Ama-Fuchs dystrophy

I-Fuchs (ebizwa ngokuthi "ama-fooks") i-dystrophy yisifo samehlo lapho amangqamuzana ahlanganisa ingaphakathi le-cornea kancane kancane eqala ukufa. Lesi sifo sihlasela kakhulu amehlo womabili.

Ama-fuchs dystrophy angazuzwa njengefa, okusho ukuthi angadluliselwa kusuka kubazali kuye ezinganeni. Uma omunye wabazali bakho enalesi sifo, unamathuba angama-50% okuba nalesi sifo.

Kodwa-ke, lesi simo kungenzeka futhi kubantu abangenawo umlando womndeni owaziwayo wesifo.

I-Fuchs dystrophy ivame kakhulu kwabesifazane kunabesilisa. Izinkinga zombono aziveli ngaphambi kweminyaka yobudala engama-50 ezimweni eziningi. Kodwa-ke, umhlinzeki wezokunakekelwa kwempilo angakwazi ukubona izimpawu zesifo kubantu abathintekayo ngama-30s noma ama-40 abo.

I-Fuchs dystrophy ithinta ungqimba oluncane lwamaseli agxila engxenyeni engemuva ye-cornea. Lawa maseli asiza ukumpompa uketshezi oluningi ngaphandle kwe-cornea. Njengoba kulahleka amaseli amaningi, uketshezi luqala ukwakheka ku-cornea, lubangele ukuvuvukala ne-cornea enamafu.

Ekuqaleni, uketshezi lungakha kuphela ngesikhathi sokulala, lapho iso livaliwe. Njengoba lesi sifo siba sibi kakhulu, amabhamuza amancane angakheka. Amabhamuza akhula futhi angagcina ephukile. Lokhu kubangela ubuhlungu beso. I-Fuchs dystrophy nayo ingadala ukwakheka kwe-cornea, okuholele ezinkingeni zokubona eziningi.

Izimpawu zingafaka:

• Ubuhlungu bamehlo
• Ukuzwela kwamehlo ekukhanyeni nasekukhanyeni
• Umbono onkungu noma ophuphuthekile, ekuqaleni ekuseni kuphela
• Ukubona ama-halos anemibala azungeze amalambu
• Umbono wokuwohloka usuku lonke

Umhlinzeki angahlola i-Fuchs dystrophy ngesikhathi sokuhlolwa kwesibani.

Olunye uvivinyo olungenziwa lubandakanya:

• I-Pachymetry - ilinganisa ubukhulu be-cornea
• Ukuhlolwa kwe-microscope ejwayelekile - kuvumela umhlinzeki ukuthi abheke ungqimba oluncane lwamaseli agudla ingxenye engemuva ye-cornea
• Ukuhlolwa kwe-acuity ebonakalayo

Amaconsi wamehlo noma amafutha okuthambisa uketshezi oluvela ku-cornea asetshenziselwa ukudambisa izimpawu ze-Fuchs dystrophy.

Uma kuvela izilonda ezibuhlungu ku-cornea, amalensi athambile noma ukuhlinzekwa ukudala izigaxa phezu kwezilonda kungasiza ekunciphiseni ubuhlungu.

Ukuphela kokwelapha i-Fuchs dystrophy ukufakelwa i-corneal.

Kuze kube muva nje, uhlobo oluvame kakhulu lokufakelwa kwe-corneal bekungena i-keratoplasty. Phakathi nale nqubo, kukhishwa ucezu oluncane olujikelezayo lwe-cornea, kusale imbobo ngaphambili kweso. Ucezu olufanayo lwe-cornea oluvela kumnikeli womuntu luyabe seluthungwa kuvulwe ngaphambili kweso.

Inqubo entsha ebizwa nge-endothelial keratoplasty (i-DSEK, i-DSAEK, noma i-DMEK) isibe inketho ekhethwayo kubantu abane-Fuchs dystrophy. Kule nqubo, kufakwa kuphela izingqimba zangaphakathi ze-cornea, esikhundleni sazo zonke izingqimba. Lokhu kuholela ekubuyiseleni ngokushesha futhi kube nezinkinga ezimbalwa. Ukuthunga kaningi akudingeki.

I-Fuchs dystrophy iba yimbi ngokuhamba kwesikhathi. Ngaphandle kokufakelwa kwe-corneal, umuntu one-Fuchs dystrophy enamandla angaba yimpumputhe noma abe nobuhlungu obukhulu futhi anciphise umbono.

Amacala amancane we-Fuchs dystrophy avame ukuba nzima ngemuva kokuhlinzwa kwe-cataract. Udokotela ohlinzayo we-cataract uzohlola le ngozi futhi angaguqula inqubo noma isikhathi sokuhlinzwa kwakho kwe-cataract.

Shayela umhlinzeki wakho uma une:

• Ubuhlungu bamehlo
• Ukuzwela kweso ekukhanyeni
• Umuzwa wokuthi okuthile kusesweni lakho lapho kungekho lutho lapho
• Izinkinga zombono ezifana nokubona ama-halos noma umbono onamafu
• Umbono ofinyela

Akukho ukuvimbela okwaziwayo. Ukugwema ukuhlinzeka nge-cataract noma ukuthatha izinyathelo ezithile zokuqapha ngesikhathi sokuhlinzwa kwe-cataract kungabambezela isidingo sokufakelwa kabusha kwe-corneal.

I-Fuchs ’dystrophy; I-Fuchs ’endothelial dystrophy; I-Fuchs ’corneal dystrophy

Folberg R. Iso. Ku: Kumar V, Abbas AK, Aster JC, ama-eds. Ama-Robbins & Cotran Pathologic Isisekelo Sezifo. Umhlaka 10. IPhiladelphia, PA: Elsevier; 2021: isahluko 29.

IPatel SV. Ngokuya ekuhlolweni kwemitholampilo kuma-fuchs endothelial corneal dystrophy: ukuhlukaniswa kanye nezinyathelo zomphumela - i-Bowman Club Lecture 2019. I-BMJ Open Ophthalmology. 2019; 4 (1): e000321. I-PMID: 31414054 pubmed.ncbi.nlm.nih.gov/31414054/.

IRosado-Adames N, i-Afshari NA. Izifo ze-endothelium ye-corneal. Ku: Yanoff M, Duker JS, ama-eds. I-Ophthalmology. Umhlaka 5. IPhiladelphia, PA: Elsevier; 2019: isahluko 4.21.

I-Salmon JF. I-Cornea. Ku: Salmon JF, ed. IKanski’s Clinical Ophthalmology. Umhlaka 9. IPhiladelphia, PA: Elsevier; 2020: isahluko 7.