I-porphyria enqamulelayo

-Delile

• Izimpawu ze-porphyria enqamulelayo
• Ukwelashwa kwe-porphyria enqamulelayo

I-porphyria yesikhumba esivele isikhathi eside iyinhlobo ejwayelekile kakhulu ye-porphyria edala ukuthi kuvele izilonda ezincane esikhunjeni esivezwe yilanga, njengemuva kwesandla, ubuso noma isikhumba, ngenxa yokushoda kwe-enzyme ekhiqizwa isibindi eholela ukuqoqwa kwensimbi esikhunjeni.igazi nesikhumba. I-porphyria enqamulelayo ayinakhambi, kepha ingalawulwa ngokusetshenziswa kwemithi ebekwe ngudokotela wesikhumba.

Ngokuvamile, i-porphyria yesikhumba ebambezelekile ivela ngesikhathi sokukhula, ikakhulukazi ezigulini ezivame ukuphuza utshwala noma ezinezinkinga zesibindi, njenge-hepatitis C, ngokwesibonelo.

I-porphyria yesikhumba esivele isikhathi eside imvamisa ayisiyo eyofuzo, kepha kwezinye izimo ingadlula isuke kubazali iye ezinganeni, futhi ukwelulekwa ngezakhi zofuzo kuyanconywa ngaphambi kokukhulelwa, uma kunamacala amaningi emndenini.

Izimpawu ze-porphyria enqamulelayo

Isibonakaliso sokuqala se-porphyria esinqunyiwe ukubonakala kwamabhamuza amancane esikhunjeni adalulwe yilanga, okuthatha isikhathi ukuphola, kepha ezinye izimpawu zifaka:

• Ukukhula ngokweqile kwezinwele ebusweni;
• Isikhumba esiqinile kwezinye izindawo, njengezingalo noma ubuso;
• Umchamo omnyama.

Ngemuva kokuphela kwamabhulethi, kungavela izibazi noma izindawo ezikhanyayo ezithatha isikhathi eside ukuphola.

Ukuxilongwa kwe-porphyria enesikhumba kufanele kwenziwe ngudokotela wesikhumba ngokuhlolwa kwegazi, umchamo kanye nendle ukuqinisekisa ubukhona be-porphyrin kumaseli, njengoba kuyinto ekhiqizwa isibindi ngesikhathi sesifo.

Ukwelashwa kwe-porphyria enqamulelayo

Ukwelashwa kwe-porphyria enezinwele kufanele kuqondiswe ngudokotela wesikhumba ngokubambisana ne-hepatologist, ngoba kuyadingeka ukulawula amazinga e-porphyrin akhiqizwa isibindi. Ngakho-ke, ngokuya ngezimpawu zesiguli, ukwelashwa kungenziwa ngamakhambi we-porphyria enqamulelayo, njenge-chloroquine noma i-hydroxychloroquine, ukuhoxa kwegazi njalo ukwehlisa amazinga wensimbi kumaseli noma inhlanganisela yakho kokubili.

Ngaphezu kwalokho, ngesikhathi sokwelashwa kunconywa ukuthi isiguli sigweme ukuphuza utshwala nokuchayeka elangeni, noma ngabe sine-sun, futhi indlela engcono yokuvikela isikhumba elangeni ukusebenzisa amabhulukwe, amajuzi anemikhono emide, isigqoko namagilavu, isibonelo .