Umlobi: Randy Alexander
Usuku Lokudalwa: 24 Epreli 2021
Ukuvuselela Usuku: 9 Hamba 2025
Anonim
Systemic Sclerosis and Scleroderma: Visual Explanation for Students
Ividiyo: Systemic Sclerosis and Scleroderma: Visual Explanation for Students

-Delile

I-Systemic Sclerosis (SS)

ISystemic sclerosis (SS) ukuphazamiseka okuzenzakalelayo. Lokhu kusho ukuthi yisimo lapho amasosha omzimba ehlasela umzimba. Izicubu ezinempilo zibhujiswa ngoba amasosha omzimba ngephutha acabanga ukuthi yinto yangaphandle noma ukutheleleka. Kunezinhlobo eziningi zokuphazamiseka okuzenzakalelayo okungathinta amasistimu womzimba ahlukile.

I-SS ibonakala ngokushintshwa kokubukeka nokubukeka kwesikhumba. Lokhu kungenxa yokwanda komkhiqizo we-collagen. I-Collagen iyingxenye yezicubu ezixhuma.

Kodwa ukuphazamiseka akugcini ekuguqulweni kwesikhumba. Kungathinta i-:

  • imithambo yegazi
  • imisipha
  • inhliziyo
  • uhlelo lokugaya ukudla
  • amaphaphu
  • izinso

Izici ze-systemic sclerosis zingavela kwezinye izifo ezizimele. Uma lokhu kwenzeka, kubizwa ngokuthi ukuxhuma okuxubile okuxubile.

Lesi sifo sijwayele ukubonwa kubantu abaneminyaka engama-30 kuya kwengama-50 ubudala, kodwa singatholakala noma ngasiphi isikhathi. Abesifazane banamathuba amaningi okutholakala ukuthi banaso lesi simo kunabesilisa. Izimpawu nobukhulu besimo ziyahlukahluka kuye ngomunye umuntu ngokuya ngamasistimu nezitho ezithintekayo.


I-systemic sclerosis ibizwa nangokuthi i-scleroderma, i-progressive systemic sclerosis, noma i-CREST syndrome. I- “CREST” imele:

  • i-calcinosis
  • Isimo sikaRaynaud
  • ukungasebenzi kahle kwesisu
  • sclerodactyly
  • telangiectasia

I-CREST syndrome iyindlela elinganiselwe yokuphazamiseka.

Izithombe zeSystemic Sclerosis (Scleroderma)

Izimpawu zeSystemic Sclerosis

I-SS ingathinta isikhumba kuphela ezinyathelweni zokuqala zesifo. Ungaqaphela ukuqina kwesikhumba sakho nezindawo ezicwebezelayo ezikhula zizungeze umlomo wakho, impumulo, iminwe, nezinye izindawo ezinamathambo.

Njengoba isimo siqhubeka, ungaqala ukuqala ukunyakaza okulinganiselwe kwezindawo ezithintekile. Ezinye izimpawu zifaka:

  • ukulahleka kwezinwele
  • ama-calcium deposits, noma izigaxa ezimhlophe ngaphansi kwesikhumba
  • imithambo yegazi emincane, evulekile ngaphansi kwesikhumba
  • ubuhlungu obuhlangene
  • ukuphelelwa umoya
  • ukukhwehlela okomile
  • isifo sohudo
  • ukuqunjelwa
  • ubunzima bokugwinya
  • i-esophageal reflux
  • ukuqunjelwa esiswini ngemuva kokudla

Ungaqala ukuzwa ukuphazamiseka kwemithambo yegazi eminwe nasezinzwaneni zakho. Ngemuva kwalokho, imikhawulo yakho ingahle ibe mhlophe futhi iluhlaza okwesibhakabhaka lapho usemakhazeni noma uzizwa ucindezeleke ngokweqile ngokomzwelo. Lokhu kubizwa ngokuthi yinto kaRaynaud.


