Umlobi: Laura McKinney
Usuku Lokudalwa: 8 Epreli 2021
Ukuvuselela Usuku: 1 Ujulayi 2024
Anonim
Sjögren Syndrome | Rheumatology
Ividiyo: Sjögren Syndrome | Rheumatology

-Delile

Yini i-secondary Sjogren's syndrome?

I-Sjogren's syndrome yisifo sokuzilimaza somzimba esilimaza izindlala ezikhiqiza umswakama, okwenza kube nzima ukukhiqiza amathe nezinyembezi. Uphawu lwesifo ukungena kwezitho ezihlosiwe ngama-lymphocyte. Lapho i-Sjogren's syndrome ivela yodwa, ibizwa ngokuthi i-primary Sjogren's syndrome.

Uma usuvele unesinye isifo sokuzilimaza, lesi simo sibizwa ngokuthi yi-secondary Sjogren's syndrome. Ngama-Sjogren wesibili, ungahle ube nesimo esimnene sesimo. Kodwa usazohlangabezana nezimpawu zesifo esivele sikhona. Isizathu esivame kakhulu seSjogren's secondary yi-rheumatoid arthritis (RA), olunye uhlobo lwesifo sokuzilimaza.

Izimpawu

Izimpawu ze-Sjogren's zingafaka amehlo omile, umlomo, umphimbo, kanye nemigwaqo yomoya engenhla. Ungaba nobunzima bokukunambitha noma ukugwinya ukudla kwakho. Ungase futhi uhlakulele ukukhwehlela, ukushaqeka, izinkinga zamazinyo, noma ube nobunzima bokukhuluma. Kwabesifazane, ukoma kwesitho sangasese sowesifazane kungenzeka.

Izinhlobo zokuqala nezesibili zamaSjogren's angaba nezimpawu ezifanayo, ezibandakanya:


  • ukukhathala
  • Inkungu yobuchopho
  • imfiva
  • ubuhlungu obuhlangene
  • ubuhlungu bemisipha
  • ubuhlungu bezinzwa

Ngokuvamile, izimbangela zikaSjogren:

  • ukuqubuka kwesikhumba
  • izinkinga ezinkulu zamathumbu
  • ukuvuvukala kwesibindi, izinso, amanyikwe, noma amaphaphu
  • ukungazali noma ukuya esikhathini ngaphambi kwesikhathi

Ama-Secondary Sjogren's angahambisana nale mibandela elandelayo:

  • RA
  • i-cholangitis eyinhloko ye-biliary
  • lupus
  • scleroderma

Ngenkathi izimpawu ze-RA zivame ukufaka ukuvuvukala, ubuhlungu, nokuqina kwamalunga, kungadala nezinye izimpawu ezifana nezikaSjogren. Lokhu kufaka phakathi:

  • umkhuhlane omncane
  • ukukhathala
  • ukulahlekelwa isifiso sokudla

Izici zobungozi

Ngokusho komtholampilo waseCleveland, abantu abangaphezu kwesigidi e-United States bane-primary Sjogren’s. Amaphesenti angaphezu kuka-90 ngabesifazane. Ungayithuthukisa i-Sjogren's nganoma yisiphi isikhathi, kepha ivame ukutholakala ngemuva kweminyaka yobudala engama-40, ngokusho kweMayo Clinic. Imbangela ngqo kaSjogren ayaziwa. Kodwa njenge-RA, kuyisifo samasosha omzimba.


Imbangela eqondile yeRA nayo ayaziwa, kodwa kukhona ingxenye yezakhi zofuzo ethintekayo. Uma unelungu lomndeni elinanoma yisiphi isifo se-autoimmune, njenge-RA, usengozini yokuthola esinye, futhi.

Ukuxilongwa

Asikho isivivinyo esisodwa seSjogren's. Ukuxilongwa kungenzeka ngemuva kokuthi utholakale unesinye isifo sokuzilimaza nokuthuthukisa ukoma komlomo namehlo. Noma ungahlangabezana nezinkinga ezinzima zesisu noma ubuhlungu bezinzwa (i-neuropathy).

Ukuxilonga ama-Sjogren's secondary ne-RA, kuzodingeka ukuthi uvivinye uchungechunge lwezivivinyo. Ngokuvamile lokhu kufaka ama-antibodies e-SSA / SSB kanye ne-lip biopsy ephansi ukubheka izindawo ezigxile kuma-lymphocyte. Ungathunyelwa kudokotela wamehlo ukuhlola iso elomile. Udokotela wakho uzokhipha nezinye izimbangela zezimpawu zakho.

Ukuhlolwa kwe-Sjogren's

Udokotela wakho uzoqala abheke umlando wakho ophelele wezokwelapha bese enza ukuhlolwa komzimba. Bazophinde ba-oda lezi zivivinyo ezilandelayo:

  • ukuhlolwa kwegazi: Lokhu kusetshenziselwa ukubona ukuthi unawo yini ama-antibodies athile afana ne-Sjogren's. Udokotela wakho uzobheka ama-anti-Ro / SSA nama-anti-La / SSB antibodies, ANA, ne-rheumatoid factor (RF).
  • i-biopsy: Phakathi nale nqubo, udokotela wakho uzogxila kwizindlala zakho zamathe.
  • Ukuhlolwa kukaSchirmer: Ngesikhathi sokuhlolwa kweso kwemizuzu emihlanu, udokotela wakho ubeka iphepha lokuhlunga ekhoneni leso lakho ukuze ubone ukuthi limanzi kanjani.
  • I-Rose-Bengal noma i-lissamine test stain test: Lokhu okunye ukuhlolwa kwamehlo okulinganisa ukoma kwe-cornea.

