Umlobi: Roger Morrison
Usuku Lokudalwa: 18 Usepthemba 2021
Ukuvuselela Usuku: 1 Ujulayi 2024
Anonim
I-Shy-Drager syndrome: kuyini, izimpawu nokwelashwa - Impilo
I-Shy-Drager syndrome: kuyini, izimpawu nokwelashwa - Impilo

-Delile

I-Shy-Drager syndrome, ebizwa nangokuthi "multiple system atrophy with orthostatic hypotension" noma i- "MSA" iyimbangela engajwayelekile, engathi sína nengaziwa, ebonakala ngokuwohloka kwamangqamuzana ohlelweni lwezinzwa oluphakathi noluzimele, olulawula imisebenzi izinguquko ezingahlangene umzimba.

Uphawu olukhona kuzo zonke izimo, ukwehla komfutho wegazi lapho umuntu esukuma noma elele phansi, noma kunjalo abanye bangabandakanyeka futhi ngenxa yalesi sizathu ihlukaniswe yizinhlobo ezi-3, umehluko wayo:

  • I-Parkinsonian shy-drager syndrome: iveza izimpawu zesifo sika-Parkinson, njengokuthi, lapho ukunyakaza kuhamba kancane, ukuqina kwemisipha nokuthuthumela;
  • I-Cerebellar shy-drager syndrome: ukungahambisani kahle kwezimoto, ubunzima bokulinganisa nokuhamba, ukugxila kumbono, ukugwinya nokukhuluma;
  • I-Shy-drager syndrome ehlanganisiwe: ihlanganisa amafomu e-parkinsonia ne-cerebellar, ngokuba nzima kakhulu kunakho konke.

Yize izimbangela zingaziwa, kunokusola ukuthi i-shy-drager syndrome izuzwe njengefa.


Izimpawu eziyinhloko

Izimpawu eziyinhloko ze-Shy-Drager syndrome yilezi:

  • Nciphisa inani lezithukuthuku, izinyembezi namathe;
  • Kunzima ukubona;
  • Kunzima ukuchama;
  • Ukuqunjelwa;
  • Ukungabi namandla ocansini;
  • Ukungabekezelelani kokushisa;
  • Ukulala okungenakuphumula.

Lesi sifo sivame kakhulu emadodeni ngemuva kweminyaka engama-50. Futhi ngenxa yokuthi ayinazo izimpawu ezithile, kungathatha iminyaka ukufinyelela ekuxilongweni okulungile, ngaleyo ndlela kubambezeleke ukwelashwa okufanele, okuthi, yize kungalapheki, kusize ukuthuthukisa ikhwalithi yempilo yomuntu.

Ukuxilongwa kwenziwa kanjani

I-syndrome ivame ukuqinisekiswa nge-scan ye-MRI ukubona ukuthi yiziphi izinguquko ubuchopho obungahle bube nazo. Kodwa-ke, okunye ukuhlolwa kungenziwa ukuhlola imisebenzi engazibandakanyi yomzimba, njengokulinganisa ukucindezelwa kwegazi ukulala nokuma, ukuhlolwa kwezithukuthuku ukuhlola ukujuluka, isinye nesisu, ngaphezu kwe-electrocardiogram ukulandelela izimpawu zikagesi ezisuka enhliziyweni.


Yelashwa kanjani

Ukwelashwa kwe-Shy-Drager syndrome kuqukethe ukukhulula izimpawu eziveziwe, njengoba lesi sifo singelapheki. Imvamisa kufaka ukusetshenziswa kwemithi efana ne-seleginin, ukunciphisa ukukhiqizwa kwe-dopamine ne-fludrocortisone ukwandisa umfutho wegazi, kanye ne-psychotherapy ukuze umuntu akwazi ukubhekana kangcono nezikhathi zokuxilongwa nezomzimba, ukugwema ukulahleka kwemisipha.

Ngaphezu kokusiza ekunciphiseni izimpawu, kungavezwa izinyathelo zokuqapha ezilandelayo:

  • Ukumiswa kokusebenzisa isisu;
  • Phakamisa ikhanda lombhede;
  • Ukuhlala endaweni yokulala;
  • Ukusetshenziswa kasawoti okwandisiwe;
  • Sebenzisa amabhande okunwebeka ezithweni ezingezansi nasesiswini, ukunciphisa ukungakhululeki okubangelwa ukundindizela.

Kubalulekile ukuqaphela ukuthi ukwelashwa kwe-Shy-Drager Syndrome kwenzelwa ukuthi umuntu akwazi ukuthola induduzo enkulu, ngoba ayisivimbi ukuqhubeka kwesifo.

Ngoba kuyisifo okunzima ukuselapha futhi siyathuthuka emvelweni, kujwayelekile ukuthi ukufa kubangelwe yizinkinga zenhliziyo noma zokuphefumula, kusuka eminyakeni engu-7 kuye kwengu-10 ngemuva kokuqala kwezimpawu.


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