Isifo seMaffucci

-Delile

• Izimpawu zeMaffucci Syndrome
• Ukwelashwa kweMaffucci's Syndrome
• Izithombe zeMaffucci's Syndrome
• Umthombo:Izikhungo Zokulawulwa Nokuvikelwa Kwezifo
• Isixhumanisi esiwusizo:

I-Maffucci syndrome yisifo esingajwayelekile esithinta isikhumba namathambo, esidala izicubu kuqwanga, ukukhubazeka emathanjeni kanye nokuvela kwezimila ezimnyama esikhunjeni okubangelwa ukukhula okungajwayelekile kwemithambo yegazi.

Ngo- izimbangela ze-Maffucci syndrome zingofuzo futhi zithinta abesilisa nabesifazane ngokulinganayo. Ngokuvamile, izimpawu zesifo zikhula ebuntwaneni ezineminyaka engama-4-5 ubudala.

THE IMaffucci syndrome ayinakhambi, nokho, iziguli zingathola ukwelashwa ukunciphisa izimpawu zesifo futhi zenze ngcono izinga lazo lempilo.

Izimpawu zeMaffucci Syndrome

Izimpawu eziyinhloko ze-Maffucci syndrome yilezi:

• Izicubu ze-Benign kuqwanga lwezandla, izinyawo namathambo amade engalo nemilenze;
• Amathambo aba ntekenteke futhi angaqhekeka kalula;
• Ukunciphisa amathambo;
• Ama-Hemangiomas, aqukethe izicubu ezincane ezimnyama noma eziluhlaza okwesibhakabhaka esikhunjeni;
• Mfushane;
• Ukuntuleka kwemisipha.

Abantu abane-Maffucci Syndrome bangaba nomdlavuza wamathambo, ikakhulukazi kugebhezi, kodwa futhi nomdlavuza we-ovari noma wesibindi.

O ukuxilongwa kweMaffucci syndrome kwenziwa ngokuhlolwa komzimba kanye nokuhlaziywa kwezimpawu ezethulwe iziguli.

Ukwelashwa kweMaffucci's Syndrome

Ukwelashwa kwe-Maffucci's Syndrome kuqukethe ukunciphisa izimpawu zesifo ngokuhlinzwa ukulungisa ukukhubazeka kwamathambo noma izithasiselo zokusiza ukukhula kwengane.

Abantu abahlaselwe yilesi sifo kufanele babonane njalo nodokotela wamathambo ukuze ahlole ushintsho emathanjeni, ukukhula komdlavuza wamathambo nokwelapha ukuqhekeka okwenzeka ngenxa yalesi sifo. Udokotela wesikhumba kufanele futhi aboniswe ukuze ahlole ukubukeka nokuthuthuka kwama-hemangiomas esikhunjeni.

Kubalulekile ezigulini ukuthi zihlolwe njalo ngokomzimba, ama-radiographs noma ama-computed tomography scan.

Izithombe zeMaffucci's Syndrome

Umthombo:Izikhungo Zokulawulwa Nokuvikelwa Kwezifo

Isithombe 1: Ukuba khona kwezicubu ezincane emajoyini eminwe okufana ne-Maffucci's Syndrome;

Isithombe sesi-2: IHemangioma esikhunjeni sesiguli esine-Maffucci syndrome.

Isixhumanisi esiwusizo:

• IHemangioma
• I-Proteus Syndrome