Umlobi: Tamara Smith
Usuku Lokudalwa: 26 Ujanuwari 2021
Ukuvuselela Usuku: 2 Ujuni 2025
Anonim
Injani ukwelashwa kwe-hemophilia - Impilo
Injani ukwelashwa kwe-hemophilia - Impilo

-Delile

Ukwelashwa kwe-hemophilia kwenziwa ngokufaka esikhundleni izakhi ezijiyayo ezingenamuntu, okuyi-factor VIII, esimweni sohlobo lwe-hemophilia A, ne-factor IX, esimweni sohlobo lwe-hemophilia B, njengoba kungenzeka ukuvimbela ukopha ngokweqile.

I-Hemophilia yisifo sofuzo lapho kuncipha khona ukusebenza noma ukungabikho kwezinto ezijiyisayo, okungamaprotheni akhona egazini asebenza lapho kuqhekeka isitsha segazi, esivimbela ukopha ngokweqile. Ngakho-ke, lapho usebenzisa ukushintshwa kwezinto ezijiyisayo, kungenzeka ukuthi umuntu one-hemophilia aphile impilo ejwayelekile, ngaphandle kwemikhawulo eminingi. Funda kabanzi nge-hemophilia.

Izinhlobo zokwelashwa

Yize lungekho ikhambi, ukwelashwa kwe-hemophilia kusiza ukuvimbela ukopha ukuthi kungenzeki kaningi, futhi kufanele kuqondiswe yi-hematologist futhi kungenziwa ngezindlela ezimbili ezihlukene:


  • Ukwelashwa kokuvimbela: iqukethe ukushintshwa kwezinto ezijiyayo ngezikhathi ezithile, ukuze zihlale zikhuphukile emzimbeni, futhi zivimbele ukopha okungaba khona. Lolu hlobo lokwelashwa lungahle lungadingeki ezimweni ze-haemophilia emnene, futhi kunganconywa ukuthi ukwelashwa kuphela uma kukhona uhlobo oluthile lokopha.
  • Ukwelashwa ngemuva kokopha: kuyindlela yokwelashwa okufunwayo, eyenziwe kuzo zonke izimo, ngokusetshenziswa kwe-clotting factor concentrate lapho kunesiqephu esopha, esivumela ukuthi sixazululwe ngokushesha okukhulu.

Kunoma ikuphi ukwelashwa, amanani kufanele abalwe ngokwesisindo somzimba, ubunzima be-hemophilia kanye namazinga womsebenzi wokujiya umuntu ngamunye egazini lakhe. I-Factor VIII noma i-IX igxila kuqukethe i-ampoule eyimpuphu ehlanjululwa ngamanzi acolisisiwe ukuze isetshenziswe.

Ngaphezu kwalokho, ezinye izinhlobo ze-hemostatic agent concentrates zingasetshenziswa ukusiza ekuhlanganiseni, njenge-cryoprecipitate, prothrombin complex kanye ne-desmopressin, ngokwesibonelo. Lezi zindlela zokwelashwa zenziwa mahhala yi-SUS, ezikhungweni ze-hematology zombuso, ngokumane udluliselwe ngudokotela ojwayelekile noma i-hematologist.


Ukwelashwa ezimweni ze-hemophilia ene-inhibitor

Amanye ama-hemophiliacs angakha amasosha omzimba aphikisana ne-factor VIII noma i-IX concentrate esetshenziselwa ukwelashwa, ebizwa ngama-inhibitors, engaphazamisa impendulo yokwelashwa.

Kulezi zimo, kungadingeka ukwenza ukwelashwa ngamanani aphezulu, noma ngokuhlanganiswa kwezinye izingxenye zegazi ezijiyayo.

Ukunakekelwa ngesikhathi sokwelashwa

Abantu abane-hemophilia kufanele bathathe lezi zinyathelo zokuphepha ezilandelayo:

  • Prakthiza imisebenzi yomzimba, ukuqinisa imisipha namalunga, ukunciphisa amathuba wokopha. Kodwa-ke, kubalulekile ukugwema ukuthinteka kwezemidlalo noma ukuthintana komzimba okunodlame;
  • Bheka ukuvela kwezimpawu ezintsha, ikakhulukazi ezinganeni, nokwehla ngokwelashwa;
  • Yiba nemithi njalo, ikakhulukazi uma kwenzeka kuhamba;
  • Yiba nomazisi, njengesongo, elibonisa lesi sifo, ngezimo eziphuthumayo;
  • Yazisa ngesimo lapho wenza noma iyiphi inqubo, njengokufaka umuthi wokugoma, ukuhlinzwa kwamazinyo noma izinqubo zokwelashwa;
  • Gwema imishanguzo eyenza ukopha, njenge-aspirin, anti-inflammatories kanye nama-anticoagulants, isibonelo.

Ngaphezu kwalokho, ukwelashwa ngokomzimba kufanele futhi kube yingxenye yokwelashwa kwe-hemophilia, njengoba kukhuthaza ukusebenza kwezimoto okuthuthukile, kunciphisa ubungozi bezinkinga, njenge-acute hemolytic synovitis, okuwukuvuvukala kokuhlangana ngenxa yokopha, futhi kuthuthukisa ithoni yemisipha, ngakho-ke kunganciphisa ngisho nesidingo sokuthatha izinto zokuvala igazi futhi kuthuthukise ikhwalithi yempilo.


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