Izimbangela ze-Systemic Sclerosis

I-SS yenzeka lapho umzimba wakho uqala ukukhiqiza ngokweqile i-collagen futhi ihlangana nezicubu zakho. I-Collagen yiprotheni eyakheke kakhulu eyakha zonke izicubu zakho.

Odokotela abaqiniseki ukuthi yini ebangela ukuthi umzimba ukhiqize i-collagen eningi kakhulu. Imbangela ngqo ye-SS ayaziwa.

Izici Zengozi Ye-Systemic Sclerosis

Izici zobungozi ezingakhuphula amathuba akho okuthuthukisa lesi simo zifaka:

  • ukuba ngumdabu waseMelika
  • ukuba yi-African-American
  • ukuba ngowesifazane
  • usebenzisa imithi ethile yamakhemikhali efana neBleomycin
  • ukuvezwa uthuli lwe-silica kanye nama-solvents organic

Ayikho indlela eyaziwayo yokuvimbela i-SS ngaphandle kokunciphisa izinto ezinobungozi ongazilawula.

Ukuxilongwa kwe-Systemic Sclerosis

Ngesikhathi sokuhlolwa komzimba, udokotela wakho angabona izinguquko zesikhumba eziyizimpawu ze-SS.

Umfutho wegazi ophakeme kungenzeka ubangelwe ukushintsha kwezinso kusuka ku-sclerosis. Udokotela wakho angalawula ukuhlolwa kwegazi njengokuhlolwa kwe-antibody, i-rheumatoid factor, kanye nesilinganiso sedimentation.


Ezinye izivivinyo zokuxilonga zingafaka:

  • iX-ray yesifuba
  • ukuhlolwa komchamo
  • i-CT scan yamaphaphu
  • ama-biopsies esikhumba

Ukwelashwa kwe-Systemic Sclerosis

Ukwelashwa akukwazi ukwelapha lesi simo, kepha kungasiza ekwehliseni izimpawu nokuhamba kancane kwezifo. Ukwelashwa ngokujwayelekile kusekelwe kwizimpawu zomuntu kanye nesidingo sokuvimbela izinkinga.

Ukwelashwa kwezimpawu ezijwayelekile kungabandakanya:

  • ama-corticosteroids
  • ama-immunosuppressants, njenge-methotrexate noma i-Cytoxan
  • izidakamizwa ezingezona ukuvuvukala

Ngokuya ngezimpawu zakho, ukwelashwa kungafaka futhi:

  • imithi yengcindezi yegazi
  • imithi yokusiza ukuphefumula
  • ukwelashwa ngokomzimba
  • ukwelashwa okulula, njenge-ultraviolet A1 phototherapy
  • Amafutha e-nitroglycerin aphatha izindawo ezenzelwe ukuqinisa isikhumba

Ungenza ushintsho lwendlela yokuphila ukuze uhlale uphilile nge-scleroderma, njengokugwema ukubhema ugwayi, ukuhlala usebenza kahle nokugwema ukudla okubangela isilungulela.

Izinkinga Ezingaba khona zeSystemic Sclerosis

Abanye abantu abane-SS babhekana nokuqhubeka kwezimpawu zabo. Izinkinga zingafaka:

  • ukuhluleka kwenhliziyo
  • umdlavuza
  • ukwehluleka kwezinso
  • umfutho wegazi ophakeme

Uyini Umbono Wabantu abaneSystemic Sclerosis?

Ukwelashwa kwe-SS kuthuthuke kakhulu eminyakeni engama-30 edlule. Yize lisekhona ikhambi le-SS, kunezindlela eziningi zokwelapha ezahlukahlukene ezingakusiza ukuphatha izimpawu zakho.Khuluma nodokotela wakho uma ngabe ezinye zezimpawu zakho ziphazamisa impilo yakho yansuku zonke. Bangasebenza nawe ukulungisa uhlelo lwakho lokwelashwa.

Kufanele futhi ucele udokotela wakho ukuthi akusize uthole amaqembu osizo endawo e-SS. Ukukhuluma nabanye abantu abanokuhlangenwe nakho okufanayo nawe kungenza kube lula ukubhekana nesimo esingalapheki.

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