Ukwelashwa kwe-nemaline myopathy

-Delile

• Izimpawu ze-nemaline myopathy
• Izimpawu zokuthuthuka ku-nemaline myopathy
• Izimpawu zokuwohloka kwe-nemaline myopathy

Ukwelashwa kwe-nemaline myopathy kufanele kuqondiswe udokotela wezingane, esimweni sengane nengane, noma ngudokotela wamathambo, esimweni somuntu omdala, esenzelwe ukwelapha lesi sifo, kepha ukukhulula nokwelapha izimpawu, ukuthuthuka izinga lempilo.

Imvamisa, ukwelashwa kuqalwa ngezikhathi ze-physiotherapy ukusiza ukuqinisa imisipha ebuthakathaka ngokwenza izivivinyo ezithile eziguqulwe yi-physiotherapist.

Ngaphezu kwalokho, futhi ngokuya ngezimpawu ezingavela, ukwelashwa kungenziwa futhi nge:

• Ukusetshenziswa kwe-CPAP: kungumshini onesifihla-buso esisetshenziswa ezimeni ezilinganiselayo nezinzima ukusiza ukuphefumula, ikakhulukazi ngesikhathi sokulala. Funda kabanzi ku: CPAP;
• Ukusetshenziswa kwesihlalo esinamasondo: kuyadingeka ezimweni ze-nemaline myopathy ezibangela ubunzima bokuhamba ngenxa yobuthakathaka bemisipha yomlenze;
• Ukubekwa kwethumbu le-gastrostomy: siqukethe ithubhu elincane elifakwa ngqo esiswini elivumela ukondliwa ezimweni ezinzima kakhulu;
• Ukutholwa kwama-antibiotic: zisetshenziswa kwezinye izimo ukwelapha izifo zokuphefumula, ezifana ne-pneumonia, ezivame ukwenzeka ngenxa yezinkinga zokuphefumula ezibangelwa i-myopathy.

Ezimweni ezinzima kakhulu, kungadingeka ukuhlala esibhedlela ukuze uthole ukwelashwa okufanele futhi ugweme izinkinga ezinkulu, ezifana nokuboshwa ngokuphefumula, okubeka engozini impilo yesiguli.

Izimpawu ze-nemaline myopathy

Izimpawu eziyinhloko ze-nemaline myopathy zifaka:

• Ubuthakathaka bemisipha, ikakhulukazi ezingalweni nasemilenzeni;
• Ukuphefumula kanzima noma ukugwinya;
• Ukubambezeleka kwentuthuko;
• Kunzima ukuhamba.

Ngaphezu kwalezi zimpawu, kujwayelekile nokuthi ezinye izici zivele, njengobuso obuncane, umzimba omncane, ukubukeka komlomo ovulekile, unyawo olungenalutho, isifuba esijulile kanye nokukhula kwesifo sokuqaqamba kwamalunga omzimba noma kwamathambo.

Izimpawu zivame ukuvela ngemuva nje kokuzalwa ngoba yisifo sofuzo, kepha kwezinye izimo, izimpawu zokuqala zingakhula kuphela lapho usumdala.

O ukuxilongwa kwe-myopathy ye-nemalitic kwenziwa nge-biopsy yemisipha lapho kunezimpawu zokusola kwalesi sifo, ikakhulukazi lapho ukubambezeleka kokukhula kanye nobuthakathaka obungapheli bemisipha buvela.

Izimpawu zokuthuthuka ku-nemaline myopathy

Azikho izimpawu zokuthuthuka ku-nemaline myopathy, njengoba lesi sifo singathuthuki. Kodwa-ke, izimpawu zingalungiswa ngokwelashwa, okuvumela impilo engcono.

Izimpawu zokuwohloka kwe-nemaline myopathy

Izimpawu zokuwohloka kwe-nemaline myopathy zihlobene nezinkinga, ezifana nokutheleleka nokuboshwa ngokuphefumula, ngakho-ke kufaka phakathi umkhuhlane ongaphezu kuka-38ºC, ubunzima bokuphefumula, ukuphefumula okungajulile, iminwe eluhlaza okwesibhakabhaka nobuso.