Umlobi: Janice Evans
Usuku Lokudalwa: 24 Ujulayi 2021
Ukuvuselela Usuku: 23 Ujuni 2025
Anonim
I-ovalocytosis eyifa - Umuthi
I-ovalocytosis eyifa - Umuthi

I-ovalocytosis ye-Hereditary yisimo esingajwayelekile esidluliswa ngemindeni (esizuzwe njengefa). Amaseli egazi amile okweqanda esikhundleni esiyindilinga. Kuyindlela ye-elliptocytosis eyifa.

I-Ovalocytosis itholakala kakhulu kubantu baseNingizimu-mpumalanga Asia.

Izinsana ezisanda kuzalwa ezine-ovalocytosis zingaba ne-anemia ne-jaundice. Abantu abadala kaningi abazibonisi izimpawu.

Ukuhlolwa ngumhlinzeki wakho wezokunakekelwa kwempilo kungakhombisa ubende obukhulisiwe.

Lesi simo sitholwa ngokubheka ukuma kwamangqamuzana egazi ngaphansi kwesibonakhulu. Ukuhlolwa okulandelayo kungenziwa futhi:

  • Qedela ukubalwa kwegazi (i-CBC) ukuhlola ukubulawa kwegazi noma ukubhujiswa kwamangqamuzana egazi abomvu
  • I-smear yegazi ukuthola ukuma kweseli
  • Izinga leBilirubin (lingaba phezulu)
  • Ileactate dehydrogenase level (ingahle ibe phezulu)
  • I-Ultrasound yesisu (ingakhombisa amatshe enyongo)

Ezimweni ezinzima, lesi sifo singelashwa ngokususwa kobende (splenectomy).

Isimo singase sihlotshaniswe nenyongo noma izinkinga zezinso.


Ovalocytosis - ifa

  • Amaseli egazi

IGallagher PG. Ama-anemia we-hemolytic: ulwelwesi lwegazi elibomvu nokukhubazeka komzimba. Ku: IGoldman L, iSchafer AI, ama-eds. Imithi yeGoldman-Cecil. Umhla ka-26. IPhiladelphia, PA: Elsevier; 2020: isahluko 152.

IGallagher PG. Ukuphazamiseka kwamangqamuzana egazi abomvu. Ku: Hoffman R, Benz EJ, Silberstein LE, et al, ama-eds. I-Hematology: Izimiso Eziyisisekelo Nokuzijwayeza. Umhla wesi-7. IPhiladelphia, PA: Elsevier; 2018: isahluko 45.

IMerguerian MD, iGallagher PG. I-elliptocytosis eyifa, ifa le-pyropoikilocytosis, kanye nokuphazamiseka okuhlobene nako. Ku: Kliegman RM, St Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Incwadi kaNelson Yezingane. Umhlaka 21. IPhiladelphia, PA: Elsevier; 2020: isahluko 486.

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