I-dysplasia emnandi

I-Fibrous dysplasia yisifo samathambo esiqeda futhi sithathe indawo yethambo elijwayelekile ngezicubu zethambo ezinemicu. Ithambo elilodwa noma amaningi angathinteka.

I-fibplous dysplasia imvamisa ivela ebuntwaneni. Iningi labantu liba nezimpawu lapho selineminyaka engama-30 ubudala. Lesi sifo sivela kaningi kwabesifazane.

I-Fibrous dysplasia ixhunyaniswe nenkinga ngezakhi zofuzo (gene mutation) ezilawula amaseli akhiqiza amathambo. Ukuguqulwa kwenzeka lapho ingane ikhula esibelethweni. Isimo asidluliswa sisuka kumzali siye enganeni.

Izimpawu zingafaka noma yikuphi okulandelayo:

• Ubuhlungu bamathambo
• Izilonda zamathambo (izilonda)
• Izinkinga zezindlala ze-Endocrine (hormone)
• Ukuqhekeka noma ukukhubazeka kwamathambo
• Umbala wesikhumba ongajwayelekile (i-pigmentation), eyenzeka ngeMcCune-Albright syndrome

Izilonda zamathambo zingama lapho ingane ifinyelela ebusheni.

Umhlinzeki wezokunakekelwa kwempilo uzokwenza ukuhlolwa komzimba. Ama-X-ray amathambo ayathathwa. Kunganconywa i-MRI.

Alikho ikhambi le-dysplasia enemicu. Ukuphuka kwamathambo noma ukukhubazeka kuphathwa njengoba kudingeka. Izinkinga zeHormone zizodinga ukwelashwa.

Umbono uncike ebucayi besimo kanye nezimpawu ezenzekayo.

Ngokuya ngamathambo athintekile, izinkinga zempilo ezingaba nomphumela zifaka:

• Uma kuthinteka ithambo logebhezi, kungaba nombono noma ukulahleka kokuzwa
• Uma kuthinteka ithambo lomlenze, kungaba nobunzima bokuhamba nezinkinga ezihlangene ezifana nesifo samathambo

Shayela umhlinzeki wakho uma ingane yakho inezimpawu zalesi simo, njengokuphindaphindeka kwamathambo nokukhubazeka kwethambo okungaqondakali.

Ochwepheshe be-orthopedics, endocrinology, kanye ne-genetics bangabandakanyeka ekutholeni nasekunakekelweni kwengane yakho.

Ayikho indlela eyaziwayo yokuvimbela i-fibrous dysplasia. Ukwelashwa kuhlose ukuvimbela izinkinga, njengokuphindaphindeka kwamathambo, ukusiza ukwenza isimo sibe nzima kakhulu.

Ukuvuvukala kwe-fibrous hyperplasia; I-Idiopathic fibrous hyperplasia; Isifo seMcCune-Albright

• I-anatomy yamathambo engaphambili

ICzerniak B. I-Fibrous dysplasia kanye nezilonda ezihlobene. Ku: Czerniak B, ed. Amathambo kaDorfman noCzerniak. Okwesibili. IPhiladelphia, PA: Elsevier Saunders; 2016: isahluko 8.

Heck RK, PC yokudlala. Izicubu zamathambo zeBenign nezimo ezingezona ezokuvuvukala zifanisa izicubu zethambo. Ku: Azar FM, Beaty JH, Kanale ST, ama-eds. I-Operational Orthopedics yaseCampbell. Umhlaka 13. IPhiladelphia, PA: Elsevier; I-2017: isahluko 25.

UMthengisi SN, uNadol JB. Ukubonakaliswa kwe-Otologic kwesifo se-systemic. Ku: Flint PW, Haughey BH, Lund V, et al, ama-eds. I-Cummings Otolaryngology: Ukuhlinzwa Kwekhanda Nentamo. Umhlaka 6. IPhiladelphia, PA: Elsevier Saunders; 2015: isahluko 149.

UShiflett JM, uPerez AJ, Umzali AD. Izilonda zogebhezi ezinganeni: dermoids, langerhans cell histiocytosis, fibrous dysplasia, and lipomas. Ku: Winn HR, ed. Ukuhlinzwa Kwe-Youmans neWinn Neurological. Umhla wesi-7. IPhiladelphia, PA: Elsevier; 2017: isahluko 219.