I-acid mucopolysaccharides

I-acid mucopolysaccharides isivivinyo esilinganisa inani lama-mucopolysaccharides akhishwe emchameni kungaba phakathi nesiqephu esisodwa noma ngaphezu kwesikhathi samahora angama-24.

AmaMucopolysaccharides ngamaketanga amade amangqamuzana kashukela emzimbeni. Zivame ukutholakala ku-mucus nakuluketshezi oluzungeze amalunga.

Ukuhlolwa kwamahora angama-24, kufanele uchamele esikhwameni noma esitsheni esikhethekile njalo lapho usebenzisa indlu yangasese. Imvamisa, uzonikezwa iziqukathi ezimbili. Uzochama uqonde ngqo esitsheni esincane esikhethekile bese udlulisela lowo mcolo kwesinye isitsha esikhulu.

• Ngosuku lokuqala, chamela endlini yangasese lapho uvuka ekuseni.
• Ngemuva kokuchama kokuqala, chamela esitsheni esikhethekile njalo lapho usebenzisa indlu yokugezela amahora angama-24 alandelayo. Dlulisa umchamo esitsheni esikhulu bese ugcina isitsha esikhulu endaweni epholile noma esiqandisini. Gcina lesi sitsha sivalekile.
• Ngosuku lwesi-2, chama ungene esitsheni ekuseni futhi lapho uvuka bese udlulisela lo mchamo esitsheni esikhulu.
• Faka ilebula esitsheni esikhudlwana ngegama lakho, usuku, isikhathi sokuphothula, bese usibuyisela njengokuyalelwe.

Okosana:

Geza kahle indawo ezungeze umchamo (umgodi lapho kuphuma khona umchamo). Vula isikhwama sokuqoqa umchamo (isikhwama sepulasitiki esinephepha lokunamathisela ekugcineni).

• Kwabesilisa, faka wonke umthondo esikhwameni bese unamathisela iphepha lokunamathisela esikhunjeni.
• Kwabesifazane, beka isikhwama phezu kwamafolda amabili esikhumba ohlangothini lwesitho sangasese sowesifazane (i-labia). Beka inabukeni enganeni (ngaphezu kwesikhwama).

Hlola usana kaningi, bese ushintsha isikhwama ngemuva kokuthi usana seluchamile. Khipha umchamo esikhwameni ungene esitsheni esihlinzekwe ngumhlinzeki wakho wezokunakekelwa kwempilo.

Izingane ezisebenzayo zingasusa isikhwama, zidale ukuthi umchamo ungene emanabukeni. Ungadinga izikhwama zokuqoqa ezengeziwe.

Uma usuqedile, ilebula isitsha bese usibuyisela njengoba utsheliwe.

Akukho ukulungiselela okukhethekile okudingekayo.

Isivivinyo sihilela ukuchama okujwayelekile kuphela, futhi akukho ukungaphatheki kahle.

Lokhu kuhlolwa kwenzelwa ukuxilonga iqembu elingajwayelekile lokuphazamiseka kofuzo okubizwa nge-mucopolysaccharidoses (MPS). Lokhu kufaka phakathi, i-Hurler, Scheie, ne-Hurler / Scheie syndromes (MPS I), i-Hunter syndrome (i-MPS II), i-Sanfilippo syndrome (i-MPS III), i-Morquio syndrome (i-MPS IV), i-Maroteaux-Lamy syndrome (i-MPS VI), ne-Sly syndrome (MPS VII).

Isikhathi esiningi, lokhu kuhlolwa kwenziwa ezinganeni ezingaba nesifo noma umlando womndeni ngesinye salezi zinkinga.

Amazinga ajwayelekile ahlukahluka ngobudala nakulebhu kuya kubhu. Khuluma nomhlinzeki wakho mayelana nencazelo yemiphumela yakho ethile yokuhlolwa.

Amazinga aphakeme ngokungajwayelekile angahambisana nohlobo lwe-mucopolysaccharidosis. Ukuhlolwa okuqhubekayo kuyadingeka ukuthola uhlobo oluthile lwe-mucopolysaccharidosis.

AMP; I-Dermatan sulfate - umchamo; Umchamo i-heparan sulfate; Umchamo dermatan sulfate; I-Heparan sulfate - umchamo

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I-Spranger JW. I-Mucopolysaccharidoses. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Incwadi kaNelson Yezingane. Umhlaka 21. IPhiladelphia, PA: Elsevier; 2020: isahluko 107.

I-Turnpenny PD, u-Ellard S. Amaphutha wokuzalwa we-metabolism. Ku: Turnpenny PD, Ellard S, eds. Izinto ze-Emergy ze-Medical Genetics. Umhla ka-15. IPhiladelphia, PA: Elsevier; 2017: isahluko 18.