Isifo seVon Hippel-Lindau

-Delile
- Isifinyezo
- Siyini isifo seVon Hippel-Lindau (VHL)?
- Yini ebangela isifo seVon Hippel-Lindau (VHL)?
- Ziyini izimpawu zesifo iVon Hippel-Lindau (VHL)?
- Sitholakala kanjani isifo seVon Hippel-Lindau (VHL)?
- Yiziphi izindlela zokwelapha isifo seVon Hippel-Lindau (VHL)?
Isifinyezo
Siyini isifo seVon Hippel-Lindau (VHL)?
Isifo iVon Hippel-Lindau (VHL) yisifo esingajwayelekile esidala ukuthi izimila nama-cysts zikhule emzimbeni wakho. Zingakhula ebuchosheni bakho nakumgogodla, izinso, amanyikwe, izindlala ze-adrenal, kanye nomgudu wokuzala. Izimila zivame ukuba nobungozi (hhayi umdlavuza). Kodwa ezinye izicubu, njengalezo ezisezinso nasezinyikeni, zingaba nomdlavuza.
Yini ebangela isifo seVon Hippel-Lindau (VHL)?
Isifo iVon Hippel-Lindau (VHL) yisifo sofuzo. Izuzwe njengefa, okusho ukuthi idluliselwa kusuka kumzali iye enganeni.
Ziyini izimpawu zesifo iVon Hippel-Lindau (VHL)?
Izimpawu ze-VHL zixhomeke kubukhulu nasendaweni yamathumba. Zingafaka
- Ukuphathwa ikhanda
- Izinkinga ngokulinganisela nokuhamba ngezinyawo
- Isiyezi
- Ubuthakathaka bezitho
- Izinkinga zombono
- Umfutho wegazi ophezulu
Sitholakala kanjani isifo seVon Hippel-Lindau (VHL)?
Ukuthola nokwelapha i-VHL kusenesikhathi kubalulekile. Umhlinzeki wakho wezokunakekelwa kwempilo angasola ukuthi une-VHL uma unamaphethini athile ama-cysts nezicubu. Kukhona ukuhlolwa kofuzo kweVHL.Uma unayo, uzodinga ezinye izivivinyo, kufaka phakathi ukuhlolwa kwe-imaging, ukubheka izicubu nama-cysts.
Yiziphi izindlela zokwelapha isifo seVon Hippel-Lindau (VHL)?
Ukwelashwa kungahlukahluka, kuya ngendawo nosayizi wamathumba nama-cysts. Ngokuvamile kuhilela ukuhlinzwa. Izicubu ezithile zingaphathwa ngokwelashwa ngemisebe. Umgomo ukwelapha ukukhula ngenkathi kuncane nangaphambi kokulimala unomphela. Uzodinga ukuqapha ngokucophelela udokotela kanye / noma neqembu lezokwelapha elijwayele lesi sifo.
I-NIH: Isikhungo Sikazwelonke Sokukhubazeka Kwezinzwa NeStroke