Coloboma: kuyini, izinhlobo, izimpawu kanye nokwelashwa

-Delile
IColoboma, eyaziwa kakhulu ngokuthi i-cat's eye syndrome, wuhlobo lokungalungi kweso lapho kukhona ushintsho esakhiweni seso, olungathinta ijwabu leso noma iris, ukuze iso libukeke lifana nelika ikati, kepha amandla okubona cishe agcinwa njalo.
Yize i-coloboma ivame kakhulu esweni elilodwa, futhi ingahle ihlangane, kwezinye izimo, ithinte amehlo womabili, kepha uhlobo lwe-coloboma lungahluka kusuka kwelinye iso kuye kwelinye. Alisekho ikhambi lalolu hlobo lokuphazamiseka, kepha ukwelashwa kusiza ukunciphisa ezinye zezimpawu futhi kuthuthukise ikhwalithi yempilo yomuntu.

Izinhlobo ze-coloboma
IColoboma ingenzeka ngenxa yokuguqulwa okungahleliwe kwezakhi zofuzo okungazuzwa noma kwenzeke ngokuzenzekelayo ngaphandle kwamanye amacala emndenini. Kodwa-ke, izimo eziningi ze-coloboma zenzeka ngenxa yezinguquko ngesikhathi se-embryogenesis yokukhulelwa.
Ngokwesakhiwo seso elithintekile, i-coloboma ingahlukaniswa ngezinhlobo eziningana, okuyiyona eyinhloko:
- Ijwabu leso: ingane izalwa ilahlekile isiqeshana sejwabu leso eliphezulu noma elingezansi, kepha inombono ojwayelekile;
- I-optic nerve coloboma: izingxenye zezinzwa ze-optic azikho, ezingagcina zithinte umbono noma zibangele ukungaboni;
- IColoboma yeretina: i-retina ayithuthukisiwe kahle noma inamaphutha amancane athinta umbono, okungadala amabala amnyama esithombeni esibonwayo, isibonelo;
- I-Macular coloboma: kukhona ukwehluleka ekwakhiweni kwesifunda esiphakathi se-retina ngakho-ke, umbono uthinteka kakhulu.
Yize kunezinhlobo eziningana ze-coloboma, okuvame kakhulu i-iris, lapho iris inesimo esihlukile kwesivamile, ifana neso lekati.
Izimpawu eziyinhloko
Izimpawu ze-coloboma ziyahluka ngohlobo lwazo, noma kunjalo, izimpawu nezimpawu ezivame kakhulu yilezi:
- Umfundi ngesimo se 'keyhole';
- Ukuntuleka kwesiqephu sejwabu leso;
- Ukuzwela ngokweqile ekukhanyeni;
- Ubunzima bokukubona lokho abuthuthuki ngezingilazi.
Ngaphezu kwalokho, uma kuyi-coloboma ye-optic nerve, i-retina noma i-macula, ukwehla okukhulu ekhonweni lokubona nakho kungavela futhi, kwezinye izingane, bangazalwa bengaboni.
Njengoba lezi zinguquko zivame ukuhlobene nezinye izinkinga, njenge-cataract, i-glaucoma noma i-nystagmus, isibonelo, udokotela angadinga ukwenza izivivinyo eziningana emehlweni engane ukuze ahlole ukuthi ngabe zikhona yini ezinye izinkinga ezidinga ukwelashwa.
Yelashwa kanjani
Ukwelashwa kwe-coloboma kuyadingeka kuphela lapho ushintsho lubangela ubunzima ekuboneni noma kwesinye isibonakaliso. Ngaphandle kwalokho, i-ophthalmologist ihlela kuphela ama-aphoyintimenti njalo ezinyangeni eziyi-6 ukuhlola ukukhula kweso, okungenani kuze kube seminyakeni engu-7.
Ezimweni lapho kudingeka ukwelashwa, inqubo esetshenzisiwe iyahlukahluka ngokuya ngesifo, futhi ingakhonjiswa:
- Ukusetshenziswa kwamalensi wokuxhumana anemibala: bane-iris edwetshiwe eyenza kube lula ukufihla umfundi onomumo ofana nowekati;
- Ukugqoka izibuko zelanga noma ukufaka izihlungi emawindini kusuka ekhaya nasemotweni: usizo lokwehlisa inani lokukhanya lapho kunokuzwela kwamehlo ngokweqile;
- Ukuhlinzwa kwezimonyo: ikuvumela ukuthi wakhe kabusha ijwabu leso elilahlekile noma ubuyisele unomphela ukwakheka komfundi.
Lapho ukwehla kwekhono lokubona, udokotela wezifo zamehlo angazama futhi amasu ahlukahlukene njengezibuko, amalensi noma ngisho nokuhlinzwa kwe-lasik, ukuzama ukukhomba ukuthi kukhona yini okungaba ngcono kumbono.