Yini i-blue sclera, izimbangela ezingaba khona nokuthi yini okufanele uyenze

-Delile

• Izimbangela ezingaba khona
• 1. Ukushoda kwe-iron anemia
• 2. I-Osteogenesis imperfecta
• 3. Isifo seMarfan
• 4. Isifo se-Ehlers-Danlos
• 5. Ukusetshenziswa kwemithi

I-Blue sclera yisimo esenzeka lapho ingxenye emhlophe yamehlo iba luhlaza okwesibhakabhaka, into engabonakala kwezinye izingane kuze kufike ezinyangeni eziyisithupha ubudala, futhi ingabonakala nakubantu asebekhulile abangaphezu kweminyaka engama-80, ngokwesibonelo.

Kodwa-ke, lesi simo singahlotshaniswa nokuvela kwezinye izifo njengokushoda kwe-iron anemia, i-osteogenesis imperfecta, amanye ama-syndromes ngisho nokusetshenziswa kwemithi ethile.

Ukuxilongwa kwezifo eziholela ekubonakaleni kwe-sclera eluhlaza okwesibhakabhaka kufanele kwenziwe ngudokotela ojwayelekile, udokotela wezingane noma udokotela wamathambo futhi kwenziwa ngomlando womtholampilo nomndeni womuntu, ukuhlolwa kwegazi nemifanekiso. Ukwelashwa okubonisiwe kuncike ohlotsheni besifo nokuqina kwaso, okungafaka phakathi izinguquko ekudleni, ukusetshenziswa kwemithi noma ukwelashwa ngokomzimba.

Izimbangela ezingaba khona

I-Blue sclera ingavela ngenxa yensimbi encishisiwe egazini noma ukukhubazeka ekukhiqizeni i-collagen, okuholele ekuveleni kwezifo ezinjenge:

1. Ukushoda kwe-iron anemia

Ukushoda kwe-iron anemia kuchazwa ngamanani we-hemoglobin egazini, abonwa esivivinyweni njenge-Hb, ngaphansi kokujwayelekile ngaphansi kuka-12 g / dL kwabesifazane noma ku-13.5 g / dL emadodeni. Izimpawu zalolu hlobo lwe-anemia zibandakanya ubuthakathaka, ikhanda, ukushintsha ukuya esikhathini, ukukhathala ngokweqile futhi kungaholela nasekuveleni kwe-blue sclera.

Lapho kuvela izimpawu, kunconywa ukuthi ufune usizo kudokotela ojwayelekile noma i-hematologist, ozocela ukuhlolwa okufana nokubalwa kwegazi okuphelele kanye nomthamo we-ferritin, ukubheka ukuthi ngabe umuntu une-anemia nezinga lesifo. Funda kabanzi mayelana nokuthi ungabona kanjani ukushoda kwe-iron anemia.

Okufanele ngikwenze: ngemuva kokuthi udokotela enze ukuxilongwa, kuzokhonjiswa ukwelashwa, okuvame ukuqukethe ukusebenzisa i-ferrous sulfate nokwandisa ukutholakala kokudla okune-ayoni okungaba yinyama ebomvu, isibindi, inyama yenkukhu, inhlanzi nemifino eluhlaza emnyama, phakathi kwabanye. Ukudla okunothe ku-vitamin C, okufana newolintshi, i-acerola nelamula, nakho kunganconywa, njengoba sekwenze ngcono ukumuncwa kwensimbi.

2. I-Osteogenesis imperfecta

I-Osteogenesis imperfecta yisifo esibangela ukuqaqamba kwamathambo ngenxa yezinkinga ezithile zofuzo ezihambisana nohlobo 1 lwe-collagen.Izimpawu zalesi sifo ziqala ukuvela ebuntwaneni, esinye sezimpawu ezinkulu ukuba khona kwe-blue sclera. Funda kabanzi ngezinye izimpawu ze-osteogenesis imperfecta.

Okunye ukukhubazeka kwamathambo kugebhezi nomgogodla, kanye nokuxega kwemisipha yamathambo kuyabonakala impela kulesi simo, indlela efaneleke kakhulu eyenziwa ngudokotela wezingane noma wamathambo ukuthola i-osteogenesis engaphelele ngokuhlaziya lezi zimpawu. Udokotela anga-oda i-X-ray ye-panoramic ukuqonda ubukhulu besifo futhi akhombise ukwelashwa okufanele.