Izimo ezilingisa i-Sjogren's

Qiniseka ukuthi utshela udokotela wakho nge-over-the-counter (OTC) nemithi kadokotela oyiphuzayo. Eminye imithi ingadala izimpawu ezihambisana ne-Sjogren's. Le mithi ihlanganisa:


  • i-tricyclic antidepressants efana ne-amitriptyline (Elavil) ne-nortriptyline (Pamelor)
  • ama-antihistamine afana ne-diphenhydramine (Benadryl) ne-cetirizine (iZyrtec)
  • izinto zokuvimbela inzalo ngomlomo
  • imishanguzo yegazi

Ukwelashwa ngemisebe nakho kungadala izimpawu ezifanayo, ikakhulukazi uma uthola lezi zindlela zokwelapha ezungeze ikhanda nasentanyeni.

Ezinye izinkinga zokuzivikela komzimba nazo zingalingisa i-Sjogren's. Kubalulekile ukuthi uthathe zonke izivivinyo ezinconyiwe futhi ulandele udokotela wakho ukuthola imbangela ngqo yezimpawu zakho.

Izinketho zokwelashwa

Alikho ikhambi le-Sjogren's noma i-arthritis, ngakho-ke ukwelashwa kubalulekile ekunciphiseni izimpawu nasekuthuthukiseni izinga lakho lempilo. Uhlelo lwakho lokwelashwa luncike ebukhulwini bezimpawu zakho. Kuzodingeka ukuthi uzame inhlanganisela yokwelashwa. Ezinye izinketho zifaka:

Imithi

Uma unezinhlungu nasemalungeni nasemisipheni yakho, zama ukudambisa izinhlungu kwe-OTC noma imithi elwa nokuvuvukala. Izidakamizwa ezingezona ukuvuvukala (i-NSAIDS) ezinjenge-ibuprofen (Advil, Motrin) zingasiza.

Uma bengenzi iqhinga, buza udokotela wakho ngemithi ye-corticosteroids nemithi yokulwa nesifo sokuqaqanjelwa yimithambo noma yokuzivikela. Lokhu kusebenza ngokunciphisa ukuvuvukala nokuvimbela umzimba wakho ekuhlaseleni owawo.

Nge-Sjogren's yesibili, ungahle udinge nemithi yokusiza ukukhulisa uketshezi njengezinyembezi namathe. Imithi ejwayelekile kadokotela ifaka i-cevimeline (Evoxac) ne-pilocarpine (Salagen). Ungadinga amaconsi wamehlo kadokotela ukusiza iso elomile. I-Cyclosporine (i-Restasis) ne-lifitegrast ophthalmic solution (i-Xiidra) yizinketho ezimbili.

Indlela Yokuphila

Izinketho ezithile zendlela yokuphila zingakusiza nokuthi ulwe neSjogren's neRA yesibili. Okokuqala, ungalwa nokukhathala ngokulala kahle ebusuku nokuthatha amakhefu emini. Futhi, buza udokotela wakho mayelana nokuzivocavoca umzimba okungakusiza ukuthi ukhulise ukuguquguquka komzimba futhi unciphise ubuhlungu bemisipha namalunga. Ukuzivocavoca njalo kungathuthukisa ukuguquguquka futhi kunciphise ukungakhululeki. Kuzosiza futhi ukugcina isisindo esifanele somzimba nokubeka ingcindezi emalungeni nasemisipha.

Ukugcina ukudla okunomsoco omkhulu kungathuthukisa impilo yakho yonke. Namathela ekudleni okususelwa ezitshalweni nasemafutheni alwa nokuvuvukala atholakala kofulawa bamafutha nezinhlanzi. Gwema ushukela nokudla okugayiwe. Lokhu kungakhuphula ukuvuvukala.

Ngidinga uhlobo luni lodokotela?

Odokotela abagxile kwizifo ezinjenge-arthritis babizwa ngama-rheumatologists. Uma utholwe une-arthritis, i-rheumatologist yakho cishe izokwazi ukwelapha i-Sjogren's.

Ngokuya ngobukhulu bezimpawu zakho, i-rheumatologist yakho noma udokotela ojwayelekile angakudlulisela kwabanye ochwepheshe. Zizobandakanya udokotela wezifo zamehlo, udokotela wamazinyo, noma i-otolaryngologist, owaziwa nangokuthi uchwepheshe wezindlebe, impumulo nomphimbo.

Umbono wesikhathi eside

Alikho ikhambi le-Sjogren's noma i-RA. Kepha kunezindlela eziningi zokwelashwa nezindlela zokuphila ezingakhuphula izinga lempilo yakho.

Izimpawu zesifo samathambo ziyahlukahluka kusuka kumnene kakhulu kuya ekunciphiseni, kepha isifo samathambo eSjogren's eyinhloko akuvamile ukulimaza. Okusemqoka ukuthi usebenzisane nodokotela wakho ukuthola izindlela zokwelashwa ezihamba phambili. Ezimweni ezingavamile, abantu abane-Sjogren's bangase bahlakulele i-lymphoma. Bika udokotela wakho izimpawu zokuvuvukala okungajwayelekile noma izinkinga ze-neurologic.

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