Isifo sikaWilson: izimpawu, ukuxilongwa nokwelashwa

-Delile

• Izimpawu zesifo sikaWilson
• Ukuxilongwa kwenziwa kanjani
• Indlela yokwelapha

Isifo sikaWilson yisifo sofuzo esingajwayelekile, esidalwa ukungakwazi komzimba ukuhlanganisa ithusi, okwenza ithusi liqongelele ebuchosheni, ezinso, esibindini nasemehlweni, lidale ukudakwa kubantu.

Lesi sifo siyifa, okungukuthi, sidlula sisuka kubazali siye ezinganeni, kepha sitholakala kuphela, ngokujwayelekile, phakathi kweminyaka emi-5 nengu-6 ubudala, lapho ingane iqala ukukhombisa izimpawu zokuqala zobuthi bethusi.

Isifo sikaWilson asinalo ikhambi, noma kunjalo, kukhona imishanguzo nezinqubo ezingasiza ekwehliseni ukwakheka kwethusi emzimbeni kanye nezimpawu zesifo.

Izimpawu zesifo sikaWilson

Izimpawu zesifo sikaWilson zivame ukuvela kusukela eminyakeni yobudala eyi-5 futhi zenzeka ngenxa yokufakwa kwethusi ezingxenyeni ezahlukahlukene zomzimba, ikakhulukazi ubuchopho, isibindi, i-cornea nezinso, okuyizona eziyinhloko:

• Ukuhlanya;
• I-Psychosis;
• Ukuthuthumela;
• Ukudukiswa noma ukudideka;
• Kunzima ukuhamba;
• Ukuhamba kancane;
• Izinguquko ekuziphatheni nasebuntwini;
• Ukulahleka kwamandla okukhuluma;
• I-hepatitis;
• Ukwehluleka kwesibindi;
• Ubuhlungu besisu;
• Ukuqina kwesibindi;
• I-jaundice;
• Igazi emhlanzweni;
• Ukuvela kokopha noma ukulinyazwa;
• Ubuthakathaka.

Esinye isici esivamile sesifo sikaWilson ukuvela kwamasongo abomvu noma ansundu emehlweni, abizwa ngokuthi uphawu lweKayser-Fleischer, okuvela ekuqongeleleni kwethusi kuleyo ndawo. Kujwayelekile futhi kulesi sifo ukukhombisa amakristalu ethusi ezinso, okuholela ekwakhekeni kwamatshe ezinso.

Ukuxilongwa kwenziwa kanjani

Ukutholakala kwesifo sikaWilson kwenziwa ngokuhlolwa kwezimpawu ngudokotela kanye nemiphumela yezivivinyo ezithile zaselabhorethri. Ukuhlolwa okucelwa kakhulu okuqinisekisa ukutholakala kwesifo sikaWilson umchamo wamahora angama-24, lapho kubonwa khona ithusi eliningi, kanye nokulinganiswa kwe-ceruloplasmin egazini, okuyi-protein ekhiqizwa isibindi futhi evamise ukuxhunyaniswa ithusi ukuze libe nomsebenzi. Ngakho-ke, esimweni sesifo sikaWilson, i-ceruloplasmin itholakala ezindaweni eziphansi.

Ngaphezu kwalezi zivivinyo, udokotela angacela i-biopsy yesibindi, lapho kubonakala khona izici ze-cirrhosis noma i-hepatic steatosis.

Indlela yokwelapha

Ukwelashwa kwesifo sikaWilson kuhlose ukwehlisa inani lethusi eliqongelelwe emzimbeni nokwenza ngcono izimpawu zesifo. Kunemithi engathathwa yiziguli, njengoba zibopha ithusi, zisiza ukuyisusa emathunjini nasezinsweni, njengePenicillamine, i-Triethylene melamine, i-zinc acetate kanye ne-vitamin E supplements.

Ngaphezu kwalokho, kubalulekile ukugwema ukudla ukudla okuyimithombo yethusi, njengoshokoledi, izithelo ezomisiwe, isibindi, izinhlanzi zasolwandle, amakhowe namantongomane, isibonelo.

Ezimweni ezinzima kakhulu, ikakhulukazi uma kunokukhubazeka okukhulu kwesibindi, udokotela angakhombisa ukuthi unokufakelwa kwesibindi. Bona ukuthi ukutakula kunjani ngemuva kokufakelwa kwesibindi.