Umlobi: Judy Howell
Usuku Lokudalwa: 5 Ujulayi 2021
Ukuvuselela Usuku: 1 Ujulayi 2024
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I-Polycythemia Vera: Ukubikezela nokulindela impilo - Impilo
I-Polycythemia Vera: Ukubikezela nokulindela impilo - Impilo

-Delile

I-Polycythemia vera (PV) umdlavuza wegazi ongajwayelekile. Yize lungekho ikhambi le-PV, lingalawulwa ngokwelashwa, futhi ungaphila nalesi sifo iminyaka eminingi.

Ukuqonda i-PV

I-PV ibangelwa ukuguqulwa noma ukungajwayelekile kuzakhi zofuzo zamaseli ezinhlayiya emnkantsheni wakho. I-PV iqina igazi lakho ngokukhiqiza amangqamuzana egazi abomvu amaningi kakhulu, angavimba ukugeleza kwegazi liye ezithweni nakumathishu.

Imbangela ngqo ye-PV ayaziwa, kepha kubantu abanesifo nabo banokuguquka kwesimo se- JAK2 isakhi sofuzo. Ukuhlolwa kwegazi kungakubona ukuguquka kwezakhi.

I-PV itholakala ikakhulu kubantu abadala asebekhulile. Kuyaqabukela kwenzeka kunoma ngubani ongaphansi kweminyaka engama-20.

Cishe abantu ababili kwabangu-100 000 bathintekile yilesi sifo. Kulaba bantu, kungaqhubeka nokukhula kwezinkinga zesikhathi eside ezifana ne-myelofibrosis (isibanda somnkantsha) kanye neleukemia.

Ukulawula i-PV

Inhloso enkulu yokwelashwa ukulawula ukubalwa kwamaseli akho egazi. Ukunciphisa inani lamaseli abomvu wegazi kusiza ukuvimbela amahlule angaholela kohlangothi, isifo senhliziyo, noma okunye ukulimala komzimba. Kungase futhi kusho ukuphatha ukubalwa kwamaseli amhlophe egazi nokubalwa kweplatelet. Inqubo efanayo ekhombisa ukukhiqizwa ngokweqile kwamangqamuzana egazi abomvu ibonakala futhi ikhombisa ukukhiqizwa ngokweqile kwamaseli amhlophe egazi nama-platelets.Ukubalwa kwamaseli egazi aphakeme, noma ngabe luhlobo luni lwegazi, kwandisa ubungozi bamahlule egazi nezinye izinkinga.


Ngesikhathi sokwelashwa, udokotela wakho uzodinga ukukuqapha njalo ukuze ubukele i-thrombosis. Lokhu kwenzeka lapho ihlule legazi likhula emthanjeni noma emthanjeni futhi livimba ukugeleza kwegazi liye ezithweni zakho ezinkulu noma ezicutshini.

Inkinga yesikhathi eside ye-PV yi-myelofibrosis. Lokhu kwenzeka lapho umnkantsha wakho unesibazi futhi ungabe usakwazi ukukhiqiza amaseli anempilo asebenza kahle. Wena kanye ne-hematologist yakho (onguchwepheshe wokuphazamiseka kwegazi) ningaxoxa ngokufakelwa umnkantsha wethambo ngokuya ngecala lakho.

I-leukemia enye inkinga yesikhathi eside ye-PV. Ngokuqondile, womabili ama-acute myeloid leukemia (AML) kanye ne-acute lymphoblastic leukemia (ALL) ahlotshaniswa ne-polycythemia vera. I-AML ivame kakhulu. Ungadinga ukwelashwa okukhethekile okugxile nasekuphathweni kwe-leukemia uma lokhu kuba nenkinga.

Ukuqapha i-PV

I-PV ayivamile, ngakho ukuqapha nokuhlola okuvamile kubalulekile. Lapho uthola ukuthi unesifo sokuqala, ungahle ufune i-hematologist esikhungweni esikhulu sezokwelapha. Labo ngoti begazi bazokwazi kabanzi nge-PV. Futhi kungenzeka banikeze ukunakekelwa kothile onalesi sifo.


I-Outlook ye-PV

Uma usuthole i-hematologist, sebenza nabo ukusetha uhlelo lokuqokwa. Uhlelo lwakho lokuqokwa luzoncika ekuqhubekeni kwe-PV yakho. Kepha kufanele ulindele ukubona i-hematologist yakho cishe kanye ngenyanga iye kanye njalo ezinyangeni ezintathu ngokuya ngamanani wegazi, ubudala, impilo yonke, nezinye izimpawu.

Ukuqapha nokwelashwa okujwayelekile kungasiza ekukhuliseni isikhathi sakho sokuphila futhi kuthuthukise ikhwalithi yakho yonke yokuphila. Ngokuya ngezici ezahlukahlukene, isikhathi samanje sokuphila sikhonjisiwe ukuthi sisukela ngesikhathi sokuxilongwa. Iminyaka yobudala, impilo yonke, ukubalwa kwamaseli egazi, ukuphendula ekwelashweni, izakhi zofuzo, kanye nokukhethwa kwendlela yokuphila, njengokubhema, konke kunomthelela enkambweni yalesi sifo nokubukeka kwaso kwesikhathi eside.

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