Umlobi: Joan Hall
Usuku Lokudalwa: 28 Ufebhuwari 2021
Ukuvuselela Usuku: 1 Ujulayi 2025
Anonim
I-hyperbilirubinemia yomndeni yesikhashana - Umuthi
I-hyperbilirubinemia yomndeni yesikhashana - Umuthi

I-hyperbilirubinemia yomndeni yesikhashana yisifo se-metabolic esidluliselwa emindenini. Izingane ezinalesi sifo zizalwa zine-jaundice enamandla.

I-hyperbilirubinemia yomndeni yesikhashana yisifo esizuzwe njengefa. Kwenzeka lapho umzimba ungaphuli kahle (umzimba) uhlobo oluthile lwe-bilirubin. Amazinga amaBilirubin akha ngokushesha emzimbeni. Amazinga aphezulu anobuthi ebuchosheni futhi angadala ukufa.

Usana olusanda kuzalwa lungaba:

  • Isikhumba esiphuzi (i-jaundice)
  • Amehlo aphuzi (icterus)
  • Imikhuba emibi

Uma kungalashwa, ukuquleka nezinkinga ze-neurologic (kernicterus) kungahle kuvele.

Ukuhlolwa kwegazi kumazinga we-bilirubin kungakhomba ukuqina kwe-jaundice.

I-Phototherapy enokukhanya okuluhlaza okwesibhakabhaka isetshenziselwa ukwelapha izinga eliphakeme le-bilirubin. Ukumpontshelwa kokushintshaniswa kwesinye isikhathi kuyadingeka uma amazinga ephezulu kakhulu.

Izingane ezilashwa zingaba nomphumela omuhle. Uma isimo singelashwa, kuba nezinkinga ezinzima. Lesi sifo sivame ukuthuthuka ngokuhamba kwesikhathi.


Izinkinga zokufa noma zobuchopho obunzima nezinhlelo zezinzwa (zemizwa) zingenzeka uma isimo singelashwa.

Le nkinga ivame ukutholakala ngokushesha ngemuva kokubeletha. Kodwa-ke, shayela umhlinzeki wakho wokunakekelwa kwezempilo uma ubona isikhumba sengane yakho siphenduka siphuzi. Kunezinye izimbangela ze-jaundice enganeni esanda kuzalwa ezelashwa kalula.

Ukwelulekwa ngofuzo kungasiza imindeni ukuthi iqonde isimo, nezingozi zayo zokuphindelela, nokuthi ungamnakekela kanjani umuntu.

I-Phototherapy ingasiza ekuvimbeleni izinkinga ezinkulu zalesi sifo.

I-Lucey-Driscoll syndrome

ICappellini MD, iLo SF, iSwinkels DW. I-hemoglobin, i-iron, i-bilirubin. Ku: Rifai N, ed. I-Tietz Textbook ye-Clinical Chemistry kanye ne-Molecular Diagnostics. Umhlaka 6. ISt Louis, MO: Elsevier; 2018: isahluko 38.

I-Korenblat KM, iBerk PD. Sondela esigulini nge-jaundice noma ngokuhlolwa kwesibindi okungavamile. Ku: IGoldman L, iSchafer AI, ama-eds. Imithi yeGoldman-Cecil. Umhla ka-26. IPhiladelphia, PA: Elsevier; 2020: isahluko 138.

ILidofsky SD. I-jaundice. Ku: Feldman M, Friedman LS, Brandt LJ, ama-eds. Sleisenger kanye neFordtran's Gastrointestinal and Liver Disease. Umhlaka 10. IPhiladelphia, PA: Elsevier Saunders; 2016: isahluko 21.


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