ISyringomyelia

ISyringomyelia iqoqo elifana ne-cyst le-cerebrospinal fluid (CSF) elenzeka entanjeni yomgogodla. Ngokuhamba kwesikhathi, kulimaza umgogodla.
I-cyst egcwele uketshezi ibizwa nge-syrinx. Ukwakhiwa koketshezi lomgogodla kungabangelwa:
- Ukukhubazeka kokuzalwa (ikakhulukazi ukungqubuzana kweChiari, lapho ingxenye yobuchopho iphonsela phansi entanjeni yomgogodla phansi kogebhezi)
- Ukuhlukumezeka kwentambo yomgogodla
- Izimila zomgogodla
I-cyst egcwele uketshezi imvamisa iqala endaweni yentamo. Iyanda kancane, ifaka ingcindezi emgogodleni bese idala umonakalo kancane.
Ukuqala kwe-syringomyelia kuvame ukuba phakathi kweminyaka engama-25 kuye kwengama-40 ubudala. Abesilisa bathinteka kakhulu kunabesifazane.
Uma isimo singenxa yokukhubazeka kokuzalwa, kungahle kungabikho zimpawu kuze kube yiminyaka engama-30 kuye kwengu-40 ubudala. Izimpawu ze-syringomyelia zivame ukuvela kancane futhi ziba zimbi eminyakeni eminingi. Endabeni yokuhlukumezeka, ukuqala kwezimpawu kungahle kube nezinyanga ezimbili kuya kwezi-3 ubudala. Uma kunezimpawu, zingafaka:
- Ubuhlungu bekhanda
- I-Scoliosis (ezinganeni)
- Ukulahleka kwesisindo semisipha (ukumosha, i-atrophy), kaningi ezandleni nasezandleni
- Ukulahleka kokucabanga emilenzeni engenhla
- Ukwenyuka kwengqondo emilenzeni ephansi
- Ama-spasms noma ukuqina emlenzeni noma emisipha yesandla nengalo
- Ukulahleka kwemisipha, ukulahlekelwa yikhono lokusebenzisa izingalo noma imilenze
- Ubuntofontofo obunciphisa ukuzwa kobuhlungu noma bokushisa; kwehlisa ikhono lokuzwa lapho kuthintwa isikhumba; kwenzeka entanyeni, emahlombe, ezingalweni ezingenhla, nasesiqwini ngephethini efana ne-cape; futhi kancane kancane iba yimbi ngokuhamba kwesikhathi
- Ubuhlungu phansi kwezingalo, intamo, noma emuva emuva noma emilenzeni
- Ubuthakathaka (bancipha amandla emisipha) ezingalweni noma emilenzeni
- Ukusha okungenamsebenzi noma ukulimala kwesandla
- Kunzima ukuhamba noma uzwane ukuhamba ezinganeni
- Ukunyakaza okungalawuleki kwamehlo (nystagmus)
- Isimo esithinta izinzwa esweni nasebusweni (i-Horner syndrome)
Umhlinzeki wezokunakekelwa kwempilo uzokwenza ukuhlolwa ngokomzimba abuze ngezimpawu, egxile ohlelweni lwezinzwa. Ukuhlolwa okungenziwa kufaka phakathi:
- I-MRI yekhanda nomgogodla
- I-Spinal CT scan nge-myelogram (ingenziwa lapho i-MRI ingenakwenzeka)
Alukho umuthi owaziwayo osebenzayo we-syringomyelia. Izinhloso zokwelashwa ukuvimba ukulimala komgogodla ekubeni kubi kakhulu nokwenza ngcono ukusebenza.
Kungadingeka ukwelashwa ukuze unciphise ingcindezi entanjeni yomgogodla. Ukwelashwa ngokomzimba nangokomsebenzi kungadingeka ukuze kuthuthukiswe ukusebenza kwemisipha.
I-Ventriculoperitoneal shunting noma i-syringosubarachnoid shunting ingadingeka. Le yinqubo lapho kufakwa khona ipayipi (ithubhu elincane, eliguquguqukayo) lokukhipha uketshezi oluthambile.
Ngaphandle kokwelashwa, lesi sifo singaba sibi kakhulu kancane. Ngokuhamba kwesikhathi, kungadala ukukhubazeka okukhulu.
Ukuhlinzwa kuvimbela isimo ukuthi singabi sibi kakhulu. Ukusebenza kwesistimu yezinzwa kuzothuthuka cishe kubantu abangama-30% abahlinzwa.
Ngaphandle kokwelashwa, lesi simo singaholela ku:
- Ukulahleka komsebenzi wesistimu
- Ukukhubazeka unomphela
Izinkinga ezingenzeka zokuhlinzwa zifaka:
- Ukutheleleka
- Ezinye izinkinga zokuhlinzwa
Shayela umhlinzeki wakho uma unezimpawu ze-syringomyelia.
Ayikho indlela eyaziwayo yokuvikela lesi simo, ngaphandle kokugwema ukulimala komgogodla. Ukwelashwa ngokushesha kunciphisa lesi sifo ekubeni sibi kakhulu.
I-Syrinx
Isistimu yezinzwa ephakathi
I-Batzdorf U. Syringomyelia. Ku: Shen FH, Samartzis D, Fessler RG, ama-eds. Incwadi yombhalo wesibeletho somlomo wesibeletho. IPhiladelphia, PA: Elsevier Saunders; 2015: isahluko 29.
I-Benglis DM, i-Jea A, i-Vanni S, i-Shah AH, i-Green BA. ISyringomyelia. Ku: Garfin SR, Eismont FJ, Bell GR, Fischgrund JS, Bono CM, abahleli. URothman-Simeone noHerkowitz ethi The Spine. Umhla wesi-7. IPhiladelphia, PA: Elsevier; 2018: isahluko 94.
URoguski M, Samdani AF, Hwang SW. I-syringomyelia yabantu abadala. Ku: Winn HR, ed. Ukuhlinzwa Kwe-Youmans neWinn Neurological. Umhla wesi-7. IPhiladelphia, PA: Elsevier; 2017: isahluko 301.