Ukwelashwa kwe-ectodermal dysplasia

-Delile

• Izimpawu ze-ectodermal dysplasia
• Izinhlobo ze-ectodermal dysplasia

Ukwelashwa kwe-ectodermal dysplasia akucacisiwe futhi lesi sifo asinalo ikhambi, kepha ukuhlinzwa kwezimonyo kungasetshenziswa ukuxazulula okunye ukungalungi okubangelwa yilesi sifo.

I-Ectodermal dysplasia iqukethe iqoqo lezinkinga ezingamafa ezingavamile ezivela enganeni kusukela izelwe futhi, ngokuya ngohlobo lwayo, zidala ushintsho ezinweleni, kuzinzipho, emazinyweni noma kwizindlala ezikhiqiza umjuluko, ngokwesibonelo.

Njengoba lungekho unyango oluthile lwe-ectodermal dysplasia, ingane kufanele ihambisane kaningi nodokotela wezingane ukuhlola ukukhula kwayo nokuhlola isidingo sokuhlinzwa kwezimonyo ukuze ithuthukise ukuzethemba kwayo, ngokwesibonelo.

Ngaphezu kwalokho, kubalulekile ukuhlola ukushisa komzimba wengane nsuku zonke, ikakhulukazi ezimweni lapho kungekho khona ukukhiqizwa kwezithukuthuku, njengoba kunengozi enkulu yokuhlaselwa ukushisa ngenxa yokushisa ngokweqile komzimba. Bona ukuthi ulinganisa kanjani izinga lokushisa kahle.

Ezimweni lapho kushoda khona amazinyo noma olunye ushintsho emlonyeni, kunconywa ukuthi uthintane nodokotela wamazinyo ukuze wenze ukuhlolwa okuphelele komlomo bese uqala ukwelashwa okufanele, okungabandakanya ukuhlinzwa nokufakelwa kwamazinyo, ukuvumela ingane udle ngokujwayelekile.

Izimpawu ze-ectodermal dysplasia

Izimpawu nezimpawu eziyinhloko ze-ectodermal dysplasia zifaka:

• Umkhuhlane ophindayo noma ukushisa komzimba ngaphezu kuka-37ºC;
• Ukuzwela okukhulu ezindaweni ezishisayo;
• Ukukhubazeka emlonyeni onamazinyo alahlekile, abukhali noma aqhelelene kakhulu;
• Izinwele ezincanyana kakhulu nezinamahloni;
• Izipikili ezizacile nezishintshiwe;
• Ukuntuleka kokukhiqizwa kwezithukuthuku, amathe, izinyembezi nolunye uketshezi lomzimba;
• Isikhumba esincanyana, esomile, esinamaxolo futhi esizwela kakhulu.

Izimpawu nezimpawu ze-ectodermal dysplasia azifani kuzo zonke izingane futhi, ngakho-ke, kujwayelekile ukuthi kuvele ezimbalwa zalezi zimpawu.

Izinhlobo ze-ectodermal dysplasia

Izinhlobo ezimbili eziyinhloko ze-ectodermal dysplasia zifaka:

• Anhydrous noma hypohydrotic ectodermal dysplasia: kubonakala ngokuncipha kwenani lezinwele nezinwele, ukunciphisa noma ukungabikho ketshezi lomzimba, njengezinyembezi, amathe nomjuluko noma ukungabikho kwamazinyo.
• I-Hydrotic ectodermal dysplasia: isici esiyinhloko ukungabikho kwamazinyo, noma kunjalo, kungadala nezindebe ezinkulu, zangaphandle, ikhala eliyisicaba namabala azungeze amehlo.

Imvamisa, ukutholakala kwe-ectodermal dysplasia kwenziwa ngemuva nje kokuzalwa ngemuva kokubona ukukhubazeka kwengane, noma kunjalo, kwezinye izimo lezi zinguquko kungenzeka zingabonakali kahle, ngakho-ke, zitholwa ngokuhamba kwesikhathi ekukhuleni kwengane.