IgA vasculitis - Henoch-Schönlein purpura

I-vasculitis ye-IgA yisifo esifaka amabala ansomi esikhunjeni, ubuhlungu bamalunga, izinkinga zamathumbu, kanye ne-glomerulonephritis (uhlobo lwesifo sezinso). Yaziwa nangokuthi iHenoch-Schönlein purpura (HSP).

I-vasculitis ye-IgA idalwa yimpendulo engavamile yesistimu yomzimba. Umphumela uba ukuvuvukala emithanjeni yegazi encane esikhunjeni. Imithambo yegazi emajoyintini, ezinso, noma emathunjini nayo ingathinteka. Akucaci ukuthi kungani lokhu kwenzeka.

Lesi sifo sibonakala kakhulu ezinganeni ezineminyaka ephakathi kwengu-3 nengu-15, kepha singabonakala nakubantu abadala. Kuvame kakhulu kubafana kunasemantombazaneni. Abantu abaningi abahlakulela lesi sifo babenegciwane eliphezulu lokuphefumula emasontweni edlule.

Izimpawu nezici ze-IgA vasculitis zingafaka:

• Amabala ansundu esikhunjeni (purpura). Lokhu kwenzeka cishe kuzo zonke izingane ezinalesi sifo. Lokhu kuvame ukwenzeka ngaphezulu kwezinqe, imilenze ephansi, nezindololwane.
• Ubuhlungu besisu.
• Ubuhlungu obuhlangene.
• Umchamo ongajwayelekile (ungahle ungabi nazimpawu).
• Isifo sohudo, kwesinye isikhathi sinegazi.
• Isifuba noma i-angioedema.
• Isicanucanu nokuhlanza.
• Ukuvuvukala nobuhlungu besigaxa sabafana.
• Ubuhlungu bekhanda.

Umhlinzeki wezempilo uzobheka umzimba wakho abuke nesikhumba sakho. Ukuhlolwa komzimba kuzobonisa izilonda zesikhumba (i-purpura, izilonda) nobumnene obuhlangene.

Ukuhlolwa kungafaka:

• Ukuhlolwa komchamo kufanele kwenziwe kuzo zonke izimo.
• Qedela ukubalwa kwegazi. Iplatelet kungenzeka ukuthi yejwayelekile.
• Ukuhlolwa kwe-Coagulation: lokhu kufanele kube okujwayelekile.
• Isikhumba biopsy, ikakhulukazi kubantu abadala.
• Ukuhlolwa kwegazi ukubheka ezinye izimbangela zokuvuvukala kwemithambo yegazi, njenge-systemic lupus erythematosus, i-vasculitis ehambisana ne-ANCA noma i-hepatitis.
• Kubantu abadala, kufanele kwenziwe i-biopsy yezinso.
• Ukulingisa ukuhlolwa kwesisu uma ubuhlungu bukhona.

Akukho ukwelashwa okuqondile. Amacala amaningi ayahamba ngokwawo. Ubuhlungu obuhlangene bungathuthuka ngama-NSAID afana ne-naproxen. Uma izimpawu zingapheli, ungahle unikezwe umuthi we-corticosteroid njenge-prednisone.

Lesi sifo sivame ukuba ngcono sisodwa. Izingxenye ezimbili kwezintathu zezingane ezine-IgA vasculitis zineziqephu esisodwa kuphela. Ingxenye eyodwa kwezintathu yezingane ineziqephu eziningi. Abantu kufanele babe nokulandela okulandelayo kwezokwelapha izinyanga eziyisithupha ngemuva kweziqephu ukubheka izimpawu zesifo sezinso. Abantu abadala basengozini enkulu yokuthola isifo sezinso esingalapheki.

Izinkinga zingafaka:

• Ukopha ngaphakathi emzimbeni
• Ukuvimba amathumbu (ezinganeni)
  
• Izinkinga zezinso (ezimweni ezingavamile)

Shayela umhlinzeki wakho uma:

• Uba nezimpawu ze-IgA vasculitis, futhi zihlala isikhathi esingaphezu kwezinsuku ezimbalwa.
• Unomchamo wombala noma okukhipha umchamo ophansi ngemuva kwesiqephu.

Immunoglobulin I-vasculitis; I-leukocytoclastic vasculitis; UHenoch-Schönlein purpura; I-HSP

• UHenoch-Schonlein purpura emilenzeni engezansi
• UHenoch-Schonlein purpura
• UHenoch-Schonlein purpura
• UHenoch-Schonlein purpura
• UHenoch-Schonlein purpura onyaweni losana
• UHenoch-Schonlein purpura emilenzeni yosana
• UHenoch-Schonlein purpura emilenzeni yosana
• UHenoch-Schonlein purpura emilenzeni

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