Okufanele ngikwenze: lapho uhlola ubukhona be-sclera eluhlaza okwesibhakabhaka nokukhubazeka kwamathambo okungcono ukubheka udokotela wezingane noma udokotela wamathambo ukuze kuqinisekiswe i-osteogenesis engaphelele kanye nokwelashwa okufanele kuboniswe, okungaba ukusetshenziswa kwama-bisphosphonates emthanjeni, okuyimithi qinisa amathambo. Ngokuvamile, kuyadingeka ukusebenzisa amadivayisi wezokwelapha ukuzinzisa umgogodla nokwenza amaseshini okwelapha ngokomzimba.

3. Isifo seMarfan

IMarfan syndrome yisifo esizalwa ngofuzo esidalwa yisakhi sofuzo esibusa kakhulu, esibeka engozini ukusebenza kwenhliziyo, amehlo, imisipha namathambo. Lesi sifo sibangela ukubonakaliswa kwe-ocular, njenge-sclera eluhlaza okwesibhakabhaka futhi kubangele i-arachnodactyly, okuyilapho iminwe yinde ngokweqile, ishintsha esifubeni sesifuba bese ishiya umgogodla ugobile kakhulu kolunye uhlangothi.

Emindenini enamacala alesi sifo kunconywa ukuthi kwenziwe ukwelulekwa ngezakhi zofuzo, lapho kuhlaziywa khona izakhi zofuzo bese kuthi iqembu lochwepheshe linikeze ukuholwa mayelana nokwelashwa. Thola kabanzi mayelana nokuthi kuyini ukwelulekwa ngezakhi zofuzo nokuthi kwenziwa kanjani.

Okufanele ngikwenze: ukuxilongwa kwalesi sifo kungenziwa ngesikhathi sokukhulelwa, noma kunjalo, uma kukhona ukusola ngemuva kokuzalwa, udokotela wezingane angancoma ukuhlolwa kofuzo kanye nokuhlolwa kwegazi noma kwe-imaging ukubheka ukuthi yiziphi izingxenye zomzimba lesi sifo esifinyelele kuzo. Njengoba i-Marfan's syndrome ingenalo ikhambi, ukwelashwa kusekelwe ekulawuleni izinguquko ezithweni.

4. Isifo se-Ehlers-Danlos

I-Ehlers-Danlos syndrome iyisethi yezifo ezitholwe njengefa ezibonakaliswa ukukhubazeka ekukhiqizeni i-collagen, okuholela ekuqineni kwesikhumba namalunga, kanye nezinkinga ngokuxhaswa kwezindonga zemithambo yegazi nemithambo yegazi. Funda kabanzi mayelana ne-Ehlers-Danlos syndrome.

Izimpawu ziyahlukahluka kuye ngomuntu, kepha izinguquko ezahlukahlukene zingenzeka njengokuhlukaniswa komzimba, ukulinyazwa kwemisipha kanye nabantu abanalesi sifo bangaba nesikhumba esincanyana kunokujwayelekile emakhaleni nasezindebeni, okwenza ukulimala kwenzeke kaningi. Ukuxilongwa kufanele kwenziwe ngudokotela wezingane noma udokotela ojwayelekile ngomlando womtholampilo nomndeni womuntu.

Okufanele ngikwenze: ngemuva kokuqinisekiswa kokuxilongwa, landela odokotela bezinto ezahlukahlukene, njenge-cardiologist, ophthalmologist, dermatologist, rheumatologist, okunganconywa, ukuze kuthathwe izinyathelo zokusekela ukunciphisa imiphumela yesifo ezithweni ezahlukahlukene, njengesifo ayinakhambi futhi ivame ukuba yimbi ngokuhamba kwesikhathi.

5. Ukusetshenziswa kwemithi

Ukusetshenziswa kwezinhlobo ezithile zemithi nakho kungaholela ekubonakaleni kwe-sclera eluhlaza okwesibhakabhaka, njenge-minocycline ngemithamo ephezulu nakubantu abebesebenzisa yona iminyaka engaphezu kwengu-2. Eminye imishanguzo yokwelapha ezinye izinhlobo zomdlavuza, njenge-mitoxantrone, nayo ingadala ukuthi i-sclera iphenduke iluhlaza okwesibhakabhaka, ngaphezu kokubanga ukumenyezelwa kwezipikili, kubashiye benombala ompunga.

Okufanele ngikwenze: lezi zimo zivame kakhulu, kepha-ke, uma umuntu ethatha noma iyiphi yale mithi futhi abone ukuthi ingxenye emhlophe yeso iluhlaza okwesibhakabhaka, kubalulekile ukwazisa udokotela onikeze umuthi, ukuze ukumiswa, ushintsho lwethamo noma ukushintshanisa ngomunye umuthi.