Isifo se-veno-occlusive isifo

I-pulmonary veno-occlusive disease (i-PVOD) isifo esingajwayelekile kakhulu. Kuholela kumfutho wegazi ophakeme emithanjeni yamaphaphu (i-pulmonary hypertension).

Ezimweni eziningi, imbangela ye-PVOD ayaziwa. Umfutho wegazi ophakeme wenzeka emithanjeni yamaphaphu. Le mithambo yamaphaphu ixhunywe ngqo ohlangothini lokunene lwenhliziyo.

Isimo singase sihlobane nokutheleleka ngegciwane. Kungenzeka njengokuxakeka kwezifo ezithile ezifana ne-lupus, noma ukufakelwa umnkantsha wethambo.

Lesi sifo sivame kakhulu ezinganeni nasebancane. Njengoba lesi sifo siba sibi kakhulu, sibanga:

• Imithambo emincane yamaphaphu
• Umfutho wegazi ophakeme we-pulmonary
• Ukuminyana nokuvuvukala kwamaphaphu

Izici ezingaba yingozi ze-PVOD zifaka:

• Umlando womndeni walesi simo
• Ukubhema
• Ukuvezwa kwezinto ezinjenge-trichlorethylene noma imithi ye-chemotherapy
• I-systemic sclerosis (ukuphazamiseka kwesikhumba okuzenzakalelayo)

Izimpawu zingafaka noma yikuphi okulandelayo:

• Ukuphelelwa umoya
• Ukukhwehlela okomile
• Ukukhathala ngokuzikhandla
• Ukuquleka
• Akhwehlele igazi
• Kunzima ukuphefumula ngenkathi ulele phansi

Umhlinzeki wezokunakekelwa kwempilo uzokuhlola abuze ngomlando nezimpawu zakho zezokwelapha.

Isivivinyo singaveza:

• Ukwanda kwengcindezi emithanjeni yentamo
• Ukushayisana kweminwe
• Umbala we-Bluish wesikhumba ngenxa yokushoda komoya-mpilo (i-cyanosis)
• Ukuvuvukala emilenzeni

Umhlinzeki wakho angezwa imisindo yenhliziyo engajwayelekile lapho elalele isifuba namaphaphu nge-stethoscope.

Ukuhlolwa okulandelayo kungenziwa:

• Imithambo yegazi yegazi
• I-oximetry yegazi
• I-x-ray yesifuba
• Isifuba CT
• I-catheterization yenhliziyo
• Ukuhlolwa kwemisebenzi yamaphaphu
• I-Echocardiogram
• I-biopsy yamaphaphu

Okwamanje alukho umuthi wokwelashwa osebenzayo owaziwayo. Kodwa-ke, le mithi elandelayo ingaba wusizo kwabanye abantu:

• Imithi enweba imithambo yegazi (vasodilators)
• Imithi elawula ukuphendula kwamasosha omzimba (njenge-azathioprine noma i-steroids)

Ukufakelwa kwamaphaphu kungadingeka.

Umphumela uvame ukuba mubi kakhulu ezinganeni, ngesilinganiso sokusinda kwamasonto ambalwa nje. Ukusinda kubantu abadala kungaba izinyanga kuye eminyakeni embalwa.

Izinkinga ze-PVOD zingafaka:

• Kunzima ukuphefumula okuya kuba kubi kakhulu, kufaka phakathi nasebusuku (i-apnea yokulala)
• Umfutho wegazi ophezulu wamaphaphu
• Ukwehluleka kwenhliziyo emaceleni angakwesokudla (cor pulmonale)

Shayela umhlinzeki wakho uma unezimpawu zalesi sifo.

Isifo se-pulmonary vaso-occlusive

• Uhlelo lokuphefumula

UChin K, uChannick RN. Umfutho wegazi ophezulu wamaphaphu. Ku: Broaddus VC, Mason RJ, Ernst JD, et al, abakwa-eds. Incwadi kaMurray neNadel Yemithi Yokuphefumula. Umhlaka 6.IPhiladelphia, PA: Elsevier Saunders; 2016: isahluko 58.

UChurg A, uWright JL. Umfutho wegazi ophezulu wamaphaphu. Ku: Leslie KO, Wick MR, ama-eds. I-Pathology yePulmonary Pathology: Indlela Yokuxilonga. 3rd ed. IPhiladelphia, PA: Elsevier; 2018: isahluko 12.

UMclaughlin VV, uHumbert M. Pulmonary hypertension. Ku: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, ama-eds. Isifo Senhliziyo SikaBraunwald: Incwadi Yemithi Yezinhliziyo Nemithambo. Umhla ka-11. IPhiladelphia, PA: Elsevier; 2019: isahluko 85.