Ukuxhuma Phakathi Kwe-Exocrine Pancreatic Insufficiency kanye neCystic Fibrosis

-Delile

• Yini ebangela i-cystic fibrosis?
• Yiziphi izinto ezinobungozi ze-cystic fibrosis?
• Ngabe i-EPI ne-cystic fibrosis zihlobene kanjani?
• Yiziphi izinhlobo zokwelashwa ezitholakalayo ze-EPI?
• Ukuthatha

ICystic fibrosis yisifo esizuzwe njengefa esidala ukuthi uketshezi lomzimba lube luqine futhi lunamathele esikhundleni sokuzaca nokugijima. Lokhu kuthinta kanzima amaphaphu nohlelo lokugaya ukudla.

Abantu abane-cystic fibrosis banezinkinga zokuphefumula ngoba i-mucus ivale amaphaphu abo ibenze babe sengozini yokutheleleka. Isicubu esijiyile siphinde sivale amanyikwe futhi sivimbele ukukhishwa kwama-enzyme wokugaya ukudla. Cishe amaphesenti angama-90 abantu abane-cystic fibrosis baphinde bahlakulele ukungasebenzi kahle kwe-exocrine pancreatic (EPI).

Qhubeka ufunde ukuze ufunde kabanzi mayelana nobudlelwano phakathi kwale mibandela emibili.

Yini ebangela i-cystic fibrosis?

I-cystic fibrosis idalwa yisici kuhlobo lwe-CFTR. Ukuguquka kwesakhi sofuzo kubangela ukuthi amaseli enze uketshezi olujiyile, olunamathelayo. Iningi labantu abane-cystic fibrosis batholakala besebancane.

Yiziphi izinto ezinobungozi ze-cystic fibrosis?

ICystic fibrosis yisifo sofuzo. Uma abazali bakho benesifo noma uma bephethe ufuzo olungasebenzi kahle, usengozini enkulu yokuthola lesi sifo. Umuntu one-cystic fibrosis kufanele azuze izakhi zofuzo ezimbili eziguquliwe, eyodwa kumzali ngamunye. Uma uphatha kuphela ikhophi eyodwa yofuzo, ngeke ube ne-cystic fibrosis kodwa ungumphathi wesifo. Uma abathwali bezakhi zofuzo ababili benengane, kunamathuba angamaphesenti angama-25 okuthi ingane yabo izoba ne-cystic fibrosis. Kunamathuba angamaphesenti angama-50 okuthi ingane yabo izothwala isakhi sofuzo kodwa ingenayo i-cystic fibrosis.

ICystic fibrosis nayo ivame kakhulu kubantu bomdabu waseNyakatho Yurophu.

Ngabe i-EPI ne-cystic fibrosis zihlobene kanjani?

I-EPI iyinkinga enkulu ye-cystic fibrosis. ICystic fibrosis iyimbangela yesibili evame kakhulu ye-EPI, ngemuva kwesifo sokuqaqamba kwamalunga okungamahlalakhona. Kwenzeka ngoba amafinyila aminyene emanyikwe yakho avimba ama-enzyme e-pancreatic ukuthi angene emathunjini amancane.

Ukuntuleka kwama-enzyme e-pancreatic kusho ukuthi umgudu wakho wokugaya ukudla kufanele udlulise ukudla okungagayekile ngokwengxenye. Amafutha namaprotheni kunzima kakhulu kubantu abane-EPI ukugaya.

Lokhu kugaywa okuncane nokumuncwa kokudla kungaholela ku:

• ubuhlungu besisu
• ukuqunjelwa
• ukuqunjelwa
• isifo sohudo
• indle enamafutha futhi evulekile
• ukuncipha komzimba
• ukungondleki

Noma udla inani elijwayelekile lokudla, i-cystic fibrosis ingenza kube nzima ukugcina isisindo esinempilo.

Yiziphi izinhlobo zokwelashwa ezitholakalayo ze-EPI?

Indlela yokuphila enempilo nokudla okunomsoco kungakusiza ukuphatha i-EPI yakho. Lokhu kusho ukukhawulela ukuphuza utshwala, ukugwema ukubhema, nokudla ukudla okunomsoco onemifino eminingi nokusanhlamvu okuphelele. Iningi labantu abane-cystic fibrosis bangadla ukudla okujwayelekile lapho amaphesenti angama-35 kuye kwangama-45 ama-calories avela emafutheni.

Kufanele futhi uthathe okufakwa esikhundleni se-enzyme ngakho konke ukudla kwakho kanye nokudla okulula ukuze uthuthukise ukugaya ukudla. Ukusetshenziswa kokungezelela kungasiza ekwakheleni amavithamini i-EPI evimbela umzimba wakho ekungeneni.

Uma ungakwazi ukugcina isisindo esinempilo, udokotela wakho angase asikisele ukusebenzisa ithubhu yokondla ebusuku ukuvimbela ukungondleki kusuka ku-EPI.

Kubalulekile ukuthi udokotela wakho aqaphe umsebenzi wakho we-pancreatic, noma ngabe okwamanje awunawo umsebenzi owehlisiwe ngoba ungancipha ngokuzayo. Ukwenza kanjalo kuzokwenza isimo sakho silawuleke futhi kunganciphisa amathuba akho okuqhubeka nomonakalo kuma-pancreas akho.

Ukuthatha

Esikhathini esedlule, abantu abane-cystic fibrosis babenamathemba amafushane okuphila. Namuhla, amaphesenti angama-80 abantu abane-cystic fibrosis afinyelela ebudaleni. Lokhu kungenxa yentuthuko enkulu ekwelashweni nasekuphathweni kwezimpawu. Ngakho-ke ngenkathi lisekhona ikhambi le-cystic fibrosis, kunethemba elikhulu.