Ungayibona kanjani futhi uyiphathe kanjani i-Leigh Syndrome

-Delile
I-Leigh's syndrome yisifo esingavamile sezakhi zofuzo esidala ukubhujiswa okuqhubekayo kwesistimu yezinzwa emaphakathi, ngaleyo ndlela kuthinte ubuchopho, umgogodla noma i-optic nerve, ngokwesibonelo.
Ngokuvamile, izimpawu zokuqala zivela phakathi kwezinyanga ezi-3 neminyaka emi-2 yobudala futhi zifaka phakathi ukulahleka kwamakhono ezimoto, ukuhlanza nokulahleka kokudla. Kodwa-ke, ezimweni ezingavamile kakhulu, lesi sifo singabonakala nakubantu abadala kuphela, abaneminyaka yobudala engama-30, sikhula kancane.
I-Leigh's syndrome ayinalo ikhambi, kepha izimpawu zayo zingalawulwa ngemithi noma ngokwelashwa ngokomzimba ukuthuthukisa ikhwalithi yempilo yengane.

Ziyini izimpawu eziyinhloko
Izimpawu zokuqala zalesi sifo zivame ukuvela ngaphambi kweminyaka yobudala eyi-2 ngokulahleka kwamakhono abesevele etholakele. Ngakho-ke, kuya ngeminyaka yengane, izimpawu zokuqala zesifo zingafaka ukulahleka kwamakhono njengokuphatha ikhanda, ukuncela, ukuhamba, ukukhuluma, ukugijima noma ukudla.
Ngaphezu kwalokho, ezinye izimpawu ezijwayelekile zifaka:
- Ukuphelelwa isifiso sokudla;
- Ukuhlanza njalo;
- Ukucasuka ngokweqile;
- Ukudlikizela;
- Ukubambezeleka kwentuthuko;
- Kunzima ekutholeni isisindo;
- Ukwehla kwamandla ezingalweni noma emilenzeni;
- Ukudlidliza kwemisipha nokuqaqamba kwemisipha;
Ngokukhula kwalesi sifo, kusesejwayelekile ukukhuphuka kanye ne-lactic acid egazini, okuthi uma isiningi kakhulu, ithinte ukusebenza kwezitho ezinjengenhliziyo, amaphaphu noma izinso, okudala ubunzima ekuphefumuleni noma ekukhuliseni inhliziyo, isibonelo.
Lapho izimpawu zivela ebudaleni, izimpawu zokuqala cishe zihlala zihlobene nombono, kufaka phakathi ukuvela kongqimba omhlophe ofiphaza umbono, ukulahleka kombono okuqhubekayo noma ubumpumputhe bombala (ukulahlekelwa amandla okuhlukanisa phakathi kokuluhlaza nokubomvu). Kubantu abadala, lesi sifo siqhubeka kancane kancane, ngakho-ke, ukuqina kwemisipha, ubunzima ekuxhumaniseni ukunyakaza nokuwohloka kwamandla kuqala ukuvela ngemuva kweminyaka yobudala engama-50.
Yelashwa kanjani
Alukho uhlobo oluthile lokwelashwa kweLeigh's Syndrome, futhi udokotela wezingane kufanele alungise ukwelashwa kwengane ngayinye kanye nezimpawu zayo. Ngakho-ke, iqembu lochwepheshe abambalwa lingadingeka ukwelapha uphawu ngalunye, kufaka phakathi i-cardiologist, i-neurologist, i-physiotherapist kanye nabanye ochwepheshe.
Kodwa-ke, umuthi osetshenziswa kabanzi futhi ovame cishe kuzo zonke izingane ukwengezelelwa ngevithamini B1, njengoba le vithamini isiza ukuvikela ulwelwesi lwezinzwa emgudwini wezinzwa, ukubambezela ukuvela kwalesi sifo nokwenza ngcono ezinye izimpawu.
Ngakho-ke, ukubikezelwa kwalesi sifo kuyahlukahluka kakhulu, kuya ngezinkinga ezibangelwa yilesi sifo enganeni ngayinye, noma kunjalo, isikhathi sokuphila sihlala siphansi ngoba izinkinga ezinzima kakhulu ezibeka impilo engcupheni zivame ukuvela ngesikhathi sobusha.
Yini ebangela lesi sifo
I-Leigh's syndrome idalwa yisifo sofuzo esingazuzwa kubaba nomama, noma ngabe abazali abanaso lesi sifo kodwa kukhona amacala emndenini. Ngakho-ke, kunconywa ukuthi abantu abanezifo zalesi sifo emndenini benze izeluleko ngezofuzo ngaphambi kokukhulelwa ukuthola amathuba okuba nengane enale nkinga.