana ethile.

Yize lungekho ikhambi, ukwelashwa kungenziwa ngokusetshenziswa kwezidakamizwa, i-physiotherapy kanye nokudla okwanele ukuze kuvinjelwe ukuqala kwezinkinga futhi kuthuthukise ikhwalithi yempilo yengane.

Ungakuqinisekisa kanjani ukuxilongwa

Kwezinye izimo, i-Ohtahara's syndrome ingatholwa udokotela wezingane kuphela ngokubheka izimpawu nokuhlola umlando wengane.

Kodwa-ke, udokotela futhi anga-oda i-electroencephalogram, okuwukuhlolwa okungenabuhlungu, okulinganisa ukusebenza kobuchopho ngesikhathi sokubanjwa. Funda kabanzi mayelana nokuthi lokhu kuhlolwa kwenziwa kanjani.

Yelashwa kanjani

Uhlobo lokuqala lokwelashwa olukhonjiswe ngudokotela wezingane, imvamisa ukusetshenziswa kwamakhambi okulwa nesifo sokuwa, njengeClonazepam noma iTopiramate, ukuzama ukulawula ukuqala kwezinkinga, noma kunjalo, le mithi ingakhombisa imiphumela emincane, ngakho-ke, kusanconywa ezinye izindlela zokwelashwa, kufaka phakathi:

• Ukusetshenziswa kwama-corticosteroids, nge-corticotrophin noma i-prednisone: ukunciphisa inani lokuquleka kwezinye izingane;
• Ukuhlinzwa Kwesithuthwane: isetshenziswa ezinganeni lapho ukuquleka kubangelwa indawo ethile yobuchopho futhi kwenziwa ngokususwa kwaleyo ndawo, inqobo nje uma kungabalulekile ekusebenzeni kobuchopho;
• Ukudla ukudla okune-ketogenic: ingasetshenziswa kuzo zonke izimo ukugcwalisa ukwelashwa futhi iqukethe ukuqeda ukudla okunothe kuma-carbohydrate ekudleni, njengesinkwa noma i-pasta, ukuze kulawulwe ukuqala kokuquleka. Bona ukuthi yikuphi ukudla okuvunyelwe nokuvinjelwe kulolu hlobo lokudla.

Yize ukwelashwa kubaluleke kakhulu ukuthuthukisa ikhwalithi yempilo yengane, kunezimo eziningi lapho i-Ohtahara's syndrome iba yimbi ngokuhamba kwesikhathi, idale ukubambezeleka kokukhula kwengqondo nokuthuthuka kwezimoto. Ngenxa yalolu hlobo lwezinkinga, isikhathi sokuphila siphansi, cishe iminyaka emibili.

Yini ebangela lesi sifo

Isizathu se-Ohtahara's syndrome kunzima ukusibona ezimweni eziningi, kepha-ke, izinto ezimbili ezibonakala sengathi zivela lapho kuvela khona lesi sifo yizinguquko zofuzo ngesikhathi sokukhulelwa nokungasebenzi kahle kobuchopho.

Ngakho-ke, ukuzama ukunciphisa ubungozi balolu hlobo lwesifo, umuntu kufanele agweme ukukhulelwa ngemuva kweminyaka engama-35 futhi alandele zonke izincomo zikadokotela, njengokugwema ukuphuza utshwala, ukungabhemi, ukugwema ukusetshenziswa kwezidakamizwa ezingekho emthethweni nokubamba iqhaza ekubonisaneni ngaphambi kokubeletha, isibonelo. Qonda zonke izimbangela ezingaholela ekukhulelweni okuyingozi.