IPityriasis rubra pilaris
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I-Pityriasis rubra pilaris (PRP) isifo esingajwayelekile sesikhumba esidala ukuvuvukala nokukala (ukukhishwa kwesikhumba) kwesikhumba.
Kunezinhlobo ezingaphansi ezimbalwa ze-PRP. Imbangela ayaziwa, yize izici zofuzo kanye nempendulo engajwayelekile yokuzivikela komzimba kungathinteka. I-subtype eyodwa ihlotshaniswa ne-HIV / AIDS.
I-PRP yisimo sesikhumba esingalapheki lapho ama-scaly e-orange noma anemibala e-salmon enesikhumba esijiyile ekhula ezandleni nasezinyaweni.
Izindawo ezinamakhasi zingamboza ingxenye enkulu yomzimba. Iziqhingi ezincane zesikhumba esijwayelekile (ezibizwa ngokuthi iziqhingi zokulondolozwa) zibonakala ngaphakathi kwezindawo zesikhumba se-scaly. Izindawo ezinamakhasi kungenzeka zilume. Kungaba nezinguquko kuzipikili.
I-PRP ingaba nzima. Yize kungeyona impilo esongela, i-PRP inganciphisa kakhulu ikhwalithi yempilo futhi ikhawulele imisebenzi yokuphila kwansuku zonke.
Umhlinzeki wezokunakekelwa kwempilo uzohlola isikhumba sakho. Ukuxilongwa kuvame ukwenziwa ngokuba khona kwezilonda ezihlukile zesikhumba. (Isilonda indawo engajwayelekile esikhunjeni). Umhlinzeki angathatha amasampula (ama-biopsies) esikhumba esithintekile ukuqinisekisa ukuxilongwa futhi anqume izimo ezingabukeka njenge-PRP.
Ukhilimu onezihloko oqukethe i-urea, i-lactic acid, ama-retinoid, nama-steroids angasiza. Ngokuvamile, ukwelashwa kufaka amaphilisi athathwe ngomlomo afana ne-isotretinoin, acitretin, noma i-methotrexate. Ukuvezwa kokukhanya kwe-ultraviolet (ukwelashwa okulula) nakho kungasiza. Imithi ethinta amasosha omzimba okwamanje iyafundwa futhi ingasebenza ku-PRP.
Lesi sisetshenziswa singanikeza imininingwane engaphezulu ku-PRP:
- Inhlangano Kazwelonke Yezinkinga Ezingajwayelekile - rarediseases.org/rare-diseases/pityriasis-rubra-pilaris
Shayela umhlinzeki wakho uma uthuthukisa izimpawu ze-PRP. Fonela futhi uma unale nkinga futhi izimpawu ziba zimbi kakhulu.
PRP; IPityriasis pilaris; I-lichen ruber acuminatus; Isifo se-Devergie
IPityriasis rubra pilaris esifubeni
IPityriasis rubra pilaris ezinyaweni
IPityriasis rubra pilaris ezintendeni zezandla
I-Pityriasis rubra pilaris - ukusondela
UJames WD, u-Elston DM, Phatha i-JR, i-Rosenbach MA, i-IM ye-Neuhaus. I-Pityriasis rosea, i-pityriasis rubra pilaris, nezinye izifo ezibangelwa i-papulosquamous kanye ne-hyperkeratotic. Ku: James WD, Elston DM, Treat JR, Rosenbach MA, Neuhaus IM, eds. Izifo zika-Andrews 'Zesikhumba: I-Clinical Dermatology. Umhlaka 13. IPhiladelphia, PA: Elsevier; 2020: isahluko 11.
IPatterson JW. Ukuphazamiseka kombala. Ku: Patterson JW, ed. I-Weedon's Skin Pathology. Umhla wesi-4. IPhiladelphia, PA: Elsevier Churchill Livingstone; 2016: isahluko 10.