Ukukhubazeka ngezikhathi ezithile ze-Hypokalemic

I-Hypokalemic periodic paralysis (i-hypoPP) yisifo esidala ukuthi ngezikhathi ezithile sibe nobuthakathaka bemisipha futhi kwesinye isikhathi sibe sezingeni eliphansi kunelejwayelekile le-potassium egazini. Igama lezokwelapha lezinga eliphansi le-potassium yi-hypokalemia.

I-HypoPP ingenye yeqembu lokuphazamiseka kofuzo okubandakanya ukukhubazeka kwe-hyperkalemic ngezikhathi ezithile nokukhubazeka kwe-thyrotoxic periodic.

I-HypoPP yindlela ejwayelekile kakhulu yokukhubazeka ngezikhathi ezithile. Ithinta abesilisa kaningi.

I-HypoPP izalwa naso. Lokhu kusho ukuthi ikhona ngesikhathi sokuzalwa. Ezimweni eziningi, idluliselwa emindenini (ezuzwe njengefa) njengesifo esivelele se-autosomal. Ngamanye amagama, umzali oyedwa kuphela odinga ukudlulisa isakhi sofuzo esihlobene nalesi simo enganeni yakhe ukuze ingane ithinteke.

Kwezinye izimo, lesi simo singaba ngumphumela wenkinga yezofuzo engazuzwa njengefa.

Ngokungafani nezinye izinhlobo zokukhubazeka ngezikhathi ezithile, abantu abane-hypoPP banomsebenzi ojwayelekile we-thyroid. Kepha banezinga eliphansi kakhulu legazi le-potassium ngesikhathi seziqephu zobuthakathaka. Lokhu kubangelwa i-potassium esuka egazini iye kumaseli emisipha ngendlela engavamile.

Izici zobungozi zifaka ukuba namanye amalungu omndeni anokukhubazeka ngezikhathi ezithile. Ingozi iphakeme kancane emadodeni ase-Asia nawo anezifo ze-thyroid.

Izimpawu zifaka phakathi ukuhlaselwa ubuthakathaka bemisipha noma ukulahleka kokunyakaza kwemisipha (ukukhubazeka) okuzayo kudlule. Kukhona amandla emisipha ejwayelekile phakathi kokuhlaselwa.

Ukuhlasela kuvame ukuqala eminyakeni yobusha, kodwa kungenzeka ngaphambi kweminyaka yobudala eyi-10. Ukuhlaselwa kwenzeka kaningi kangakanani kuyehluka. Abanye abantu bahlaselwa nsuku zonke. Abanye banazo kanye ngonyaka. Ngesikhathi sokuhlaselwa umuntu uhlala eqaphile.

Ubuthakathaka noma ukukhubazeka:

• Okuvame kakhulu ukwenzeka emahlombe nasezinqeni
• Kungaphinde kuthinte izingalo, imilenze, imisipha yamehlo, nemisipha esiza ngokuphefumula nokugwinya
• Kuvela futhi kuqhubeke
• Okuvame ukwenzeka lapho kuvuswa noma ngemuva kokulala noma ukuphumula
• Kuyaqabukela ngesikhathi sokuvivinya umzimba, kepha kungadalwa ukuphumula ngemuva kokuzivocavoca
• Kungabangelwa i-carbohydrate ephezulu, ukudla okunosawoti omningi, ukucindezeleka, ukukhulelwa, ukuzivocavoca okunzima nokubanda
• Ukuhlaselwa kuvame ukuthatha amahora amaningana kuze kufike osukwini

Esinye isibonakaliso singabandakanya ijwabu leso i-myotonia (isimo lapho ngemuva kokuvula nokuvala amehlo, azikwazi ukuvulwa isikhashana).

Umhlinzeki wezokunakekelwa kwempilo angasola i-hypoPP ngokuya ngomlando womndeni walesi sifo. Eminye imikhondo yalesi sifo yizimpawu zobuthakathaka bemisipha eziza zihambe nemiphumela ejwayelekile noma ephansi yokuhlolwa kwe-potassium.

Phakathi kokuhlaselwa, ukuhlolwa komzimba akubonisi lutho olungajwayelekile. Ngaphambi kokuhlaselwa, kungaba nokuqina kwemilenze noma ubunzima emilenzeni.

Ngesikhathi sokuhlaselwa kobuthakathaka bemisipha, izinga le-potassium yegazi liphansi. Lokhu kuqinisekisa ukuxilongwa. Akukho ukwehla kwe-potassium yomzimba ephelele. Izinga le-potassium yegazi lijwayelekile phakathi kokuhlaselwa.

