Ukudla kwePhenylketonuria: Ukudla okuvunyelwe, okuvinjelwe nemenyu

-Delile

• Ukudla kuvunyelwe ku-phenylketonuria
• Ukudla kuvinjelwe e-phenylketonuria
• Inani le-phenylalanine elivunyelwe ngeminyaka
• Imenyu yesampula
• Isibonelo semenyu yengane eneminyaka emithathu ubudala ene-phenylketonuria:

Ekudleni kwabantu abane-phenylketonuria kubaluleke kakhulu ukulawula ukutholwa kwe-phenylalanine, eyi-amino acid etholakala kakhulu ekudleni okunothe ngamaprotheni, njengenyama, inhlanzi, amaqanda, ubisi nemikhiqizo yobisi. Ngakho-ke, labo abane-phenylketonuria kufanele bahlolwe njalo ngegazi ukuze bahlole inani le-phenylalanine egazini futhi, kanye nodokotela, babala inani le-phenylalanine abangalifaka phakathi nosuku.

Njengoba kuyadingeka ukugwema ukudla okuningi okunothe ngamaprotheni, i-phenylketonurics kufanele futhi isebenzise izithasiselo zamaprotheni ngaphandle kwe-phenylalanine, ngoba amaprotheni ayizakhamzimba ezibaluleke kakhulu emzimbeni, ezingenakususwa ngokuphelele.

Ngaphezu kwalokho, ngokungabikho kokudla kwe-phenylalanine, umzimba udinga imithamo ephezulu ye-tyrosine, engenye i-amino acid ebaluleke kakhulu ekukhuleni lapho ingekho i-phenylalanine. Ngalesi sizathu, imvamisa kuyadingeka ukwengeza nge-tyrosine ngaphezu kokudla. Bheka ukuthi ezinye izindlela zokuqapha zibalulekile ekwelapheni i-phenylketonuria.

Ukudla kuvunyelwe ku-phenylketonuria

Ukudla okuvunyelwe abantu abane-phenylketonuria yilesi:

• Izithelo:i-apula, ipheya, ikhabe, amagilebhisi, i-acerola, ilamula, i-jabuticaba, i-currant;
• Eminye impuphu: isitashi, umdumbula;
• Uswidi: ushukela, amajeli wezithelo, uju, i-sago, i-cremogema;
• Amafutha: uwoyela wemifino, okhilimu bemifino ngaphandle kobisi nezinto ezitholakele;
• Abanye: amaswidi, amalollipops, iziphuzo ezibandayo, izigaxa zezithelo ngaphandle kobisi, ikhofi, itiye, i-gelatin yemifino eyenziwe ngotshani lwasolwandle, lwesinaphi, pepper.

Kukhona nokunye ukudla okuvunyelwe i-phenylketonurics, kepha lokho kufanele kulawulwe. Lokhu kudla yikho:

• Imifino ngokujwayelekile, njengesipinashi, i-chard, utamatisi, ithanga, ama-yam, amazambane, ubhatata, i-okra, ama-beet, ukholifulawa, izaqathe, i-chayote.
• Abanye: ama-noodle elayisi ngaphandle kwamaqanda, ilayisi, amanzi kakhukhunathi.

Ngaphezu kwalokho, kunezinguqulo ezikhethekile zezithako ezinenani elincane le-phenylalanine, njengelayisi, ufulawa kakolweni noma i-pasta, isibonelo.

Yize imikhawulo yokudla ilungele i-phenylketonurics, kunemikhiqizo eminingi esezimbonini engenayo i-phenylalanine ekwakhiweni kwayo noma empofu kule-amino acid. Kodwa-ke, kuzo zonke izimo kubaluleke kakhulu ukufunda kumaphakethe womkhiqizo uma iqukethe i-phenylalanine.

Bona uhlu oluphelele lokudla okuvumelekile namanani we-phenylalanine.

Ukudla kuvinjelwe e-phenylketonuria

Ukudla okuvinjelwe e-phenylketonuria yilokho okunothe ku-phenylalanine, okuyikudla okunothe kakhulu ngamaprotheni, njenge:

• Ukudla kwezilwane: inyama, inhlanzi, ukudla kwasolwandle, ubisi nemikhiqizo yenyama, amaqanda, nemikhiqizo yenyama efana nesoseji, isoseji, ubhekeni, ham.
• Ukudla komsuka wesitshalo: ukolweni, amantongomane, ubhontshisi, uphizi, udali, imikhiqizo yesoya kanye nesoya, ama-chestnut, ama-walnuts, amakinati, ama-hazelnut, ama-alimondi, ama-pistachio, amantongomane ephayini
• Ama-sweeteners ane-aspartame noma ukudla okuqukethe lo mnandi;
• Imikhiqizo equkethe ukudla okungavunyelwe, njengamakhekhe, amakhukhi nesinkwa.

Njengoba ukudla kwama-phenylketonurics kunamaphrotheni amancane, laba bantu kufanele bathathe izithasiselo ezikhethekile zama-amino acid angenayo i-phenylalanine ukuqinisekisa ukukhula nokusebenza komzimba okufanele.

Inani le-phenylalanine elivunyelwe ngeminyaka

Inani le-phenylalanine elingadliwa nsuku zonke liyahluka ngokuya ngeminyaka nangesisindo, futhi ukondliwa kwama-phenylketonurics kufanele kwenziwe ngendlela engeqi amanani we-phenylalanine avunyelwe. Uhlu olungezansi lubonisa amanani avunyelwe ale-amino acid ngokuya ngeqembu leminyaka:

• Phakathi kwezinyanga ezingu-0 nezingu-6: 20 kuya ku-70 mg / kg ngosuku;
• Phakathi kwezinyanga eziyi-7 nonyaka owodwa: 15 kuya ku-50 mg / kg ngosuku;
• Kusuka eminyakeni engu-1 kuye kwengu-4 ubudala: 15 kuya ku-40 mg / kg ngosuku;
• Kusuka eminyakeni engu-4 kuye kwengu-7 ubudala: 15 kuye ku-35 mg / kg ngosuku;
• Kusuka ku-7 kuya phambili: 15 kuye ku-30 ​​mg / kg ngosuku.

Uma umuntu one-phenylketonuria efaka i-phenylalanine kuphela kumanani avunyelwe, ukukhula kwabo kwezimoto nokuqonda ngeke kubekeke engozini. Ukuze ufunde kabanzi bona: Qonda kangcono ukuthi yini iPhenylketonuria nokuthi ilashwa kanjani.

Imenyu yesampula

Imenyu yokudla kwe-phenylketonuria kumele ibe ngeyomuntu uqobo futhi ilungiswe ngusomsoco, ngoba kufanele icabangele iminyaka yomuntu, inani le-phenylalanine elivunyelwe kanye nemiphumela yokuhlolwa kwegazi.

Isibonelo semenyu yengane eneminyaka emithathu ubudala ene-phenylketonuria:

Ukubekezelelana: 300 mg we-phenylalanine ngosuku

Kubalulekile futhi ukuthi lowo muntu namalungu omndeni wakhe bahlole amalebula womkhiqizo ukuthi ngabe ukudla kune-phenylalanine noma cha nokuqukethwe kwayo, ngalokho kulungiswa inani lokudla okungadliwa.