Umlobi: Eugene Taylor
Usuku Lokudalwa: 8 Agasti 2021
Ukuvuselela Usuku: 22 Ujuni 2024
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-Delile

I-Polycythemia vera (PV) umdlavuza wegazi ongajwayelekile lapho umnkantsha wenza amangqamuzana egazi amaningi kakhulu. Amangqamuzana egazi abomvu athe xaxa enza igazi lijiye futhi andise nengozi yegazi.

Alikho ikhambi lamanje le-PV, kepha ukwelashwa kungasiza ekuvimbeleni izinkinga kanye nezimpawu zamakheli.

Udokotela wakho uzohlela ukuhlolwa okujwayelekile nokuqokwa ukuqapha impilo yakho. Kubalulekile ukuhlola njalo nethimba lakho lezokunakekelwa kwezempilo ukuze bazi ukuthi uzizwa kanjani.

Funda ukuze uthole kabanzi mayelana nokuthi i-PV iphathwa kanjani, nokuthi ungazi kanjani ukuthi ngabe ukwelashwa kuyasebenza yini.

Izimpawu ezijwayelekile ze-polycythemia vera

I-PV ivame ukutholakala ngomsebenzi wegazi ojwayelekile kunokuthola izimpawu. Izimpawu eziningi ze-PV zinezinye izimbangela, ngakho-ke azihlali zingamafulegi abomvu zodwa. Khuluma nodokotela wakho uma ubona ushintsho endleleni ozizwa ngayo.

Uma unezimpawu, ungahlangabezana:

  • ngizizwe ngikhathele noma ngibuthakathaka
  • ikhanda
  • isiyezi
  • ukukhala ezindlebeni (tinnitus)
  • isikhumba esibomvu
  • izinkinga zombono, kufaka phakathi izindawo eziyimpumputhe noma ukungaboni kahle
  • isikhumba esilumayo, ikakhulukazi ngemuva kokugeza okushisayo noma eshaweni
  • Ubuhlungu besisu noma umuzwa wokugcwala (okuvela kubulembu obukhulisiwe)
  • ubuhlungu besifuba
  • ubuhlungu obuhlangene noma ukuvuvukala

Kungani i-polycythemia vera idinga ukuphathwa?

Amaseli egazi amaningi e-PV enza igazi libe likhulu futhi lithuthuke kakhulu. Lokhu kungaholela ekuhlaselweni yinhliziyo okungaba yingozi, isifo sohlangothi, noma i-pulmonary embolism exhunywe kwi-vein thrombosis ejulile.


Ngenkathi i-PV ingalapheki, lokho akusho ukuthi ayikwazi ukuphathwa ngempumelelo isikhathi eside kakhulu. Ukwelashwa kwe-PV kuhlose ukunciphisa izimpawu nokunciphisa ubungozi bezinkinga ezihlobene namahlule egazi ngokwehlisa inani lamaseli egazi.

Ukwelashwa kwePolycythemia vera

Ithimba lakho lezokunakekelwa kwempilo lizoxoxa ngezindlela zokwelashwa ezihamba phambili ze-PV yakho ngokuya ngamazinga nezimpawu zegazi lakho.

Udokotela wakho angakunikeza imithi ku:

  • igazi elincanyana
  • ukuvimbela izinkinga
  • phatha izimpawu

Kubalulekile ukuthatha imishanguzo njengoba kuqondisiwe.

Izindlela zokwelapha ezilandelayo zisetshenziselwa ukwelapha i-PV:

  • I-Phlebotomy, noma ukukhipha igazi emzimbeni, kunciphisa okwesikhashana ukuminyana kwamangqamuzana egazi abomvu futhi kunciphise igazi lakho.
  • Ukwelashwa kwe-aspirin yesilinganiso esincane kusiza ukunciphisa igazi lakho.
  • I-Anagrelide (Agrylin) kunciphisa amaplatelet egazini lakho, okwehlisa ubungozi behlwili.
  • Ama-antihistamine welapha isikhumba esilumayo, uphawu oluvamile lwe-PV.
  • Izidakamizwa ze-Myelosuppressive njenge-hydroxyurea inciphisa inani lamaseli egazi akhiwe emnkantsheni wethambo.
  • I-Ruxolitinib (Jakafi) ingasiza uma i-PV yakho ingaphenduli ku-hydroxyurea, noma uma unobungozi obuphakathi noma obukhulu be-myelofibrosis.
  • I-Interferon alfa kunciphisa ukukhiqizwa kwamangqamuzana egazi kepha akuvamile ukuba kunqunywe, ngoba kuvame ukudala imiphumela emibi kakhulu kunezinye izindlela zokwelapha.
  • Ukwelashwa okulula ukusebenzisa i-psoralen ne-ultraviolet light kungasiza ekunciphiseni ukulunywa okuxhunyaniswe ne-PV.
  • Ukufakelwa komnkantsha wethambo kwesinye isikhathi kusetshenziselwa ukunciphisa inani lamaseli egazi emnkantsheni wethambo.

Ngazi kanjani ukuthi ukwelashwa kuyasebenza?

I-PV yisifo esingelapheki esingalawulwa ngempumelelo iminyaka eminingi. Ukusebenza ngokusondelana nethimba lakho lezokunakekelwa kwempilo kuqinisekisa ukuthi bayazazi noma yiziphi izinguquko empilweni yakho ukuze bakwazi ukulungisa uhlelo lwakho lokwelashwa njengoba kudingeka.


Ukuphatha i-PV kudinga ukuvakashelwa okujwayelekile nodokotela womdlavuza (oncologist) nodokotela wegazi (i-hematologist). Labo dokotela bazobheka njalo amazinga akho amangqamuzana egazi ukuqondisa izinqumo zokwelashwa.

Qiniseka ukuthi uvumela abahlinzeki bakho bezokunakekelwa kwempilo bazi uma uhlangabezana nezimpawu ezintsha, njengobuhlungu besisu noma ukuvuvukala okuhlangene.

Ukwelashwa kwakho kwamanje kungenzeka kungasebenzi uma kungabhekanwa nezimpawu, noma uma umsebenzi wegazi ukhombisa amazinga angajwayelekile amaseli egazi.

Kulokhu, udokotela wakho angalungisa uhlelo lwakho lokwelashwa kwe-PV. Lokhu kungabandakanya ukuguqula umthamo wemithi yakho noma ukuzama ukwelashwa okusha.

Ukuthatha

IPolycythemia vera (PV) wuhlobo lomdlavuza wegazi ongaqinisa igazi futhi wandise ubungozi bamahlule. Ukuqapha ngokucophelela nokuphatha kunganciphisa izimpawu nobungozi bezinkinga.

Ukuphathwa kwe-PV kufaka phakathi umsebenzi wegazi ojwayelekile, futhi kungafaka imithi kanye ne-phlebotomy. Hlala uxhumene nethimba lakho lokunakekelwa kwezempilo bese ulandela uhlelo lwakho lwezokwelapha ukuze uzizwe ungcono kakhulu.


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