Ngesikhathi sokuhlaselwa, izingqondo zemisipha ziyancipha noma azikho. Futhi imisipha iyaxhuga kunokuba ihlale iqina. Amaqembu emisipha aseduze komzimba, njengamahlombe nezinqulu, abandakanyeka kaningi kunezingalo nemilenze.

Ukuhlolwa okungenziwa kufaka phakathi:

• I-Electrocardiogram (ECG), engahle ingajwayelekile ngesikhathi sokuhlaselwa
• I-Electromyography (EMG), ejwayelekile ejwayelekile phakathi kokuhlaselwa nokungajwayelekile ngesikhathi sokuhlaselwa
• Imisipha biopsy, engakhombisa ukungajwayelekile

Olunye uvivinyo lunga-oda ukukhipha ezinye izimbangela.

Izinhloso zokwelashwa ukukhululeka kwezimpawu nokuvimbela okunye ukuhlaselwa.

Ubuthakathaka bemisipha obubandakanya imisipha yokuphefumula noma yokugwinya yisimo esiphuthumayo. Ukushaya kwenhliziyo okungajwayelekile (i-heart arrhythmias) nakho kungenzeka ngesikhathi sokuhlaselwa. Noma yikuphi kwalokhu kufanele kulashwe ngokushesha.

I-Potassium enikezwe ngesikhathi sokuhlaselwa ingamisa ukuhlaselwa. I-Potassium ingathathwa ngomlomo. Kepha uma ubuthakathaka bukhulu, i-potassium ingadinga ukunikezwa ngomthambo (IV).

Ukuthatha izithako ze-potassium kungasiza ekuvimbeleni ubuthakathaka bemisipha.

Ukudla ukudla okune-carbohydrate ephansi kungasiza ukunciphisa izimpawu.

Umuthi obizwa nge-acetazolamide ungabekwa ukuvikela ukuhlaselwa. Umhlinzeki wakho angakutshela ukuthi futhi uthathe izithasiselo ze-potassium ngoba i-acetazolamide ingadala ukuthi umzimba wakho ulahlekelwe yi-potassium.

Uma i-acetazolamide ingakusebenzeli, kungenziwa eminye imithi.

I-HypoPP iphendula kahle ekwelashweni. Ukwelashwa kungavimbela, futhi kubuyisele emuva, ubuthakathaka bemisipha obuqhubekayo. Yize amandla emisipha eqala ejwayelekile phakathi kokuhlaselwa, ukuhlaselwa okuphindaphindwayo kungagcina kubangele ukuba buthakathaka nobuthakathaka baphakade bemisipha phakathi kokuhlaselwa.

Izinkinga zempilo ezingaba ngenxa yalesi simo zifaka:

• Amatshe ezinso (umphumela ohlangothini we-acetazolamide)
• Ukushaya kwenhliziyo okungajwayelekile ngesikhathi sokuhlaselwa
• Kunzima ukuphefumula, ukukhuluma, noma ukugwinya ngesikhathi sokuhlaselwa (okungavamile)
• Ubuthakathaka bemisipha obuba ngokuhamba kwesikhathi

Shayela umhlinzeki wakho uma wena noma ingane yakho unobuthakathaka bemisipha obufikayo buqhubeke, ikakhulukazi uma unamalungu omndeni anokukhubazeka ngezikhathi ezithile.

Iya egumbini labezimo eziphuthumayo noma ushayele inombolo yendawo ephuthumayo (efana ne-911) uma wena noma ingane yakho uquleka unenkinga yokuphefumula, ukukhuluma, noma ukugwinya.

I-HypoPP ayinakuvinjelwa. Ngoba kungazuzwa njengefa, ukwelulekwa ngezofuzo kungelulekwa ngemibhangqwana esengozini yokuphazamiseka.

Ukwelashwa kuvimbela ukuhlaselwa kobuthakathaka. Ngaphambi kokuhlaselwa, kungaba nokuqina kwemilenze noma ubunzima emilenzeni. Ukwenza umsebenzi omncane lapho lezi zimpawu ziqala kungasiza ukuvimbela ukuhlaselwa okugcwele.

Ukukhubazeka ngezikhathi ezithile - i-hypokalemic; Ukukhubazeka okujwayelekile kwe-hypokalemic periodic; HOKPP; HypoKPP; HypoPP

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