Siyini isifo se-Alport, izimpawu zaso nokwelashwa

-Delile

• Izimpawu eziyinhloko
• Yini ebangela lesi sifo
• Ungakuqinisekisa kanjani ukuxilongwa
• Yelashwa kanjani

I-Alport syndrome yisifo esingajwayelekile sezakhi zofuzo esidala ukulimala okuqhubekayo emithanjeni yegazi encane ese-glomeruli yezinso, evimbela isitho ukuthi sikwazi ukuhluza igazi ngokufanele futhi sibonise izimpawu ezifana negazi emchameni nokwanda kwenani lamaprotheni ekuhlolweni kwegazi. umchamo.

Ngaphezu kokuthinta izinso, lesi sifo singadala nezinkinga ekuzweni nasekubukeni, njengoba sivimbela ukukhiqizwa kweprotheni ebalulekile ekusebenzeni kwamehlo nezindlebe.

I-Alport's syndrome ayinalo ikhambi, kepha ukwelashwa kusiza ekunciphiseni izimpawu futhi kubambezele nokuthuthuka kwalesi sifo, kuvimbele ukusebenza kwezinso kungathinteki.

Izimpawu eziyinhloko

Izimpawu ezivame kakhulu ze-Alport's syndrome zifaka:

• Igazi emchameni;
• Umfutho wegazi ophakeme;
• Ukuvuvukala kwemilenze, amaqakala, izinyawo nobuso.

Ngaphezu kwalokho, kukhona nezimo lapho ukuzwa nokubona kuthinteka khona yilesi sifo, kubangele ubunzima bokuzwa nokubona.

Uma kungathathwa izinyathelo zokuzivikela ezifanele, lesi sifo singaqhubekela ekuhlulekeni okungapheli kwezinso futhi sidinge i-dialysis noma ukufakelwa kwezinso.

Yini ebangela lesi sifo

Isifo i-Alport's syndrome sibangelwa izinguquko ezakhiweni zofuzo eziqukethe imiyalo yokukhiqizwa kweprotheni eyaziwa ngokuthi uhlobo IV collagen. Lolu hlobo lwe-collagen luyingxenye ye-glomeruli yezinso futhi, ngakho-ke, uma lungekho, imithambo yegazi kulezi zifunda iyalimala futhi yelaphe, iphazamise ukusebenza kwezinso.

Ngokunjalo, le collagen nayo ikhona ezindlebeni nasemehlweni ngakho-ke, ushintsho kulezi zitho lungavela ngokuhamba kwesikhathi.

Ungakuqinisekisa kanjani ukuxilongwa

Akukho sivivinyo esithile sokuxilonga i-Alport's syndrome, ngakho-ke udokotela wakho angalawula izivivinyo eziningana, njengokuhlolwa komchamo, ukuhlolwa kwegazi noma ukuhlolwa kwezinso ukukhomba ukuthi ngabe kukhona yini ushintsho olungadala i-syndrome.

Yelashwa kanjani

Ukwelashwa kwe-Alport's syndrome kwenziwa ngenhloso yokuqeda izimpawu, ngoba alukho uhlobo oluthile lokwelashwa. Ngakho-ke, kujwayelekile ukusebenzisa imishanguzo ye-high blood pressure kanye ne-diuretics, ukuze ulawule umfutho wegazi futhi uvimbele ukwanda kokulimala kwezinso.

Ngaphezu kwalokho, kunconywa futhi ukuthi ugcine ukudla okunosawoti omncane ukuvimbela ukusebenza kwezinso ngokweqile. Nakhu ukuthi ungakugcina kanjani ukudla kwalolu hlobo.

Ezimweni ezibucayi kakhulu, lapho izinso zithinteke kakhulu futhi kungekho ukuthuthuka kwezimpawu, kungadingeka ukuqala i-dialysis noma ukufakelwa izinso.