Umlobi: John Pratt
Usuku Lokudalwa: 9 Ufebhuwari 2021
Ukuvuselela Usuku: 29 Hamba 2025
Anonim
Isifo seRomberg - Impilo
Isifo seRomberg - Impilo

-Delile

I-Parry-Romberg syndrome, noma nje i-Romberg syndrome, yisifo esingajwayelekile esibonakala ngokuqina kwesikhumba, imisipha, amafutha, izicubu zamathambo nezinzwa zobuso, okudala ukusonteka ngobuhle. Ngokuvamile, lesi sifo sithinta kuphela uhlangothi olulodwa lobuso, noma kunjalo, singadlulela kuwo wonke umzimba.

Lesi sifo ayinakhambikodwa-ke, ukuthatha imithi nokuhlinzwa kusiza ukulawula ukuqhubeka kwesifo.

Ukuguquguquka kobuso obubonwe kusuka ohlangothiniUkuguquguquka kobuso obubonwe ngaphambili

Yiziphi izimpawu ezisiza ukukhomba

Ngokuvamile, lesi sifo siqala ngokushintsha kobuso ngenhla nje komhlathi noma esikhaleni esiphakathi kwekhala nomlomo, kudlulele nakwezinye izindawo ebusweni.


Ngaphezu kwalokho, ezinye izimpawu zingavela, njenge:

  • Kunzima ukuhlafuna;
  • Kunzima ukuvula umlomo wakho;
  • Iso elibomvu futhi elijulile emzileni;
  • Izinwele zobuso eziwayo;
  • Amabala akhanyayo ebusweni.

Ngokuhamba kwesikhathi, i-Parry-Romberg syndrome nayo ingadala ushintsho ngaphakathi emlonyeni, ikakhulukazi ophahleni lomlomo, ngaphakathi kwezihlathi nezinsini. Kwezinye izimo, izimpawu zezinzwa ezinjengokuquleka nobuhlungu obukhulu ebusweni bungakhula.

Lezi zimpawu zingathuthuka zisuka eminyakeni emi-2 kuye kwengu-10, bese zifaka isigaba esizinzile lapho kungasekho zinguquko ebusweni.

Indlela yokwelashwa

Ekwelapheni izidakamizwa ze-Parry-Romberg Syndrome immunosuppressive ezifana ne-prednisolone, methotrexate noma i-cyclophosphamide ziyathathwa ukusiza ukulwa nalesi sifo nokunciphisa izimpawu, ngoba izimbangela eziyinhloko zalesi sifo zingama-autoimmune, okusho ukuthi amaseli amasosha omzimba ahlasela izicubu kobuso, okwenza ukukhubazeka, isibonelo.


Ngaphezu kwalokho, kungahle futhi kudingeke ukuthi uhlinzwe, ikakhulukazi ukwakha kabusha ubuso, ngokwenza okunamafutha, kwemisipha noma kwamathambo. Isikhathi esihle kakhulu sokuhlinza siyahluka kuye ngomuntu ngamunye, kepha kunconywa ukuthi kwenziwe ngemuva kokuthomba nalapho umuntu eseqedile ukukhula.

-Yintshisekelo

I-Neuronal ceroid lipofuscinoses (NCL)

I-Neuronal ceroid lipofuscinoses (NCL)

I-Neuronal ceroid lipofu cino e (NCL) i ho iqembu lezinkinga ezingavamile zama eli ezinzwa. I-NCL idluli elwa ngemindeni (ezuzwe njengefa).Lezi yizinhlobo ezintathu eziyinhloko ze-NCL:Umuntu omdala (i...
Ukunakekelwa ngaphambi kokubeletha ku-trimester yakho yokuqala

Ukunakekelwa ngaphambi kokubeletha ku-trimester yakho yokuqala

I-Trime ter i ho ukuthi "izinyanga ezi-3." Ukukhulelwa okujwayelekile kuhlala ci he ezinyangeni eziyi humi futhi kunama-trime ter ama-3.I-trime ter yokuqala iqala lapho ingane yakho ikhulelw...