Umlobi: William Ramirez
Usuku Lokudalwa: 20 Usepthemba 2021
Ukuvuselela Usuku: 1 Ujulayi 2024
Anonim
Hereditary Hemorrhagic Telangiectasia - HHT Center of Excellence at UCLA
Ividiyo: Hereditary Hemorrhagic Telangiectasia - HHT Center of Excellence at UCLA

I-Telangiectasias mincane, ikhulise imithambo yegazi esikhunjeni. Imvamisa ayinabungozi, kepha ingahlotshaniswa nezifo eziningana.

I-Telangiectasias ingahle ikhule noma kuphi ngaphakathi komzimba. Kepha zibonakala kalula esikhumbeni, ulwelwesi lwamafinyila, nabamhlophe bamehlo. Imvamisa, azibangeli zimpawu. Amanye ama-telangiectasias opha futhi abangela izinkinga ezinkulu. I-Telangiectasias nayo ingavela ebuchosheni noma emathunjini futhi idale izinkinga ezinkulu ekuphumeni kwegazi.

Izimbangela zingafaka:

  • I-Rosacea (inkinga yesikhumba ebangela ukuthi ubuso bube bomvu)
  • Ukuguga
  • Inkinga ngezakhi zofuzo
  • Ukukhulelwa
  • Ukuvezwa yilanga
  • Imithambo ye-Varicose
  • Ukusetshenziswa ngokweqile kwamafutha we-steroid
  • Ukuhlukumezeka endaweni

Izifo ezihambisana nalesi simo zifaka:

  • I-Ataxia-telangiectasia (isifo esithinta isikhumba, ibhalansi nokuxhumana, nezinye izindawo zomzimba)
  • I-Bloom syndrome (isifo esizuzwe njengefa esidala ubude obufushane, ukuzwela kwesikhumba emisebeni yelanga, nokubomvu kobuso)
  • I-Cutis marmorata telangiectatica congenita (isifo sesikhumba esidala amabala abomvu)
  • I-hereditary hemorrhagic telangiectasia (i-Osler-Weber-Rendu syndrome)
  • I-Klippel-Trenaunay-Weber syndrome (isifo esibanga ibala le-port-wine, imithambo ye-varicose, nezinkinga zezicubu ezithambile)
  • I-Nevus flammeus efana ne-port-wine stain
  • I-Rosacea (isimo sesikhumba esidala ukubomvu kobuso)
  • Isifo se-Sturge-Weber (isifo esifaka ibala le-port-wine nezinkinga zesistimu yezinzwa)
  • I-Xeroderma pigmentosa (isifo lapho isikhumba kanye nezicubu ezimboze iso kuzwela kakhulu ekukhanyeni kwe-ultraviolet)
  • I-Lupus (isifo samasosha omzimba)
  • I-CREST syndrome (uhlobo lwe-scleroderma olubandakanya ukwakheka kwezicubu ezinjengezibazi esikhumbeni nakwezinye izindawo emzimbeni futhi kulimaze amaseli agudle izindonga zemithambo emincane)

Shayela umhlinzeki wakho wezokunakekelwa kwezempilo uma ubona imikhumbi ekhulisiwe esikhunjeni, ulwelwesi lwamafinyila, noma iso.


Umhlinzeki uzokwenza ukuhlolwa komzimba abuze ngezimpawu zakho, kufaka phakathi:

  • Itholakalaphi imithambo yegazi?
  • Ngabe bopha kalula ngaphandle kwesizathu?
  • Yiziphi ezinye izimpawu ezikhona?

Ukuhlolwa kungadingeka ukuze kutholakale noma kukhishwe isimo sempilo. Ukuhlolwa kungafaka:

  • Ukuhlolwa kwegazi
  • Ukuskena kwe-CT
  • Izifundo zomsebenzi wesibindi
  • Ukuhlolwa kwe-MRI
  • Ama-X-ray

I-Sclerotherapy iyindlela yokwelapha i-telangiectasias emilenzeni. Kule nqubo, isisombululo sikasawoti (usawoti) noma elinye ikhemikhali sijojelwa ngqo emithanjeni yesicabucabu emilenzeni. Ukwelashwa kwe-Laser kuvame ukusetshenziselwa ukwelapha i-telangiectasias yobuso.

Ama-ectasias we-Vascular; Isicabucabu angioma

  • I-Angioma serpiginosum
  • I-Telangiectasia - imilenze
  • I-Telangiectasias - ingalo ephezulu

UKelly R, Baker C. Ezinye izifo zemithambo yegazi. Ku: Bolognia JL, Schaffer JV, Cerroni L, ama-eds. Isikhumba. Umhla wesi-4. IPhiladelphia, PA: Elsevier; 2018: isahluko 106.


IPatterson JW. Izimila zemithambo yegazi. Ku: Patterson JW, ed. I-Weedon's Skin Pathology. Umhla wesi-4. IPhiladelphia, PA: Elsevier Churchill Livingstone; 2016: isahluko 38.

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